I-Eosinophilia-myalgia syndrome (EMS) yintlupheko engaqhelekanga ebangela ukuvuvukala kwiindawo ezahlukeneyo zomzimba kubandakanya izihlunu, isikhumba kunye nemiphunga. I-EMS ibangela amanqanaba aphezulu eeseli ezimhlophe zegazi ezaziwa njenge-eosinophil. Ezi i- eosinophil zakha ngaphakathi komzimba kwaye zingabangela iingxaki ezinzulu.
I-EMS yaqale yaqaphela ngo-1989 xa abathathu abafazi baseNew Mexico bafuna unyango lwezonyango ezifanayo.
La mabhinqa aye athathwe uphawu olufanayo lwezempilo, uL-tryptophan, okwenzekile. I-tryptophan yinto eyenzeka ngokwemvelo ekudleni (njenge-turkey). Isixa se-L-tryptophan esiyifumana ekudleni sininzi kakhulu kunomlinganiselo okhoyo ekutya kwethu. Inani elikhulu le nkunkuma lenziwe njengezongezelelo. Nangona kwakungekho ubungqina bobunzululwazi, abanye abantu bathi uL-tryptophan ingayiphatha ngokuphumelelayo ukuxinezeleka, uxhalaba, isifo se-premenstrual, kunye nokulala. I-try-to-counter L-tryptophan ivaliwe ngo-1990 emva kokuba amawaka ayechaphazeleka yi-EMS.
Iimeko ze-EMS ziye zaxelwa ukuba azixhumene nokuthatha i-L-tryptophan. Nangona kunjalo, inani lamatyala e-EMS liye lahla kakhulu ngenxa yokugqibhuka kwe-1989 kunye ne-L-tryptophan ekhutshwe kwiimarike. Inombolo ecacileyo yeemeko ze-EMS aziwa. Nangona, kuqikelelwa ukuba naphi na abantu abayi-5 000 ukuya ku-10 000 banesifo.
Uninzi lwamatyala lwabikwa kubomama baseMerika; nangona kunjalo, i-syndrome ibiwe eJamani, eCanada, nase-United Kingdom.
Iimpawu ze-EMS
Uphawu olubunzima kakhulu lwe-EMS luyabalaliswa, ubuhlungu obukhulu beentlungu eziba nzima kakhulu ngaphezu kweeveki kwaye zingabangela ukuba i- muscle spasms . Iimpawu zivame ukuqala ngokukhawuleza kunye nobubanzi ukusuka kumncinci ukuya kunzima.
Le meko inokubangela iingxaki zokusongela ubomi kwaye ibe yingozi.
Esi sifo sidlula kwizigaba - ezinzima kunye ezingapheliyo. Izigaba zithetha ezininzi iimpawu eziqhelekileyo kuquka intlungu yesisu kunye nokukhathala. Isigaba esiqatha siza kuqala kwaye sinokuhlala phi phakathi kweenyanga ezintathu nantandathu. Iimpawu eziqhelekileyo zesigaba esiqhekezayo iinguqulelo zesikhumba kunye nentlungu yesisu kwiingalo nasemilenzeni. Ulusu lwabo bachaphazelekayo lunokuba lukhube, lukhuphe, okanye lube lukhuni njenge-eosinophilic fasciitis).
Ngethuba lesigxina esingapheliyo, iimpawu zibonakala zikhupha. Baya kusebenzela ixesha elide baze baxolele. Izimpawu ziquka:
- Ukuvuvuka kweengalo nemilenze, ngamanye amaxesha ubuso
- Intlungu ehlangeneyo
- Ukugqithisa kancinci kwesikhumba
- Ukukhwehlela nokuphefumula okufutshane
- Ukukhathala
- Fever
- Ukulahleka kweenwele ezisezantsi ( alopecia )
- Imiba ye-Bladder
- Utshintsho lwendlela yokuziphatha (ukuguquka, ukuguquka kwemizwelo)
- Ubunzima bokuqonda (iingxaki zememori, inkathazo ekugxilwe kuyo)
- Imiba ye-digestive (isicupunu, ukuhlanza, ukunyanzelisa)
- Intliziyo engaqhelekanga (ukuvuvukala, intliziyo engavumelekanga)
Imiba yokugaya kunye neyomzimba iyakwenzeka kakhulu xa isigaba esingapheliyo sesimo. I-EMS ngamanye amaxesha ayifumanwanga kakubi njenge- fibromyalgia , isifo esingapheliyo sokugula , i-lupus erythematosus, okanye i- arthritis .
Ukunyanga i-Eosinophilia-Myalgia Syndrome
Akukho nonyango ye-EMS, ngoko unyango lujolise ekunciphiseni iimpawu. Abo bane-EMS banokumiselwa ukusilalisa imisipha kunye neentlungu zokuxhoma. I-Prednisone inceda abantu abathile, kodwa kungekhona bonke. I-EMS iyigulo esingapheliyo (ixesha elide) ukugula. Kuhlolisiso lwabantu abangama-333 abane-EMS, iipesenti ezi-10 kuphela zichaze ngokuzifumana ngokupheleleyo emva kweminyaka emine ngesifo.
Imithombo:
Nasef, S., & Lohr, K. I-Fasciitis Eosinophili. eMedicine Journal, Vol. 3 No. 5.
Sairam, S., & Lisse, J. Eosinophilia-Myalgia Syndrome. eMedicine Journal, Vol. 3 No. 1.
IShiel, i-WC i-Eosinophilic Fasciitis (i-Shulman's Syndrome). LweMicrosoftNet.