Uhlobo lweArthritis kunye neFom yeVasculitis
Isifo se-Kawasaki ngenye yeentlobo ezili-100 ze-arthritis, ngokwe-Arthritis Foundation. Isifo se-Kawasaki sisimo se-vasculitis yesistim eqhubekayo kubantwana abancinci; I-80% yezigulane zaseKawasaki zingaphantsi kweminyaka emi-5 ubudala.
U-Tomasaku Kawasaki waqala ukufumanisa isifo ngo-1967 eJapan. Ngaphambi kokutyunjwa njengesifo seKawasaki, imeko yaziwa ngokuba yi-lymph node syndrome.
Ikwabizwa nangoku njengesifo sikaKawasaki, i-Kawasaki's syndrome kunye ne-infartial polyarteritis.
Iimpawu
Isifo se-Kawasaki sinokudibana nokuphuhliswa kwe-corterary arteritis (ukuvuvukala kwemithambo ye-coronary) kunye nokubunjwa kwe-aneurysms. E-United States, isifo se-Kawasaki sithathwa njengesona sizathu esibangela isifo senhliziyo kubantwana.
Isifo se-Kawasaki siphuthuma ngokukhawuleza kwaye siqhuba inkambo enobudlova kwixesha leveki. Ngokuqhelekileyo, imeko iya kugqiba. Nangona isisombululo, nangona kunjalo, kunokubakho iingxaki zomzimba kwiminyaka kamva.
Ezinye iimpawu ezinxulumene nezifo ze-Kawasaki ziquka:
- iimfiva eziphawulayo ezidlulileyo iintsuku ezi-5 okanye ngaphezulu (ezifunekayo ukuba zixilongwe ngee-Kawasaki Disease)
- i-conjunctiva evulekileyo (amehlo) ngaphandle kwepus
- imilomo ebomvu
- iibomvu ezibomvu emlonyeni
- ulwimi olubomvu olubonakala ngathi i-strawberry
- i-rashes kwi-trunk yomzimba
- izandla ezibomvu zezandla kunye neengqumbo ezibomvu zeenyawo
- i-edema yezandla kunye neenyawo
- ukukhumbuza isikhumba ezandleni, ezinyaweni kunye nasezifweni zobuncwane
- i-lymph node evimbayo ngokuqhelekileyo ecaleni kwentamo
- intlungu kunye kunye nokuvuvukala kaninzi kumacala omabini omzimba
Ezinye iziphumo ezingaqhelekanga ezinokuthi zenzeke ngezifo ze-Kawasaki ziquka i-aseptic meningitis, i- pyuria oyinyumba kunye ne-urethritis, isifo sohudo, intlungu yesisu, intlungu yesisu, i-jaundice ephazamisayo kunye ne-hydrops ye gallbladder.
Isizathu
Esinye isikrokrezo sisisifo esibangela sisifo sesifo seKawasaki, kodwa akukho nanye ibonakaliswe. Kukho izitenxo ezininzi ze-immunologic ezinxulumene nesifo se-Kawasaki, kwaye abanye bakholelwa ukuba yimeko ehamba ngokuzenzekelayo .
Ukukhula
E-United States, isifo se-Kawasaki sichaphazela abantwana abangama-4 000 ngonyaka. Ixhaphake kakhulu eJapan apho ifunyenwe ngama-5 000 ukuya kuma-6 000 amacala ngamnye ngonyaka.
Unyango
Xa isifo sifumaneka, unyango olukhawulezileyo lunconywa ukwenzela ukuba umonakalo kwimibhobho ye-coronary kunye nentliziyo inokuthintelwa. I-immune globulin (IVIG) engenayo i-intravenous (i-IVIG) enikwe kwizinga eliphezulu kakhulu ithathwa njengonyango oluqhelekileyo lwezifo ze-Kawasaki. I- aspirin ephezulu kakhulu iyingxenye yesicwangciso sonyango ngokunjalo. I-glucocorticoids ayisoloko isetyenziselwa ukuphatha isifo se-Kawasaki.
Xa unyango lwe-Kawasaki lwexesha lokuqala lusetyenziswa, ukufumana ngokutsha kunokwenzeka kakhulu, kodwa i-2% yezigulane zezifo ze-Kawasaki zifa ngenxa yeengxaki ze-coronary artery inflammation. Kunconywa ukuba izigulane ezinezifo ze-Kawasaki zine-EKG (echocardiogram) nganye okanye kwiminyaka emibini ukujonga iingxaki zentliziyo ezisele.
Imithombo:
Vasculitides. Izifo zeKawasaki (Isahluko 21). I-Primer kwi-Rheumatic Diseases . Uhlobo lwe 13. Ipapashwe ngu-Arthritis Foundation. Klippel J. et al.
Akukuphela nje Ukukhula Kwintlungu . I-Kawasaki Izifo Isahluko 17. UTomas JA Lehman, MD. I-Oxford University Press. 2004.
Izifo zeKawasaki. MedlinePlus. NLM kunye neNIH. 11/29/2006.