Yintoni i-IPF kunye Neyintoni Eyibangela?
Ukuba wena okanye othandekayo sele ufumene i-idiopathic pulmonary fibrosis (i-IPF), yazi ukuba bambalwa abantu abaqhelene nesi sifo. Ukuba uqala ukukhangela ulwazi oludala kwi-IPF, awunakufumana iindaba ezilungileyo. Kuze kubekho u-2014 kwakungekho naluphi na unyango olukhoyo oluye lwabahluko omkhulu kubantu abaphila nesi sifo. Ngomdla, utshintsha-ngoku kukho ukunyangwa kwesi sifo esiphucula ubomi.
Yintoni i-Idiopathic Pulmonary Fibrosis (IPF)?
IPF yindlela eqhelekileyo yeqela lezifo ezibizwa ngokuba yi-idiopathic interstitial pneumonia. I-interstitial ithetha ukuba imeko ukuba ikhona kwimimandla yamaphaphu phakathi kwe-alveoli (iibhasi ezincinci zomoya ekupheleni komthi wokuphefumula apho utshintshi lwe-oxygen ne-carbon dioxide lwenzeka) kunye nakwii-alveolar linings. UFibrosis uthetha nje ukutyhalwa. Yiyo yokutshatyalaliswa kwindonga e-alveolar kunye nezicubu eziphakathi kwazo eziphazamisa amandla oksijini ukuba adlule kwiindonga ze-alveoli kunye negazi.
Kwixesha elidlulileyo, bekucingelwe ukuba i-IPF yayiyinkqubo yokuvuvukala. Ngoku kucinga ukuba iqala ngomonakalo emiphakeni evela kumxube wemithombo, ilandelwa ukuphulukiswa okungavamile-fibrosis.
Ukucinga ukuba le nto ifana nani, cinga ukuba unqunywe ngesikhumba sakho esiphilisa ngophawu. Kubantu abaninzi, ukusika kunophilisa ngomgca obomvu oguquka umhlophe ngexesha.
Kwamanye abantu, ulusu luyamphulukisa ngokwemvelo, luye lwashiya ulwaphulo oluqinileyo nolunengqondo . I-fibrosis kwi-IPF iyafana nale ndlela yokutshatyalaliswa, kodwa ingabonakali ngaphandle komzimba.
Ukongezelela ekubeni sisifo esiqhubekayo, iipesenti ezilishumi zabantu abane-IPF kulindeleke ukuba benze umhlaza wamaphaphu.
I-IPF ifana njani?
Amanani ayahluka xa ebheka iziganeko ze-idiopathic pulmonary fibrosis, kodwa isivumelwane kukuba imeko ayifumananga; abaninzi abantu banokuba ne-IPF kwaye bafumanisa ukuba banesinye imeko, okanye badlulile ngaphambi kokuba ufumane ukuxilongwa ngokufanelekileyo.
Ngokusekelwe kuhlalutyo olulodwa eUnited States, kwafunyanwa ukuba iziganeko (inani labantu abaxilongwa rhoqo ngonyaka) lwe-IPF laliyi-58.7 ngabantu abayi-100,000. Kwesifundo esithile se-2011, kwafunyanwa ukuba ukusabalalisa (inani labantu abaphila nesifo) se-IPF kwakuyiimeko ezingama-495.5 kwi-100 000 abaxhamli be-Medicare. (Isifo esingaqhelekanga sichazwa njengelinye apho ngaphantsi kwe-1 kuma-50,000 abantu isifo. Ngoko, i-IPF ayiqhelekanga, kodwa ayinqabile.)
Ukujonga abantu abafayo ukusuka kwi-IPF ukuqikelela kwabikezela ukuba abantu abayi-13 000 ukuya kwi-17,000 baya kufa kwi-IPF e-United States ngo-2014 kwaye phakathi kwabantu abangama-28,000 no-65,000 baya kufa eYurophu. Ukubeka oku ngolu hlobo, abantu abangama-40,000 bafa ngomdlavuza wonyaka ngamnye eMelika, okwenza i-IPF ibe yimbangela ebalulekileyo yokugula nokufa.
