Ingxaki yoBongo iba Ngumntu Obulalayo
Isifo seCreutzfeldt-Jakob senza umxholo wonyaka ka-2000 xa kuqhutywe iziganeko ezibuhlungu e-United Kingdom. Ezi ziganeko zazixutywe ekudleni okujongene ne-bovine spongiform encephalopathy (BSE), isifo se-prion esibangela i-CJD eyahlukileyo, enye eyaziwa ngokuba yi "cow cow".
Uluntu unesizathu esihle sokukhathazeka ngokusasazwa kweBSE kubantu.
Isifo esichaphazelekayo seCreutzfeldt-Jakob, njengezinye iintlobo zesifo seCreutzfeldt-Jakob , siphuthuka ngokukhawuleza, sisifo esiyingozi sisifo segazi. Kodwa eso sifo asiqabile: Ukususela ngo-Oktobha 1996 ukuya kuMatshi 2011, kwaphela iingxelo ezingama-175 ze-vCJD e-United Kingdom, e-25 eFransi, e-5 eSpain, e-4 e-Ireland, e-3 nganye e-Netherlands nase-United States of America ( EU.SA), 2 nganye eCanada, e-Itali nasePortugal, kwaye enye ibe yiJapan, i-Saudi Arabia neTaiwan.
Amaziko okuLawula kunye nokuVimbela izifo (CDC) ihlola iziganeko e-United States kuzo zonke iintlobo zesifo seCreutzfeldt-Jakob.
Iintlobo ezahlukeneyo zezifo, zihlala zifa
Akukho naluphi unyango lweCreutzfeldt-Jakob, oluya kwenzeka kumntu ngeendlela ezintathu:
- Amaphesenti angama-10 ukuya kwe-15 amacala azuze ilifa, ngenxa yokuguquka komzimba.
- Uninzi lweziganeko zibonakala zibonakala ngokukhawuleza, kumntu ongenaso intsapho yembali yesifo.
- Ipesenti encinci yeemeko zenzeka ngentsholongwane, ngokuqhagamshelana nezifo zengqondo ezisulelekileyo. Kukho amaphepha aqoshiwe ayenzeka njengesiphumo esingalindelekanga senkqubo yonyango.
Isifo seCreutzfeldt-Jakob asixhomekeke kwiindlela eziqhelekileyo, njengokunyunyuzela okanye ukukhwehlela - ayikho imeko eyaziwayo yabatshati okanye amalungu omzimba omntu osulelekileyo obanjwe sisi sifo.
Iilwanyana eziNgcilisiweyo
Iziganeko zentsholongwane yeCreutzfeldt-Jakob zibonakala zidibene nokutya kwimveliso yenyama yenyama eYurophu. Isifo esifanayo, xa senziwa kwizimvu, sabizwa ngokuthi "shwa." Kukholelwa ukuba iimveliso zeegusha ezinesifo esilulelekileyo zisetyenziselwa ukondla kweenkomo, kwaye yileyo ndlela iinkomo ezitheleleke ngayo.
Iingcali zenzululwazi ziye zafumanisa ukuba oko kubangela ukuba i-BSE, i-scrapie, kunye nezifo ze-Creutzfeldt-Jakob ayinayo intsholongwane okanye ibhaktheriya njengakwezinye izifo, kodwa i-protein agent ebizwa ngokuba yi-prion. I-prion iguqula iiprotheni eziqhelekileyo zibe yintsholongwane, ezibulalayo.
Iziphumo kwiBrain
Ekubeni isifo seCreutzfeldt-Jakob sichaphazela ingqondo, iimpawu ezivelisayo ziyi-neurological. Inokuqala ngokuzenzekelayo ngokusileleka, ukudandatheka, ukudideka, ubuntu kunye nokuguquka kokuziphatha, kunye neengxaki ngememori, ukulungelelanisa kunye nokubona. Njengoko iqhubela phambili, loo mntu ukhula ngokukhawuleza kwaye akwazi ukuzibandakanya, ukunyakaza okungaqhelekanga okubizwa ngokuba yi-myoclonus.
Kwinqanaba lokugqibela lesi sifo, isigulane siphumelela yonke imisebenzi yengqondo kunye nomzimba, iphelelwa kwi-coma, ize ife. Inkqubo yesifo isoloko ithatha unyaka omnye. Esi sifo sithintela abantu phakathi kweminyaka engama-50 ukuya kwe-75, nangona kunjalo, isifo esifana nesifo se-Creutzfeldt-Jakob sichaphazele abantu abasebancinci-nakwiintsholongwane (iminyaka isukela kwiminyaka eyi-18 ukuya kuma-53 ubudala).
Kunzima ukuxilongwa
Akukho nto, njengangoku, ukuvavanywa kovavanyo lwezonyango oluchanekileyo lokufumanisa izifo zeCreutzfeldt-Jakob, kwaye ukuqinisekiswa kwesi sifo kunokwenziwa kuphela emva kokufa nge-autopsy. Ekubeni isifo singenqabile, abanye oogqirha abanako ukucinga njengento yokuxilonga kwaye bangaphulaphula iimpawu zezinye iingxaki zengqondo ezifana ne- Alzheimer's okanye i- Huntington . Iingcali zenzululwazi zibonisa ukuba uvavanyo olutsha, olusisigxina lokuvavanywa kwebhubhorari luya kukwazi ukubona iithayibhile kwigazi lomntu ogulayo.
Imithombo:
Collins, S., A. Boyd, A. Fletcher, MF Gonzales, CA McLean, CL Masters. "Ukuqhubela phambili kwimeko yokuqala yokuxilongwa kwesifo seCreutzfeldt-Jakob." J Clin Neurosci 7 (2000): 195-202.
"i-vCJD (i-Variutant Creutzfeldt-Jakob Disease)." NCIDOD. 29 Novemba 2006. Amacandelo okuLawula nokuLawula izifo. 28 Disemba 2006 http://www.cdc.gov/ncidod/dvrd/vcjd.
Ngaba, R., M. Zeidler, GE Steward, MA Macleod, JW Ironside, SN Cousens, J. Mackenzie, K. Estibeiro, AJ Green, R. Knight. "Ukuxilongwa kwintsholongwane entsha yeCreutzfeldt-Jakob." U-Ann Neurol 47 (2000): 575-582.
Wilson, K., iCode Code, M. Ricketts. "Ingozi yokufumana isifo seCreutzfeldt-Jakob ekumpontshelwa igazi: Ukuphononongwa ngokuchanekileyo kwezifundo zokulawula iimeko." BMJ 321 (2000): 17-19.