Olu hlobo lwe-Frontotemporal Degeneration Ikwabizwa ngokuba yi-Pick's Disease
Ukungafani komqondo we-frontotemporal (bvFTD) yindlela yokuziphatha enomnye weentlobo ezininzi ze-dementias eziwela kwi-"frontellemporal degeneration". Eli candelo lichaphazela malunga nama-50,000 ukuya kuma-60,000 aseMelika. Njengoko igama libonisa, olu hlobo lwesifo sengqondo oluchaphazelekayo luyakuthinta kakhulu i-lobes yangaphambili kunye neyesikhashana yengqondo. I-dementias ye-frontotemporal yeyona ndlela iqhelekileyo yindlela yokuziphatha eyahlukileyo.
Ngezinye iinkqubo ukubizwa ngokuba yi-mental-demant dementia ngokubhekiselele kwisimo sengqondo.
Yintoni Ebangelwa Izifo ZikaPickk?
Isifo sikaPick sicingelwa ukuba sibangelwa ukuhlanganiswa okungavumelekanga kwamaprotheni kwi-lobes yangaphambili neyesikhashana yengqondo. Ezi zixhobo zeeprotheyini ziyaziwa njengezixhobo ze-Pick. Njengoko baqokelela kule ndawo, iinkolelo zengqondo ziqala ukufa, ezibangela ukuguquka kwemizwelo, yokuziphatha kunye nokuqonda.
Iimpawu
Iimpawu eziqhelekileyo ze-bvFTD ziziingxaki zokuziphatha okanye iimvakalelo , kuquka ukunyusa ngokunyanisekileyo, ukuziphatha ngendlela engavumelekile, ukwenza iimpendulo ezingalunganga kuluntu, nokubonakalisa ingxoxo kunye nezenzo zokuxhatshazwa ngokwesini , kunye nokukhathazeka , ukukhathazeka , ukunganakwa nokuzingca.
Abantu abane-bvFTD banokuba nobunzima bokugcina umsebenzi, babonise ukuhla kohlambuluko lwabo, balondoloze izinto ezithile, benze ukhetho olubi lwemali, kunye namalungu omndeni osuka kunye nabahlobo ngenxa yezimvo zabo ezingenakuzikhusela nokuziphatha.
Abanye abantu abane-bvFTD nabo banamava okunyakaza okufana nesifo sika-Parkinson , kubandakanywa nesibonakaliso somzimba, ukuqina komzimba, ubuthathaka kunye nokuqina.
Ngokungafani ne- Alzheimer's , ukulahlekelwa kweememori akuqhelekanga ku-bvFTD, kwaye ukuba kuyenzeka, akude kube eso sifo sigaba sazo.
Njengomnakekeli, unokubona ubunzima beememori, kunye nemingeni ngokucwangcisa okanye ukuqwalasela (eziphathelene nokusebenza okulawulayo ).
Kwi-bvFTD enzima, ulwimi luye lwachaphazeleka, okwenza kube lula kunxibelelana .
Izifo zePickk zihluke njani kwi-Alzheimer's?
Isifo sengqondo se-frontotemporal (isifo sikaPick) sinezibonakaliso ezithintekayo zesifo se-Alzheimer ekubeni izifo zombini zichaphazela ukuqonda, iimvakalelo kunye nokuziphatha.Izibonakaliso zangaphambilini zesifo sikaPick, nangona kunjalo, ziquka ngokutsha utshintsho kwimvakalelo, isigwebo , ukusebenza komsebenzi kunye nokuziphatha, ngelixa kwi-Alzheimer's disease, imemori, ukuqhelaniswa kunye neentlupheko zoqhagamshelwano ziqhelekileyo ekuqaleni.