Ngubani Ofumana IPF? Izizathu kunye neengozi
Ayaziwa oko kubangelwa i-IPF, ngoko ke igama elithi "idiopathic," elithetha ukuba "asiyazi isizathu." Oko kwathiwa, kukho iingozi ezibangelwa abantu kwisifo.
Ezinye zezi ziquka:
- Ubudala - i-IPF isoloko ifunyaniswa kubantu abadala kunye nabadala.
- Ukutshaya - malunga nama-60 ekhulwini abantu abaphuhlisa i-IPF banomlando wokutshaya.
- Izifo ezinjenge-Viral ezifana ne- Epstein-Barr virus , ebangela i-mononucleosis.
- Ubume bokusingqongileyo kunye nokusebenza.
- Isifo se-reflux se-Gastroesophageal (GERD) - Uninzi lwabantu abaxilongwa nge-IPF banomlando weGERD ngokugquma.
- Imbali yentsapho (i- genetic predisposition ) - I-IPF isebenza kwiintsapho kwaye utshintsho oluthile lwezityalo lubonakala landisa ingozi.
Kukho izizathu ezininzi eziyaziwayo ze-pulmonary fibrosis, ezinjenge-radiation kunye namayeza, kodwa ezi ngcaciso aziyi kuhlulwa phantsi kwe-fibrodium ye-idiopathic.
ILizwi
Ngenxa yezizathu ezingaziwa, ukufa okuvela kwi-IPF kubonakala ngathi kwanda emhlabeni jikelele. Ngexesha elifanayo, uphuculo olutsha kunye nophuculo oluphuhliswayo njengoko uphando olu sifo luqhubeka . Emva kokuxilonga , kwaye ugqirha wakho kufuneka asebenzisane ukuze athole ukhetho lwenyango olusebenza kwimeko yakho. Kukho iintlobo ezahlukeneyo zonyango ezikhoyo, kwaye ezinye izigulana ziba ngabaviwa be-transplant. Ukongezelela, amaqela enkxaso afumaneka apho ungakwazi ukudibanisa nabanye kwaye ufunde iindlela zokuphila kangcono naphezu kokuba ne-IPF. Ekugqibeleni, indima yakho esebenzayo kwinkathalo yakho yezempilo ingenza umehluko, naye.
> Imithombo:
Antoniou, K., Tomassetti, S., Tsitoura, E., noCancheri. Idiopathic pulmonary fibrosis nomdlavuza wamaphaphu: ukuhlaziywa kweklinikhi kunye ne-pathogenesis. Iingcamango zangoku kwiMithi yePulmonary . 2015 Sep 18. (Epub ngaphambi kokuprinta).
Ghebremariam, Y. et al. Impembelelo yePleiotropic yeproton pump inhibitor esomeprazole ekhokelela ekunciphiseni ukuvuvukala kwemiphunga kunye ne-fibrosis. Umbhalo weMicrosoft Medicine . 2015. 13: 249.
Hutchinson, J., McKeever, T., Fogarty, A., Navaratnam, V., no R. Hubbard. Ukwanda kwehlabathi jikelele kwi-idiopathic pulmonary fibrois kwiminyaka engamashumi amabini anesixhenxe. Amanqaku e-American Thoracic Society . 2014. 11 (8): 1176-85.
Idiopathic Pulmonary Fibrosis Uphando lweeNtsholongwane, uMartinez, F., deAndrade, J., Anstrom, K., King, T., noG. Raghu. Uvavanyo lwe-acetylcysteine kwi-idiopathic pulmonary fibrosis. I-New England Journal of Medicine . 2014. 370 (22): 2093-101.
Spagnolo, P., Maher, T., noL. Richeldi. Idiopathic pulmonary fibrosis: Ukuqhubela phambili kwindlela yokwelapha i-pharmacological. Pharmacology & Therapeutics . 2015. 152: 18-27.