I-Cataplexy ne-Hypocretin Testing ingahlukahluka kwiintlobo eziphantsi
Ukuqhaqhaqhaqhoko kuhlala kubonakaliswa ngokulala ngokwemini, kodwa kukho ezinye iimpawu kunye neziphumo zokuvavanya ezisetyenziselwa ukwahlula iindidi zeemeko. Kukho iintlobo ezimbini zeenqanawa, kodwa yintoni umehluko phakathi kohlobo lwe-narcolepsy no-type 2? Funda malunga nale ntlukwano, kubandakanywa indima yokubamba kunye nokuvavanya kwamanqanaba e-hypocretin kwi-cerebrospinal fluid (CSF).
Iimpawu zeNtshontshopynga zingahlukahluka kwiintlobo zeeNtlu
Zombini iintlobo zeenqanawa zibandakanya isidingo esingenasiphelo sokulala okanye imini silele ukulala. Ngaphandle kokulala, i-narcolepsy ayiyiyo yokuxilongwa. Kukho ezinye iimpawu ezinxulumene nazo, kwaye ezinye zezi zinto zinokunceda ukuhlukanisa iintlobo eziphantsi.
Kukho iintlobo ezimbini zeedapepsy: uhlobo 1 kunye nohlobo 2. Uhlobo 1 lungabandakanya ubukho bempawu zentambo. I-Cataplexy ichazwa njengengqungquthela enye yefutshane, ngokuqhelekileyo ilahleko yomsindo we-muscle kunye nokugcinwa kwengqondo. Ubuthakathaka buya kucatshukiswa yimvakalelo enamandla. Ezi zivakalelo zihlala zilungile; umzekelo, i-cataplexy inxulumene nokuhleka. Ubuthathaka bungabandakanya ubuso, iingalo, okanye imilenze. Ezinye iidleptics ziza kuba neelusiki ze-droopy, ukuvula umlomo, ukukhutshwa kolwimi, okanye ukukhanda kwentloko. Abanye abantu banokuwela phantsi emhlabathini ngexesha lokuhlaselwa kwe-cataplexy.
Zombini iintlobo zeengxowa-ngxowa zinokubandakanya ukukhubazeka kokulala nokukhulelwa kwe-hypnagogic . Ubuthongo obuqhekekileyo ebusuku buvame ukuvela kwiimeko zombini.
Indima yovavanyo lwe Hypocretin kunye ne-MSLT
Uvavanyo oluchanekileyo lungasetyenziselwa ukwahlula phakathi kwezi zimbini zeentlobo zeenqanawa. Ukulala ngokugqithiseleyo kwemini kunqunywe ngokusekelwe kwiziphumo zovavanyo lwe- latency yokulala (MSLT).
Olu vavanyo lulandela isifundo sokulala esiqhelekileyo kwaye sibandakanya amathuba amane okanye amahlanu omnxeba athoba kwiiyure ezingama-2. Esi sifundo sinikezwa ithuba lokulala, kwaye abantu abane-narcolepsy baya kulala phantsi kwemizuzu engama-8 ngokuqhelekileyo. Ukongezelela, ukulala kwe-REM kuya kwenzeka kwiminyaka eyi-15 yokulala kufikeleleke ubuncinane emibini yamathuba omnxeba.
Ngaphezu koko, ukuvavanywa kwamanqanaba e-hypocretin kwi-CSF umthamo njengenxalenye yokugqitywa kwe - lumbar kungabonakala. Ukuba amazinga alinganiswa ukuba angaphantsi kwe-110 pg / mL, oku kuhambelana nokuxilongwa kohlobo lwe-1 lwe-narcolepsy. Ukuba amanqanaba aqhelekileyo (okanye angalinganiswa) kwaye i-cataplexy ayifumanekanga, faka u-2 i-narcolepsy ifumaneka ukuba i-MSLT ilungile. Ukuba izinga le-hypocretin lilinganiswa ukuba lingaqhelekanga kamva, okanye ukuba i-cataplexy iyaqhubeka, i-diagnostic ingatshintshwa ukuze ifake 1.
Nangona i-narcolepsy yimeko engavumelekanga, kwenzeka ngokuqhelekileyo ngokwaneleyo, kunye nohlobo 1 oluchaphazela abantu abayi-1 kwi-5,000. Uxilongo kufuneka lwenziwe ngongcali yokulala okwazi ukufaka uvavanyo olufanelekileyo kwaye emva koko unike ngonyango olululo.
Ukuba unenkxalabo yokuba unakho iimpawu zokuxhamla, ufune ukuphononongwa kwakhona ngongcali olalayo onokukunika inkxaso kunye nenkxaso oyifunayo.
> Umthombo:
> I-American Academy ye-Medicine Sleep. Ulwahlulo lwamazwe ngamazwe okuphazamiseka kokulala, 3rd ed. Darien, IL: I-American Academy yoLwazi lweMpilo, ngo-2014.