Isalathisi saseBrith kwindonga yesisu
I-Gastroschisis yintsilelo yokuzalwa apho umntwana uswelelwa khona okanye onke amathumbu akhe ngaphandle kwesisu ngenxa yokuvula okungavumelekanga kwisisu esiswini. Ukuvula kungabalwa ukusuka kumancinci kuya kumakhulu, kwaye kwezinye iimeko, ezinye izitho ziyakwazi ukuqhubela phambili kumngxuma.
Oomama abancinci abasebenzisa iziyobisi zokuzonwabisa emva kokukhulelwa okanye abatshayo banomngcipheko ophezulu wokuzalwa nosana ozalwa ne-gastroschisis, kodwa kwiimeko ezininzi, awaziwa yintoni ebangela i-disorder.
Kukho ubungqina bokuba i-gastroschisis inokufumana ilifa kwi- autosomal pattern .
Malunga ne-1 kwi-5 000 iintsana zaseUnited States zizalwe nge-gastroschisis, nangona uphando lubonisa ukuba inani lamatyala e-gastroschisis landa bobabini e-US nakwihlabathi jikelele. Ingxaki ichaphazela iintsana kuzo zonke iintlanga.
Gastroschisis Izimpawu kunye nokuxilongwa
Ukuvavanya igazi lomama okhulelwe nge-alpha-fetoprotein (AFP) liza kubonisa izinga eliphezulu le-AFP ukuba i-gastroschisis ikhona. Ingxaki ingafumaneka kwakhona nge-ultrasound yesisu. Iintsana ezine-gastroschisis zivame ukuvula u-5 cm evulekileyo kwisigxina sesisu esisecaleni lomtya. Ngokuqhelekileyo inxalenye enkulu yamathumbu amancinci iphuma ngaphandle kwesi sivulo kwaye ilala ngaphandle kwesisu. Kwezinye iintsana, intumbu enkulu kunye nezinye izitho nazo ziza kuvula.
Iintsana kunye ne-gastroschisis ziba nesisindo sokuzalwa esincinane okanye zizalwe kungekudala.
Basenokuba nezinye iziphoso zokuzalwa ezinjengamathumbu angaphantsi, okanye i-gastroschisis inokuba yinxalenye yesifo somzimba okanye isifo.
Ukunyanga iGastroschisis
Amaninzi amaninzi e-gastroschisis anokulungiswa. Udonga lwamathumbu luyolule kwaye okuphakathi kwamathumbu kubhalwe ngaphakathi ngobumnene.
Ngamanye amaxesha utyando alukwazi ukuyenza ngokukhawuleza kuba amathambo avuvukile. Kule meko, amathumbu ahlanganiswe ngesikhwama esikhethekileyo de ukuvuvukala kwehla ngokwaneleyo ukuze bakwazi ukubuyiselwa ngaphakathi emzimbeni.
Emva kokuba amathumbu abuyele ngaphakathi emzimbeni, nayiphi na enye into engaqhelekanga inokuphathwa. Kuthatha iiveki ezimbalwa ukuba amathambo aqale ukusebenza ngokuqhelekileyo. Ngaloo xesha, umntwana usondla nge-vein (ebizwa ngokuba ngumthamo we-parenteral isondlo). Ezinye iintsana ezizalwe ne-gastroschisis ziphuluke ngokupheleleyo emva kokuhlinzwa, kodwa ezinye zi novelisa iingxaki okanye zifuna iifomula ezikhethekileyo zokutya. Indlela umntwana ayenzayo ngayo ixhomekeka kuyo nayiphi na ingxaki yamathumbu emathunjini.
Inkxaso yeGastroschisis
Amacandelo amanxaso amaninzi kunye nezinye izixhobo ezikhoyo zinokukunceda ekukhathazekeni kwengqondo kunye nemali yokuthwala umntwana kunye ne-gastroschisis. Ezi ziquka:
- Ama-Mothers Of Omphaloceles (ii-MOO) - Iqela leNkxaso ye-Omphalocele kunye ne-Webring
- I-Avery's Angels Gastroschisis Foundation - Inika inkxaso nenkxaso yemali kwiintsapho ezinabantwana abazalwa ne-gastroschisis
- IBDIS - Ulwazi lweeNkcukacha zeNkcukacha zeNkcukacha zoLwazi lweNkcukacha zoLwazi kwiGastroschisis kunye ne-Omphalocele.
- NgoMatshi weDimes - Abaphandi, amavolontiya, ootitshala, abasebenzi bokufikelela, kunye nabameli basebenza kunye ukunika bonke abantwana ithuba lokulwa
- Uphando oluzalwayo lokuzalwa kwabantwana - inkonzo yokunxibelelana kwabazali edibanisa iintsapho ezinabantwana abaneziphene zokuzalwa ezifanayo
- IzeMpilo zeNtwana - ulwazi olumkelwe ngogqirha ngempilo malunga nabantwana ukususela ngaphambi kokuzalwa ngokukhula
- I-CDC - Iingxaki zokuzalwa - uMnyango wezeMpilo kunye neNkonzo zoLuntu, amaziko okuLawula nokuLawula izifo
- I-NIH - I-Ofisi yezifo eziqhelekileyo - iNational Inst. lezeMpilo - iOfisi yeZifo eziPhezulu
- Inethiwekhi Yonyango YaseNtshonalanga YaseMntla yaseMelika - i-NAFTNet (iNethiwekhi yaseThekwini yaseNorthern American Fetal Therapy) yintlangano yokuzithandela yamaziko enyango e-United States naseKhanada ngokuqinisekileyo ekutyunjeni komntwana kunye nezinye iindlela zokunakekelwa kweengxaki ezahlukeneyo ze-fetus.
Umthombo:
"Gastroschisis." Isiko seNtsholongwane yokuThola kunye neNyango. Isibhedlele Sezingane SeFiladelphia. 26 uAgasti 2008
UYang, uPing, uTerri H. Beaty, uMa J. Khoury, u-Elsbeth Chee, uWalter Stewart kunye noLeon Gordis. Uphando lwe-genetic-epidemiologicalic of omphalocele kunye ne-gastroschisis: Ubungqina bokuba i-heterogeneity. " I-American Journal ye-Medical Genetics 44 (2005): 668 - 675.