Isifo esiziMzimba esisodwa
I-Sjogren's syndrome ebizwa ngokuba ngumgqirha waseSweden, u-Henrik Sjögren, owakufumanisa ekuqaleni kwe-1900-isifo esizimelayo , isifo esibangelwayo njengesimo esiyintloko ngaphandle kwesinye isifo se-rheumatic okanye njengesimo sesibini kunye nesinye isimo se-rheumatic. Phantse ama-50 ekhulwini le-Sjogren's syndrome yenzeka nje kuphela.
Ezinye iipesenti ezingama-50 ze-Sjogren's syndrome zenzeka njengesiqulatho sesibini, ubuninzi be- rheumatoid arthritis , i-systemic lupus erythematosus, i- scleroderma , i- polymyositis , okanye i-dermatomyositis.
Ngokutsho kweSjogren's Syndrome Foundation, i-Sjogren's syndrome enye yeemeko ezixhaphakileyo ezizimeleyo kwaye zichaphazela ezininzi ezinezigidi ezingama-Amerika. Iipesenti ezingama-90 zeSjogren's syndrome izigulane ngabafazi. Umyinge weminyaka yobudala ungaphezulu kweminyaka engama-40 ubudala-kodwa amadoda, abafazi kunye nabantwana banokuhlakulela isifo se-Sjogren nanini na.
Isizathu
Isizathu se-Sjogren's syndrome asiyazi. Ngokwe-American College of Rheumatology, izifo zofuzo kunye nezifo zentsholongwane zingakhuphula umngcipheko wokuphuhlisa i-syndrome. IHormones inokuba yinto ebalulekileyo.
Iimpawu
Ngokutsho kweSjogren's Syndrome Foundation, iimpawu zingabandakanya:
- Amehlo adibeneyo anokuzivakalela okanye ukutshisa
- Umlomo omile
- Unzima ukuhlafuna, ukugwinya nokuthetha
- Ulwimi oluqhekekileyo okanye olunzulu
- Emile, ovuthayo emqaleni
- Ukwahluka kwintleko okanye iphunga
- Ukubola kwamazinyo
- Izifo zesilonda zomlomo
- Intlungu ehlangeneyo
- Ubunzima bokugaya
- Iphunga elomileyo kunye nekhumba
- Ukuvuvukala kweengqungquthela ebusweni
- Ukuma komzimba
- Ukukhathala
- I-lymph nodes ekhulisiweyo
Iingxaki ezininzi ezinxulumene ne-Sjogren's syndrome ziquka:
- Ukurhoxiswa kwiingalo nemilenze ehlobene ne- vasculitis
- Ukuvuvukala kwimiphunga, isibindi kunye neentso
- Iingxaki ze-neurological ezibangelwa ukugada, ukuxubha kunye nobuthathaka
- I-Lymphoma kwinani elincinci lezigulane
Ukuxilongwa
Ngokumalunga neempawu, iziphumo ezivela ekuhloliseni ngokomzimba kunye novavanyo oluthile lokuxilonga lunceda ukuxilongwa kwe-Sjogren's syndrome. Akukho vavanyo olulodwa luyakwazi ukuqinisekisa ukuba ukuxilongwa ngokwalo. Izilingo ezinceda ukulungiselela ukuxilongwa zibandakanya:
- I-anti-nuclear antibody (uvavanyo lwe-ANA) - iipesenti ezingama-70 zezigulane ze-Sjogren zivavanya i-ANA, kodwa i-antibody ingaba khona kubantu abanezempilo.
- I-SSA (i-anti-Ro) kunye ne-SSB (i-anti-La) - Ama-Antibodies afunyanwa ngabantu abane-syjrome ye-primary ye-Sjogren. Akuzona zonke izigulane zikaSjogren ezivavanya i-SSA ne-SSB.
- Isifo se-Rheumatoid - iipesenti ezingama-60 ukuya kuma-70 zabantu abaxilongwa nge-Sjogren's syndrome zineempembelelo ze-rheumatoid factor.
- I-immunoglobulins - Iiprotheni zegazi eziqhelekileyo ziphakanyisiwe kwiSjogren's syndrome.
