Ukuxilongwa ngokuhlukileyo kocwiliso lobuso kunye ne-Mastocytosis
Ukuba ujamelana nesifo se-episodic ukuxhamla ungacatshungulwa ukuba kunzima kangakanani ukufumana uxilongo. Yintoni enxulumene nokutshatyalaliswa komzimba kumastocytosis onjengaye kwaye zeziphi ezinye zeemeko ezingenokuba yimbangela yezibonakaliso zakho?
Inkcazo
Iiseli ezincinci iiseli zamasosha omzimba atholakala kwimida yegazi kwesikhumba, umzila wesisu, isifo sokuphefumula kunye nephepha le-genitourinary.
Ziqulethe i-granules yezinto ezininzi, ezona ziqhelekileyo zazo zi- histamine . Ezi granules zikhutshwa ngokuphendula ukudibanisa nezinto ezithile zangaphandle. I-Histamine, ibangela ukuba ezininzi iimpawu ezilinganayo neempembelelo, ezifana ne-chechy, amehlo ename kunye neentsontsho kunye nokuqiniswa kwe-airways emiphakeni yethu.
I-Mastocytosis yimeko apho kukho inani eliqhelekileyo kunamanani eesisitye esisisigxina kwiisishu. Lezi zitshixo zesikhumba zibangela impendulo yesikhumba ebizwa ngokuba yi-urticaria pigmentosa (imihlathi) ngokukhawuleza emva kokugubha isikhumba ngento ephikisayo.
Izibonakaliso zokuPhukisa ubuso
Ukuhluthwa kweso siqu nge mastocytosis ngokuqhelekileyo kuza ngokukhawuleza. Eyona nto ibonakala kakhulu ebusweni nasemzimbeni omkhulu kwaye ingaba ne-bumps brown-brown. Ubuso ngokuqhelekileyo buba bubomvu kwaye bushushu kwaye bube bunzima kakhulu (i-pruritic.) Kungathi uzive ngathi utsha okanye uvutha umlilo.
utshintsho kwigazi lokuhamba
Ezinye izibonakaliso ngeMastocytosis
Ukongeza kwi-flushing facial, abantu abane-mastocytosis bahlala bebona iimpawu kuwo wonke umzimba wabo obangelwa ukukhululwa kweemali ezinkulu ze-histamine okanye ezinye iikhemikhali. Ezinye iimpawu ziquka:
- Iipilpitations
- Uxinzelelo lwegazi oluphantsi
- Iintlungu zesifuba
- Uhudo olushushu
- Isihlunu kunye nokuhlanza
- Intlungu zesisu
- Ukukhathala
Abacebisi
Abantu abaninzi abane-mastocytosis abakwazi ukuchonga iziganeko ezibangelwa ukuqhuma, kodwa abanye abantu baye bafumanisa ukuba ukusetyenziswa, ukushisa okanye ukuxhalaba kungabangela.
Amachiza afana ne-opioid narcotics afana ne-morphine kunye ne-codeine, kunye ne-aspirin okanye ezinye izidakamizwa ezingekho-steroidal ezichasayo ezifana ne-ibuprofen okanye i-naproxen nazo zingaqalisa ukuhlaselwa.
Ukuxilongwa
I-Mastocytosis inokuba nzima ukuyixilonga kwaye inokuyenza inkxalabo. Ukuchonga ngokuchanekileyo iimpawu zeempawu zonyango kwi-diagnostic. Ngamanye amaxesha izilonda zesikhumba kunye ne- bone marrow ziyi-biopsied kwaye umchamo uhlolisise amazinga okwandisa amachiza aqulethwe kwiiseli zesigxina.
Ukuxilongwa kwenziwa lula kubabo abane-classic urticaria pigmentosa, kodwa kusenokuba ngumngeni. Kusenokukrokra xa abantu benento ebonakala ngathi iyingozi yokuphendula ngaphandle kokungena kuzo naziphi na izilwanyana ezibonakalayo okanye ukuba umntu uhlakulela inambuzane enobungozi obukhulu kakhulu be-anaphylactic reaction.
