Ukuchonga iGuillain-Barré Syndrome

Yintoni onokuyilindela ngexesha lovavanyo lwakho

UGuilin-Barré uyinto engavumelekanga apho umzimba we-immune system uphosakela iindawo zeengxube zomzimba zentsholongwane kwaye zithumela izifo eziza kuhlasela loo misonto. Umphumo oqhelekileyo unobuthathaka kunye nobuthathaka obuqala kwiingcebiso zeminwe kunye neenzwane kwaye zisasazela ngaphakathi emzimbeni.

Phantse iipesenti ezingama-30 zexesha, lobu buthathaka buba nzima kangangokuba isiguli asikwazi ukuphefumula ngokwabo.

Kananjalo abakwazi ukugwinya ukutya okanye umatha ngaphandle kokuba "behla ityhubhu engalunganga" kunye nemiphunga yabo. Ngenxa yezi zizathu, u-Guillain-Barré unokusongela ubomi kwaye ufuna ukugqithiswa kwamagqirha, ngokuqhelekileyo kwisibhedlele. Apha uya kufumana indlela oogqirha abone ngayo ukuba isigulane sinesifo se-Guillain-Barré.

Uvavanyo lweMzimba

Ngaphandle kokuba uthathe imbali echanekileyo ukuba uthathe isigqibo sokuba ngaba u-Guillain-Barré unokwenzeka, ugqirha uya kukhangela iziphumo ezithile ekuhloleni ngokomzimba. Ngenxa yokuba izibilini zomhlaba zonakaliswe eGuillain-Barré, iingcamango , ezifana ne-knee-jerk reflex, zivame ukuba zingekho. Ugqirha uya kuvavanya iingalo kunye nemilenze ukuze abone ukuba ababuthathaka kwaye benze iimvavanyo ezivakalayo ukuba babone ukuba kukho naluphi na uhlobo lwe-numbness. Oogqirha abanenkxalabo malunga noGuillain-Barré baya kuqwalasela ngokugqithiseleyo iintsholongwane zengxaki kuba xa ezi zonakaliswe, kunokukhokelela ekufuneni intubation okanye umoya wokungenisa umoya ukuze kuqinisekiswe ukuba isigulane siqhubeka siphefumula.

I-Electromyography kunye noPhando lweeNerving Studies (EMG / NCS)

Xa inkqubo ye-nervous system ihlushwa yisifo, iyatshintsha uhlobo lweempawu zombane ezithunyelwe kwaye zifunyenwe kule nkqubo. Ngokulinganisa olu tshintsho ngezixhobo ezizodwa, oogqirha abanako ukuxelela kuphela ukuba kukhona into engalunganga, kodwa nokuba yiyiphi inxalenye yezibilini ezichaphazelekayo.

Le ngcaciso inokukunceda ukukhokela izigqibo malunga nokukhetha unyango, kunye nokunika ugqirha ingcamango yokuba isigulo siyingozi kangakanani kwaye kuya kuthatha ixesha elingakanani umntu ukuba abuyele.

Ngokomzekelo, ukuba umntu unobuthakathaka obusasa phezulu, njengoGuillain-Barré, unokukwazi, ezi zifundo zinganceda ukuba i-axon okanye i-myelin ishaath of the nerve ihlaselwa. U-Myelin ujikeleze i-axon kwaye unceda iimpawu zombane zihamba ngokukhawuleza kunokuba zingenjalo. Ukuba umbane uhamba ngokuthe ngcembe ngentsholongwane, oogqirha banokwenkqangaza ukuba i-myelin ihlaselwa, apho imeko eqhelekileyo kaGuillain-Barré mhlawumbi ibangelwa.

Ngakolunye uhlangothi, ukuba i-axon ihlaselwa, isignali engaphantsi kombane iya kuyenza. Ukuba oku kulinganiswa ngezifundo zokuqhutyelwa kwamanzi, enye yeendlela eziqhelekileyo ze-axonal zeGuillain-Barré zinokuba zixanduva. Ukuba oku kuchaphazela zombini i-sensory ne-motor neurons, isigulane sinokuba ne-acute motor ne-sensonal neuropathy (AMSAN).

Lumbar Ukuhamba

Kwiingxaki ezizenzekelayo ezichaphazela inkqubo ye-nervous, inani leprotheni emzimbeni we- cerebrospinal fluid (CSF) linokuphakama.

Ngenxa yalesi sizathu, ukutyhulwa kwe-lumbar kungenziwa. Ukwenza i-lumbar puncture kunganceda ukulawula abanye abaxhamli be-Guillain-Barré, ezifana nezifo.

Uvavanyo lweGazi

Akuqhelekanga ukuba oogqirha bafumane iimvavanyo zegazi ukuze bancede bafumene i-Guillain-Barré syndrome. Kwezinye iimeko, oku kunokukunceda ukufumana i-antibody inoxanduva. Ngokomzekelo, ukuhluka kweMiller-Fisher kaGuillain-Barré ngokuqhelekileyo kudibene ne-antibody ebizwa ngokuba yi-GQ1b. Ukufumanisa lo mkhuhlane uqinisekisa ukuxilongwa kweMiller-Fisher, kwaye unokwenza ukuba ugqirha uqaphele ngokukodwa ngexesha elizayo lokungena.

Iimvavanyo zegazi nazo zinceda ekulawuleni ezinye iimeko ezinokubonakala zifana ne-Guillain-Barré syndrome.

Ngokuxhomekeke kwimbali kunye nokuhlolwa komzimba, ugqirha unokuvavanya iimpawu zomhlaza , ukusuleleka, okanye i-toxins, njenge-mercury.

Kubalulekile ukwazi ngokuchanekileyo oko kubangela ingxaki ukuze ugweme ukunikezela ngemithi engafanelekanga. Ukufakela ukuxilongwa kukaGuillain-Barré kuvumela ukuba oogqirha bezogqirha bagxininise unyango olufanelekileyo, kwaye banokukunika ulwazi oluthe xaxa malunga noko ukulindele ukuba isifo sifunde, ukuba uza kubuyiselwa ngokukhawuleza njani, kwaye luhlobo luni loncedo oluya kulufuna ukubuyela kulo iinyawo kwakhona.

Imithombo:

I-Ropper AH, i-Samuels MA. I-Adams kunye neMigaqo yeVictor ye-Neurology, 9-ed: I-McGraw-Hill Companies, Inc., 2009. Ilungu leMcCabe, u-O'Connor EJ.

I-Yuen T. Ngoko, i-Continuum: I-Peripheral Neuropathies, i-Immune-Mediated Neuropathies, uMqulu 18, iNombolo 1, ngoFebruwari 2012.