- Iimvavanyo ezikhethekileyo ze-ophthalmologic okanye iimvavanyo zamazinyo zingalawulwa ukuba zihlolwe ukumelela okungavamile okanye ezinye izinto ezingaqhelekanga. Uvavanyo lunokubandakanya: Uvavanyo lukaSchirmer lwamehlo omile (ugqirha ubeka amanqaku ephepha ngaphantsi kweepilisi ezincinci kunye nemilinganiselo yokumanzisa emaphepha emva kwemizuzu emi-5); ukukhawula ukukhanya kwesibane (eyenziwa yi-ophthalmologist usebenzisa izixhobo zokukhulisa nokuhlolisisa iliso, ukujonga ukuma nokuvuvukala); ukutshiza kunye nedayi ebalulekileyo (ukujonga umonakalo ebusweni belihlo); ukuhlolwa komlomo (ugqirha uhlola ukungaqhelekanga kwaye unokufumana isampuli se-sali yokutshekisha umgangatho); i-lip biopsy (ugqirha uyasusa iincinci ezincinci ezivela emlonyeni ophantsi ukuze kuhlolwe i-microscopic examination).
Unyango
Unyango lwe-Sjogren's syndrome luhlukileyo kumntu ngamnye, kuxhomekeke kwiziphi iindawo zomzimba ezichaphazelekayo. Nangona kungekho nonyango kwiSjogren's syndrome, ukuhlanjululwa komlomo, izitishi zokufaka umquba, i-gel, kunye ne-gum kunokunciphisa impawu zomlomo. Amachiza kunye nokunyangwa kweziyobisi kumlomo owomileyo ohambelana ne-Sjogren's syndrome kunokubandakanya u-saliva kunye ne-mucus evuselela iziyobisi, njengale:
- I-Salagen (i-Pilocarpine hydrochloride)
- Evoxac (Cevimeline HCI)
Iinyembezi zomzimba kunye namafutha okugcoba kwamehlo anokunceda ukuphelisa amehlo omile angapheliyo. Amachiza kunye nokunyangwa kweziyobisi zonyango elomileyo elihambelana neSjogren's syndrome kungaquka:
- Restasis (i-Cyclosporine Ophthalmic Emulsion)
- I-Hydroxypropyl Cellulose (Amaconsi Amaso kunye namaPellets)
Iingxaki ezingaphezulu, ezifana nentlungu edibeneyo okanye ukubandakanywa kwentlungu, kudla ukuphathwa nge- NSAID (izidakamizwa ezingenayo i-steroidal anti-inflammatory drugs). I-lung, iinjongo, isitya segazi, okanye iingxaki zesistim seentsholongwane zingaphathwa nge:
- Corticosteroids
- I-DMARD (izifo-guqula izidakamizwa zokulwa ne-antirheumatic) okanye i-immunosuppressives
ILizwi
Isikhathi esiphakathi kokuqala kweempawu zokuxilongwa kwe-Sjogren's syndrome kuthiwa liyiminyaka engaphezu kwe-6. Emva koko, kukho izimbangela ezininzi zamehlo oomileyo nomlomo owomileyo omele ulawulwe ngaphandle. Umlomo omile kunye noomileyo yimpawu eziqhelekileyo ezinxulumene neSjogren's syndrome, kodwa iimpawu azikho kuphela. Amanye amayeza, athathwe kwezinye iimeko, angabangela ukoma. Kwaphela ukuphela komzimba kuhambelana neempawu zokomisa. Kubalulekile ukuba ungagxininisi kwizigqibo ngenxa yokuba unamehlo owomileyo okanye umlomo owomileyo. Ukuba unayo le mpawu, jonga ugqirha ukuba uphononongo olupheleleyo kunye nokuxilongwa. I-Rheumatologists ilawula izigulane ze-Sjogren's syndrome, ngelixa izidokotela zamazinyo kunye noogqirha bamajoni bangaphatha iimpawu ezithile. Isifo sikaSjogren sisimo esinokunyanga. Ngonyango olunempumelelo, abaninzi abantu banokuphila kakuhle.
Siya kukhankanywa ukuba singakhankanyi izilwanyana ezilula zamehlo omile. Gweba amehlo akho ukuwahambisa. Blink 5 okanye amaxesha ama-6 ngomzuzu. Khusela amehlo akho emoyeni nakwiimpawu. Qinisekisa ukusebenzisa i-humidifier ekhaya lakho. Gwema umsi, kwaye ugweme ukwakheka kwamehlo okungacasula. Ngokufanayo, kukho iingcebiso eziqhelekileyo zokulawula umlomo owomileyo. Ukuhlamba i-gum okanye usinayo kwi-candy hard candy. Sip amanzi emini. Sebenzisa i-lip balm ukuze unciphise imilomo eyomileyo.
> Imithombo:
> NgeSjogren's Syndrome. Sjogren's Syndrome Foundation.
> Imibuzo Neempendulo NgeSjogren's Syndrome, i-NIAMS, ihlaziywe ngoSeptemba 2016.
> Udell, James, MD. Sjogren's Syndrome. Ikholeji yaseMerika yaseRheumatology. Ukuhlaziywa ngoMashi 2017.