Isifo seMoto seNigon
I-Primary scalosis sclerosis (i-PLS) isifo se-neuron esichaphazelekayo . I-PLS ithintela iiseli zesiswini zomzimba ezilawula ukunyakaza ngokuzithandela kwezihlunu, ezibizwa ngokuba ngama-neurons. Ngokuhamba kwexesha, la ma-neurons alahlekelwa amandla abo okusebenza, abangela ukungabi nantlungu kodwa ukunyameka okuqhubekayo kunye nokuqina komzimba.
Ayaziwa ukuba kutheni i-PLS ivele, okanye ncamashi indlela iisensi zeentsimbi ezonakaliswa ngayo.
I-Primary scalosis sclerosis ibonakala iqala emva kweminyaka engama-40 ukuya kuma-50 ubudala. Ayaziwa ukuba bangaphi abantu abachaphazelekayo kwi-PLS, kodwa kunqabile kakhulu.
Iimpawu
Ukulahlekelwa kwamaseli esiswini kubangela ukuba imisipha ibe nzima kwaye kunzima ukuhamba. Ngokuqhelekileyo, iingxaki zeemisipha ziqala emilenzeni kwaye zinyusa umzimba kumthi, iingalo kunye nezihlunu ebusweni nasentanyeni. Ukuqhubela phambili kwe-PLS kuyahluka ukusuka kwimeko ukuya kwimeko-Abanye bangathuthuka ngokukhawuleza kwiminyaka embalwa okanye ngokukhawuleza kwiminyaka embalwa.
Iimpawu zokuQala. Kwiimeko ezininzi, uphawu lokuqala lwe-PLS lubuthathaka bomzimba kunye nokuqina kumalungu angaphantsi. Ezinye iimpawu zokuqala ziquka:
- Umlenze owodwa uvame ukuchaphazeleka ngaphezu kwesinye, ngokunyuka okuthe ngcembe komnye umlenze
- Ukunyakaza okunyanzelekileyo kwemilenze ngenxa yeengxaki zentsholongwane ezingabonakaliyo
- Ubunzima bokuhamba nokugcina ukulinganisela, njengokunciphisa okanye ukukhubeka
- Ukuchithwa kwemisipha echaphazelekayo
- Ukuqhelana ngokubanzi
Iimpawu zoPhuculo. Abantu abachaphazelekayo banokuba nzima ngakumbi ukuhamba. Ukusetyenziswa kwereka okanye ifowuni efanayo ukukunceda ekuhambeni kunokufuneka. Kwezinye iimeko, ezinye iimpawu zingaphambi kokuphuhliswa kobuthathaka emasimini. Ezinye iimpawu zingabandakanya:
- Iimfudu ze-Muscle ezandleni okanye kwisiseko sobuchopho.
- Iintlungu ezibuhlungu emilenzeni, emva, okanye entanyeni
- Ingxaki ihamba ngezandla kwaye yenza imisebenzi efana nokudibanisa iinwele okanye amazinyo
- Ubunzima ukwenza amagama (dysarthria) okanye ukuthetha
- Unzima ukugwinya (dysphagia)
- Ukulahlekelwa kolawulo lwe-bladder ekupheleni kwexesha eliphambili le-scalosis
Iimpawu zihamba ngokukhawuleza ngokuhamba kwesikhathi.
Ukuxilongwa
Akukho luvavanyo oluthile lwe-primary scalosis sclerosis, ngoko ke ixesha elininzi ixesha lokuxilongwa lwenzeka ngenxa yokuphelisa ezinye izizathu ezibangelwa iimpawu. Ngenxa yokuba i- amyotrophic lateral sclerosis (i-ALS, okanye isifo sikaLou Gehrig) iyaziwa ngokubanzi, kwaye ngenxa yokuba izifo zibini zibonakalisa iimpawu ezifanayo, i-PLS idla ngokudibanisa ne-ALS.
Unyango
Akukho nonyango okwangoku kwe-PLS, ngoko unyango lujolise ekunciphiseni iimpawu zesifo. Unyango lwe-PLS luquka:
- Imithi enjengeBaclofen neTyzanidine ukunciphisa ama-muscle spasms
- Ukunyangwa kweziyobisi ukujongana nokulahlekelwa kwesilwanyana
- Uphuhliso lwezobugcisa kunye nokusebenza ukuze kuncediswe ukunciphisa ama-spasms, ukuphucula ukuhamba, kunye nokubonelela ngezixhobo ukukunceda ngokuhamba nokutya
- Ulwaphulo lwentetho ukunceda ngokuthetha
- I-Orthotics kunye nezihlangu zifaka ukukhupha iingxaki zeengxaki kunye neenyawo
Inkxaso
I-Primary latal sclerosis iveza ukukhubazeka okuqhubekayo kunye nokulahleka komsebenzi kodwa ayichaphazeli ingqondo okanye iyanciphise ubomi bezilwanyana ngqo. Ngenxa yoko, amaqela enkxaso njengeSpastic Paraplegia Foundation kwizigulane kunye neentsapho zawo kubalulekile ekuguquleleni umthwalo kunye nemithwalo yengqondo yesi sifo.
> Imithombo:
Isiko seSizwe seNational Psychology and Stroke. I-NINDS I-Primary Lateral Sclerosis Information Page.
ISpastic Paraplegia Foundation. Malunga neeplani.
ISpastic Paraplegia Foundation. Unyango kunye ne zonyango.
I-National Organisation for Rare Diseases. I-Primary Lateral Sclerosis.