I-SPS ibangele i-Muscle Stiffness ne-Spasms
Isifo somntu osisigxina (esibizwa nangokuthi i-Moersch-Woltmann syndrome) okanye i-SPS yinkqubo engabonakali yinkqubo yesifo se-nervous stability. Uphando lubonisa ukuba isifo esinzima somntu sisifo sengqondo esisodwa, kwaye abantu abane-syndrome bavame ukuxhatshazwa ngokuzenzekelayo njengolu hlobo lwesifo sikashukela okanye i- thyroiditis .
Isifo somntu osisigxina sichaphazela bonke abesilisa nabesifazane kwaye singaqala nanini na ubudala, nangona ukuxilongwa ebuntwaneni kubunqabile.
Ayaziwa ukuba bangaphi abantu abahluphekayo kuyo.
Izibonakaliso ze-Stiff Person Syndrome
Iimpawu zesifo somntu onzima singabandakanya:
- Ukuqina kobunzima kwi-trunk kunye neengalo eziza kwaye zihamba-oku kubangela ukuqina kobuhlungu okanye intlungu, ukunyaniseka okuthe tye, nokuhamba
- Iimfudu ezinamandla kwiingalo nasemilenzeni xa umntu ehlaselwa, echukumiseka, ecasulayo, okanye exhalabisa
- Umqolo ophantsi we-curve (lordosis) kunye namaqhinga adibeneyo emzimbeni, ngokuhamba kwexesha
- Ukuwa ngexesha lokuphazamiseka kwemisipha (kungabangela iingxaki ezongezelelweyo ezinxulumene nazo)
Ukuxilongwa kwe-Stiff Person Syndrome
Izimpawu zibonisa ukuxilongwa. Nangona kunjalo, ngenxa yokuba sisifo esiyintlekeleko, sinokuthi singaphathwa kakubi njengesifo se- Parkinson , i- multiple sclerosis , i- fibromyalgia , okanye ingxaki yengqondo.
Ukuxilongwa ngamanye amaxesha kunokuqinisekiswa ngobukho be-anti-GAD antibodies, okanye ezinye iindidi ze-antibodies xa i-syndrome idibene neentsholongwane ezithile.
Nangona kunjalo, iipesenti ezingama-35 zezigulane ezinesifo somntu onzima asinayo i-antibodies kwaye ayikho i-cancer edibeneyo.
Ezinye iimvavanyo zingenziwa, ezifana ne-hemoglobin A1C ukujonga isifo sikashukela okanye i-hormone ye-thyroid-stimulating (TSH) ukujonga i-thyroiditis. Ukuvavanywa kwamathambo (i-electromyography okanye i-EMG) inokwenziwa kwakhona.
Unyango lwe-Stiff Person Syndrome
Nangona kungekho nonyango lwe-syndrome yomntu onzima, kukho unyango olukhoyo. Izidakamizwa ezifana ne-azathioprin (i-Azasan), i-diazepam (iValium), i-gabapentin (i-Neurontin), i-tiagabine (i-Gabitril), okanye i-baclofen (i-Lioresal) ingasetyenziswa. Iimpawu kwii-cancer ezinxulumene zinokuphucula emva kokuba isisu sisuswe kwaye unyango lwe-steroid lunikezelwa. Ukutshintshiselwa kwePlasma (plasmapheresis) kunceda ukunciphisa iimpawu kwabanye abantu, kodwa olu unyango lugcinwa kulabo abasongela ubomi bokuphefumula. Kwabanye, i-immunoglobulin ene-intravenous (IVIg) iyanceda. Ulwaphulo lwangokwenyama lunokunceda ukukhulula iimpawu ezinxulumene nokuxhatshazwa kwemisipha ende, kodwa kungase kubangele ukuphazamiseka kwemisipha. I-Corticosteroids inokukunceda ngokunjalo, nangona kufuneka banikwe ngokucophelela abo abanesifo sikashukela.
Imithombo:
"Ikhasi leNkcukacha Yomntu onamaNINDS." Ngxaki. 14 uFebruwari 2007. I-National Institute of Neurological Disorders and Stroke. http://www.ninds.nih.gov/disorders/stiffperson/stiffperson.htm.
Rodgers-Neame, uNancy. "Umntu onamahloni." eMedicine. 20 uMatshi 2006. I-WebMD. http://www.emedicine.com/neuro/topic353.htm.
I-autoantibodies kwiprotheni ye-128-kd yesipapapheni kwintathukazi yabasetyhini abane-stiff-syndrome kunye nomhlaza wesifuba. AU iFolli F; Solimena M; Cofiell R; Austoni M; Tallini G; Fassetta G; Bates D; Cartlidge N; Bottazzo GF; Piccolo G; okqhubekayo. SO N Engl J Med 1993 Feb 25; 328 (8): 546-51
I-Heterogeneity ye-autoantibodies kwi-syndrome yomntu onzima. AU Grimaldi LM; Martino G; Braghi S; Quattrini A; Furlan R; Bosi E; Comi GSO Ann Neurol 1993 Jul; 34 (1): 57-64.
Isifo somntu osisigxina se-Steroid esiphendulayo: isifundo sekliniki kunye ne-electrophysiological yezifundo ezimbini. AU I-Piccolo G; Cosi V; Zandrini C; Moglia ASO Ital J Neurol Sci 1988 Dec; 9 (6): 559-66.