Ukuxilongwa
Ukuxilongwa kwe-BvFTD kudlalwa ngokukhawuleza kuba ekuqaleni kunokucatshulwa ukuba umntu ochaphazelekayo unobundlobongela, ugoce, uxinezelekileyo okanye usebenze ngokungafani. Njengoko iimpawu ziqhubela phambili, kunjalo, iintsapho zihlala zifuna uncedo lonyango ukuxilongwa kunye unyango. Ukuxilongwa kuxhomekeke kubuninzi beempawu ezichazwe ngasentla, kunye nokukwazi ukulawula olunye uhlobo lwe-dementias ezifana ne-Alzheimer's okanye isifo sengqondo se-masentim . Ukuphonononga imigaqo eqhotyoshelweyo ye-FTD eyahlukileyo yokuziphatha ingaba luncedo kumalungu entsapho ukuba i-BvFTD ifunyanwe okanye iqwalaselwe ngugqirha.
I-MRI inokukunceda ekufumaneni i-bvFTD kuba iya kubakho ukubonisa i- atrophy (shrinkage) ye- lobe yangaphambili yengqondo. Njengoko eso sifo siyaqhubeka, i-atrophy iya kwanda kwaye isasaze kwiindawo zexeshana, kunye ne-basal ganglia.
Ukuxhamla kunye nokuLindelwa koBomi (i-Long-Term Outlook)
Umyinge wokulindela ubomi ukususela ekuqaleni kweempawu kuba malunga nesibhozo ukuya kweyisithoba, nangona abanye abantu behlala iminyaka engama-20 okanye nesifo. Njengawo nawuphi na umqondo weengqondo, ingaba sisifo esinzima kubantu abanonophelo, kunye nabo bafumana.
Unyango
Unyango lunokuquka ukuzama ukusebenzisa izicwangciso zokuziphatha ezingezizo iziyobisi ukwenzela ukunqanda ukuziphatha okuthe ngqo.
Abanye oogqirha babonelela abantu abachasayo ukubizwa ngokuthi i-serotonin reuptake inhibitors (i-SSRIs), enokunceda ngezinye iindlela zokuziphoqa-ukunyanzelisa okanye ukunyusa.
ILizwi
Kuqhelekile ukuba uzive ukhululekile ngamanye amaxesha njengoko ujamelana nemingeni yokuziphatha kwe-frontotemporal dementia. Ungayithobeli isilingo sokuzama ukwenza konke wena; Kunoko, funa ufumane inkxaso kubantu abakujikelezile, nokuba ingaba yinkqubo yokuxhasa uluntu, ingxoxo ye-intanethi malunga ne-BvFTD okanye umhlobo ozimisele ukukhipha ikhofi okanye uhlale ekhaya kunye nomthandayo xa ulala.
Ukongezelela, uMbutho we-Frontotemporal Dementia ubhala amaqela ezenkxaso zengingqi kunye nezixhobo ze-intanethi kunye nomgca wefowuni uncedo.
Imithombo:
Annals of Neurology. Ukutshintsha kunye ne-hypothalamus utshintsho kwi-behavioral-variant demokrasia ye-frontotemporal. http://www.ncbi.nlm.nih.gov/pmc/article/PMC3084499
Umbutho we-Frontotemporal Degeneration. Iingqinisiso zamazwe ngamazwe malunga neendlela zokuziphatha ezihlukeneyo ze-FTD. http://www.theaftd.org/wp-content/uploads/2009/02/Table-3-International-census statement--behavioural-variant-FTD.pdf
Amabhanki, S., Weintraub, S. Journal of Geriatric Psychiatry kunye Neurology. Iimpawu ze-Neuropsychiatric kwiMpawu ezahlukileyo kwi-Frontotemporal Dementia kunye nePrayimari yePrayimari ePhambili. Http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2892801/
Neurology. Ukuvakalelwa kweendlela ezikhoyo zokuxilongwa kweendlela zokuziphatha ezibangelwa yi-frontotemporal dementia. http://www.ncbi.nlm.nih.gov/pmc/articles/PMC2821829/
KwiYunivesithi yaseCalifornia, eSan Francisco. Izifo eziqhubekayo: Uhlobo lwe-FTD oluthile. http://memory.ucsf.edu/ftd/overview/ftd/progrression/multiple