Isizathu esingaziwa esona sifundo sokuLawula
I-Mondini syndrome, eyaziwa nangokuthi i-Mondini dysplasia okanye i-Mondini malformation, ichaza imeko apho i-cochlea engaphelelanga, iphendulela enye kunye nesiqingatha esinye kwisithuba esiqhelekileyo sesibini nesiqingatha. Le meko yaqala ukuchazwa ngo-1791 ngudokotela uCarlo Mondini kwisiqendu esithi "I-Anatomic Section ye-Boy's Born Intelligent." Uguqulelo oluvela kwisiLatin sasekuqaleni lwalo nqaku lwapapashwa ngo-1997.
Isiqendu sokuqala sikaCarlo Mondini sineenkcazo ecacileyo ye-malformation ebizwa ngegama lakhe. Kule minyaka, abanye oogqirha baye basebenzisa eli gama ukuchaza ezinye izinto ezingabonakaliyo. Xa kuxoxwa ngempembelelo yeM Mondini, kubalulekile ukuba nencazelo ecacileyo ye-cochlea kunye nezinye izakhiwo zangaphakathi zendlebe njengoko igama elithi 'Mondini' lingadideka.
Izizathu
Lo ngumntwana ozalwayo (okhoyo ngexesha lokuzalwa) isizathu sokulahlekelwa kwindlebe. Inkohlakalo ye-Mondini iyenzeka xa kukho ukuphazanyiswa ekuphuhlisweni kweendlebe zangaphakathi ngeliveki yesixhenxe yesisu. Oku kunokuchaphazela enye okanye zombini iindlebe kwaye ingaba yodwa okanye iyenzeka ngezinye iintlobo zeentlungu okanye i-syndromes. Ama-syndromes ayaziwa ukuba anxulumene neentlungu zeM Mondini ziquka i-Pendred Syndrome, i-DiGeorge Syndrome, i-Klippel Feil Syndrome, i-Fountain Syndrome, i-Wildervanck Syndrome, i-CHARGE syndrome, kunye nezinye i-chromosomal trisomies.
Kukho imeko apho i-Mondini iingqinisiso ziye zaxhunyaniswa neendlela zokuzimela ze-autosomal kunye ne-autosomal i-patriotic heritage .
Ukuxilongwa
Ukuxilongwa kweengcamango zeM Mondini zenziwe ngezifundo ze-radiographic, ezifana neziphumo ze-CT eziphambili ze-CT.
Ukuvala Ukulahleka kunye noTyango
Ukulahleka kweendlebe ezinxulumene neengxaki zeM Mondini ziyahluka, nangona kunjalo ziqhelekile. Ukuncediswa kwezixhobo kunconywa xa kukho ukuvala okwaneleyo ukuva ukuba kunenzuzo. Kwiimeko apho izixhobo ezivakalayo zingekho kakuhle, ukufakelwa kwe-cochlear kwenziwe ngempumelelo.
Ezinye izinto
Abantu abaneentlungu zeMondini bangasengozini enkulu yokumelana ne-meningitis. I-malformation inokudala indawo elula yokungena kumkhuhlane ojikeleze ingqondo kunye nentambo yomthambo. Kwiimeko apho kukho iziqendu ezininzi (okanye eziphindaphindiweyo) ze-meningitis, ukuhlinzwa ukuvala le ngongoma yokungena kunokuboniswa.
Iphulo leMalmini linokuchaphazela inkqubo yokulinganisela indlebe yangaphakathi. Abantwana abanokungahambi kakuhle kweMancini bangabonisa ukulibaziseka kokuphuhliswa ekuthuthukiseni imoto ngenxa yokunciphisa igalelo kwingqondo kwi-balance system. Kwezinye iimeko, imiba engalingani ingabonakali de ibe ngumdala.
> Imithombo:
> Hain, T (2012). Mondini kunye noMichel Ukuchithwa kweendlebe zangaphakathi. Utywala kunye noLungelelwano.
> Bona, W (1999). Yintoni 'i-Mondini' kunye neliphi igama elinguGama? I-American Journal ye-Neuroradiology.
> Mondini C. Minor imisebenzi yaseCarlo > Mondini: > I-anatomic kwicandelo lomfana ozelwe isisithulu. U-J Otol 1997; 18: 288-293
> Mondini Dysplasia (2012). I-Ofisi yePhando loPhando lweZifo.