Ezinye izizathu ezinokwenzeka
Njengoko kuphawuliwe, i-mastocytosis ingaba nzima kakhulu ukufumanisa iziphumo zombini ngenxa yempawu ezininzi (ezinokubangelwa ziinkalo ezahlukeneyo) kwaye ngenxa yezinye izizathu ezibangelwa ukutshatyalaliswa kweso.
Ezi zizathu ezinye ziba yinto ekhethiweyo yekliniki (isifo sonke sodwa) okanye endaweni yenye imeko okanye izifo. Ezinye iimeko ezinokubangela ukugqithisa kweso saso eyingxenye yokuxilongwa ngokungafaniyo kubandakanya:
- Xha ga mshelana
- I-Photodermatitis - iRash ukusuka ekuphumeni kwelanga
- Rosacea
- Ukutshisa kwe-Menopausal
- Ulwaphulo lweziyobisi
- Isifo sentliziyo
- I-Carcinoid syndrome - Ukutshatyalaliswa ebusweni kwi-carcinoid syndrome kunokubonakala kufana neyo nge-mastocytosis kwaye ibangelwa yimichiza ekhutshwe yi-tumor
- Pheochromocytoma
- I-Cushing syndrome
- Anaphylaxis
- Ezinye izicubu ezifana ne-medullary carcinoma ye-thyroid, isifo se-iscoratic islet, kunye ne-renal carcinoma (umhlaza wesifo.)
Unyango
Kukho iindlela ezininzi zokonyango kwi-mastocytosis kuye kuxhomekeke kwiimpawu eziphambili. Unyango luquka:
- Antihistamines
- I-Aspirin kunye ne-non-stroidal anti-inflammatory drugs ezifana ne-Advil (ibuprofen) - Nangona kwabanye abantu la mayeza angabangela ukuba
- I-Cromolyn sodium - i- Cromolyn yintlanzi yesitampu eselunxwemeni ngamanye amaxesha isetyenziswe kunyango lwe-asthma
- Iimpawu ze-steroid
- I-PUVA. (Photochemotherapy)
Ngaphantsi kwindlela yokucubungela ubuso kunye ne-Mastocytosis
Ingaba ufunyanwe ukuba unesifo se-mastocytosis njengento ebangela ukutshatyalaliswa kweso sigqirha okanye ugqirha wakho uthe u-mastocytosis ungenye yezizathu ezibangelwa iimpawu zakho, mhlawumbi uvakalelwa kakhulu ngenxa yokwesaba. Qhubeka ubuza imibuzo kwaye ube ngummeli wakho ekunyamekeleni kwakho. Ukufumana ukuxilongwa kwaye ekugqibeleni unyango lunokuthatha ixesha. Ukuba awufumani iimpendulo, cinga ukufumana umbono wesibini.
Ukuphazamiseka okunjenge-mastocytosis (kunye nezinye iimeko kwi-diagnostic differentiation) aqhelekanga, kwaye akuwona wonke ugqirha oye wabona ukuphendulwa kweklasi. Oko kwathiwa, sifunde okuninzi malunga nale miqathango kwiminyaka yamuva nje ngokuba ukuqonda kwethu kwindlela yokuzivikela komzimba kunye ne-endocrine. Ekubeni le miqathango iyabunqabile ukuba akunakwenzeka ukuba unamaqela okuxhasa endaweni yakho, kodwa uluntu lwenkxaso yoluntu luvumela abantu ukuba baxhumane nabanye abajongene nemingeni efana nehlabathi jikelele.
Imithombo:
Gulen, T., Hagglund, H., Dahlen, B., noG. Nilsson. I-Mastocytosis: I-Spectrum Spectrum Spectrum kunye neNtsholongwane yokuThengisa izifo ze-Enigmatic Disease. Umbhalo weMithi yoPhakathi . 2016. 279 (3): 211-28.
UHana-Shmouni, F., Stratakis, C., kunye noKoch. Ukuqhuma kwi-Neuro (Endocrinology). Iingxelo kwi-Endocrine kunye neengxaki zeMetabolic . 2016. 17 (3): 373-380.
Ikizoglu, G. Ubuso obomvu obubuyiselwe kwakhona: Ukutshiza. Dermatological Clinic . 2014. 32 (6): 800-8.