Lo mntu unokuthi unokubeka engozini yegazi
I-Lupus anticoagulant (LA) yi-antiphospholipid antibody etholakala kubantu abaninzi abane-lupus. I-anupoagulant ye-Lupus yandisa amandla egazi lakho lokuvala. Ngoko ke, ukuba unalowo unqandwa ngumntu, unomngcipheko omkhulu wokufumana i- clot yegazi . Awudingi ukuba ne-lupus ukuba ube ne-LA.
Ngokutsho kwe-Johns Hopkins Centre ye-Lupus, ii-antiphospholipid antibodies zi-antibodies ezibhekiswe kuzo:
- Iimbumba zeembrane ezibizwa ngokuba yi-phospholipids
- Iiprotheni ezithile zegazi ezibopha nge-phospholipids
- Iinkomfa ezibunjwa xa iiprotheni kunye ne-phospholipids zibopha
Phantse ama-50 ekhulwini labantu abane-lupus bane-antibospholipid antibodies. Ama-antibospholipid antibodies aphazamisa umsebenzi oqhelekileyo wemithambo yegazi kwaye inokukhokelela ekunciphiseni imithwalo yegazi okanye iimbambo zegazi. Ezi nkxalabo zingakhokelela ekubetheni , ukuhlaselwa yintliziyo, nokukhulelwa kwesisu.
Akusoloko ihambisana neLupus
I-antiphospholipid antibody lupus anticoagulant yafunyanwa okokuqala kwizigulane ze- lupus erythematosus kwizi -1940. Namhlanje, oogqirha baqonda ukuba i-LA iphinda ivele kubantu abanezinye izifo ezizimele (ezifana nesifo sovuba), izifo ezithile kunye nezidumbu, kunye nabantu abathatha imithi ethile, kuquka i-phenothiazines, i-phenytoin, i-hydralazine, i-quinine, okanye i-antibiotic amoxicillin .
Igama le-lupus anticoagulant lidukisa kuba libonisa ukuba umntu olwa ne-antibody ukwanda kwegazi.
Enyanisweni, i-lupus anticoagulant inceda igazi ukuba livale. Enyanisweni, malunga neepesenti ezingama-50 zezigulane ze-lupus ezine-lupus anticoagulant ziya kuba ne-blood clot kwiminyaka engamashumi amabini anesithuba, okwenza ubukho bokuba ngumntu onobungozi bungozi.
Ukuba unayo i-lupus anticoagulant, kufuneka uqaphele ngakumbi iimpawu kunye neempawu ze-clot yegazi kuquka:
- Ukuvuvuka komlenze okanye ubomvu
- Ukuqhawukelwa ngumphefumlo
- Ubunzima, ubunzima, kunye ne-pallor kwisandla okanye umlenze
Uvavanyo lweLupus Anticoagulant
Iimvavanyo ze-Coagulation, ezilinganisela ukuba kuthatha ixesha elingakanani igazi ukuba livale, zisetyenziselwa ukubona i-lupus anticoagulant. Oogqirha baphatha izigulane ze-lupus zivame ukuqala ngolu vavanyo lwe-coagulation olubizwa ngokuba yi-thromboplastin time (activated partial thromboplastin time).
Ukuba iziphumo ze-aPTT ziqhelekileyo, oogqirha baya kusebenzisa uvavanyo oluvayo ngakumbi. Ngokuqhelekileyo, lo yixesha leentsholongwane likaRussell (RVVT) eliguquguqukayo, elisebenzisa i-phospholipid kunye nesifo kwiNyoka kaRussell inyoka ukuze ihlolwe i-lupus anticoagulant. Ezinye iimvavanyo ze-coagulation ezinokuthi zingasetyenziselwa inkqubo ye-platelet ye-neutralization (PNP) kunye nexesha le-kaolin yokuqhawula (KCT).
Ukuthintela izambatho zegazi
Abantu abavavanya i-LA bahlala bexelwe abagcini begazi ukuba bancede ukukhusela ama-clots, kodwa kuphela xa i-clotting engaqhelekanga ibonakala. I-Steroids inokumiselwa ukuba incedise ekunciphiseni amanqanaba e-antibody.
Ngonyango olungileyo, iingxaki ezivela kwi-lupus anticoagulant zilawulwa.
Kukho ezinye izinto onokuzenza ukukhusela ama-blood clots ukuba unayo i-LA:
- Gwema iipilisi zokulawulwa kokuzalwa kokuzalwa kunye namayeza e-hormone yokunyuka komzi
- Musa ukutshaya okanye ukusebenzisa ezinye iimveliso zecuba
- Musa ukulala okanye ulale ixesha elide ngaphandle kokuba ulele
- Xa uhamba, vuka ngezikhathi ukugcina igazi lakho lihamba
- Hambisa amaqhosha akho phezulu nangaphantsi xa ungeke ujikeleze
Ukuba unomdla ngegazi, uthetha ugqirha malunga ne-LA kunye nomngcipheko wakho wokuphuhlisa igazi. Ugqirha wakho unokufumana iziphakamiso, ezithile kuwe, ezinokukunceda ukunciphisa umngcipheko wakho.
Imithombo:
Antiphospholipid Antibodies. I-Johns Hopkins Centre Lupus.
I-Lupus Anticoagulants kunye neAntiphospholipid Antibodies. MedlinePlus. ILayibrari yeSizwe ka-US yamayeza. NgoJanuwari 20, 2015.
Antiphospholipid Antibodies. Lupus Foundation yaseMelika. Agasti 2008.