Iimvavanyo eziqhelekileyo zokuxilongwa kunye nokuba kutheni i-Diagnosis ilukhuni
Ekubeni iimpawu ze-idiopathic pulmonary fibrosis (i- IPF ) zifanisa ezo zintliziyo kunye neemeko zamaphaphu, ngokuqhelekileyo kuthatha ixesha elide lokuxilonga lesi sifo. Ngeli xesha lexesha, ngokuphindaphindiweyo unyaka okanye ezimbini, izigulane zihlala zibona oogqirha abaninzi bezama ukufumana isizathu seempawu zabo.
Iimpawu eziqhelekileyo ze-IPF
Njengayezinye izifo zamaphaphu, njengeCOPD, kukho umonakalo omkhulu emiphakeni ngaphambi kokuba iimpawu zivele.
Ezi zimpawu zingabandakanya:
- Ukuphefumula , ngokukodwa ngomsebenzi, ngokuqhelekileyo kuyimpawu zokuqala. Ngethuba le nkinga yokuphefumula ibuhlungu kangangokuthi ukuphefumla okufutshane kuyenzeka nakwiindawo zokuphumla.
- Ukukhwehlela okuqhubekayo okuqhelekileyo kumile (okungenayo ukuvelisa)
- Ukungcoli, ukuphefumula ngokukhawuleza
- Ukukhathala
- Ukulahlekelwa isisindo ngaphandle kokuzama ( ukulahlekelwa kwesisindo esingachazwanga )
- I-Clubbing - I-Clubbing yimeko apho iminwe neenzwane zikhuliswa khona ekupheleni, zifana ne-spoon-down down.
- Iimpawu zeMiscle kunye kunye
Ukuhlola i-IPF
Okwangoku, akukho vavanyo lokuhlola i-IPF, kwaye ukuxilongwa kusekelwe kubantu ababonisa iimpawu. Inkqubo yokujonga umdlavuza wemiphunga , nangona kunjalo, inokuthabatha i-IPF kubantu ukuba ngubani ovunywayo kwaye avunywe.
Ukuxilongwa kunye nokuThengisa
Ukuxilongwa kwe-IPF ngokuqhelekileyo kuthatha ixesha elithile, kunye nabantu abaninzi abahamba unyaka okanye amabini kwaye bebona oogqirha abaninzi ngaphambi kokuxilongwa.
Isizathu salokhu kukuba iimpawu zokuqala ze-IPF zilinganisa ngokuthe ngantoni nakwezinye iimeko ezininzi, kuquka isifo senhliziyo. Abantu abaninzi banokuphelelwa kwintliziyo ebanzi ngaphambi kokufunyaniswa ngokusekelwe kwimpawu eziqhelekileyo zokuqala.
Ezinye iimvavanyo ugqirha wakho unokuyalela ziquka:
- I-CT yesisombululo esiphezulu: I- IPF idla ngokuxilongwa ngokusekelwe kwiziphumo eziqhelekileyo ezibonwe kwi-CT yesisombululo esiphezulu se-chest. Kwi-CT scan, i-fibrosis ibonakala kwiyiphi i-radiologist ebhekisela kumzekelo we-honeycombed.
- I-biopsy ye-Lung: Kukho amaxesha apho i-scan kuphela yodwa ingakuqinisekisa ukuxilongwa kwe-IPF, kodwa ukuba ukuxilongwa kubhekene nombuzo we- lung biopsy kunokucetyiswa . Oku kunokwenziwa njengenxalenye ye-bronchoscopy, ngokufakela encinci kwisifuba (thoracoscopy) okanye nge-thoracotomy. I-biopsy yenziwe ngokuyinhloko ukulawula ezinye izizathu ezinokubangela izifo zemiphunga ezifana nomhlaza wemiphunga okanye i-sarcoidosis.
- Ezinye iimvavanyo ezinceda ekuxilongweni nasekuxhaseni: Ukuhlanganiswa kovavanyo kunye nezinye iimvavanyo zenziwa rhoqo zombini ukuncedisa ukuxilongwa, ukuchonga indlela imiphunga esebenza ngayo, kunye nokubona ukuba isifo sele siphumelele kangakanani. Ezinye zezi ziquka:
- Imbali kunye novavanyo lomzimba.
- I-Spirometry - i-Spirometry yinto yokuvavanywa ejongene nendlela umoya okhutshwa ngayo ngamandla ngethuba lesibini, kwaye luphawu lomsebenzi wamaphaphu.
- Ezinye iimvavanyo zomsebenzi wamapulmoni
- Oxyetry
- Iigesi zegazi ezijikelezayo - zombini i-oximetry kunye ne-ABG zenziwa ukuvavanya umxholo we-oksijini wegazi.
- Ukuvavanya isifo sofuba
- Iimvavanyo zegazi - Uphando lukhangele kwiimveliso eziza kunceda ukufumana isifo kwixesha elizayo.
I-Genetic Predisposition: Idiopathic pulmonary fibrosis ingaqhutyelwa kwiintsapho kunye nezinguquko ezithile (kwi-chromosome 11) zifunyenwe ziqhelekileyo kwi-IPF yohlobo.
ILizwi
Ingaba iimeko ze-IPF zithatha ixesha elithile ukuxilonga, xa sele ufumanisa ukuba unakho unyango olukhoyo, kwaye uphando luye lwaphuhliswa . Kanye nokulawula izinto ezithile zokuphila, unokuqhubeka nokuphila kakuhle ne-idiopathic pulmonary fibrosis .
> Imithombo:
Antoniou, K., Tomassetti, S., Tsitoura, E., noCancheri. Idiopathic pulmonary fibrosis nomdlavuza wamaphaphu: ukuhlaziywa kweklinikhi kunye ne-pathogenesis. Iingcamango zangoku kwiMithi yePulmonary . 2015 Sep 18. (Epub ngaphambi kokuprinta).
kaBoer, K., noJee Lee. Ukungabonakali kwamandla angaphantsi kwe-idiopathic pulmonary fibrosis: ukuhlaziywa. Ukuhlaselwa . 2015 Sep 13. (Epub phambi kokuprinta).
Oldham, J. et al. I-TOLLIP, i-MUC5B kunye neempendulo ku-N-acetylcystein Phakathi kwabantu ngabanye abane-Idiopathic Pulmonary Fibrosis. I-American Journal ye-Respiratory and Critical Care Medicine . 2015 Sep 2. (Epub phambi kokuprinta).
O'Riordan, T., Smith, V., kunye noG. Raghu. Ukuphuhliswa kweeNvevel Agents ze-Idiopathic Pulmonary Fibrosis: inkqubela phambili ekukhetheni okujoliswe kuyo kunye nokuqulunqwa kwesilingo. Esifubeni . 2015 Meyi 8. (Epub phambi kokuprinta).
Raghu, G. et al. Ukuxilongwa kwe-idiopathic pulmonary fibrosis ene-CT-resolution solution kwizigulane ezinobungqina obuncinane okanye obungenasifo se-radiological of honeycombing: uhlalutyo lwesekondari lolu vavanyo olulinganisiweyo. I-Lancet yeMicrosoft Respiratory Medicine . 2014. 2 (4): 277-84.