Ukuchonga nokuPhatha iDermatomyositis

Iimpawu zoKhuseleko zoLwazi kwiSifo

I-Dermatomyositis iyisifo esivuthayo (i- myopathy ) echaphazela ngokuyinhloko ulusu kunye nezihlunu kodwa kunokuchaphazela ezinye iinkqubo zomzimba zomzimba. Uphando lucebisa ukuba yinkinga yokuzimela komzimba , apho umzimba uhlasela amaseli akhe aphilileyo.

I-Dermatomyositis ingenzeka kubantu babani na. Kubantu abadala, ukuphakama kokuqala kukumalunga nama-50 ubudala ubudala. Eyaziwayo njenge-dermatomyositis yolutsha kubantwana, ubudala bokuqala buyiminyaka eyi-5-10 ubudala.

Ichaphazela amabini ngokuphindaphindiweyo njengamadoda kwaye kuvela kubantu bazo zonke iintlanga.

Dermatomyositis Izimpawu

I-Dermatomyositis iveza iimpawu zesikhumba kunye nezihlunu ezifana:

Nangona ingaqhelekanga, abantu abane-dermatomyositis banakho iimpawu zesistim ezifana ne- arthritis , ukuphefumula okufutshane, okanye ubunzima bokugwinya okanye ukuthetha. Abantu abadala abaneminyaka engama-60 ubudala kunye ne-dermatomyositis kubonakala benomngcipheko ophezulu wokuba nomhlaza.

Ukuchonga iDermatomyositis

Abantu abane-dermatomyositis bahlala benesifo sengqondo njengempawu zabo zokuqala. Ukugqithiswa kweempawu kunye neepilisi, kwakunye neendlwana ze-calcinosis kubantwana, kuya kuphakamisa ukuxilongwa. Ngamanye amaxesha izilonda zesikhumba zingaphoswa ngenxa ye-lupus erythematosus, i-psoriasis, okanye i-lichen plan.

Abantwana abane-dermatomyositis banokuba nzima ukuxilonga kude kube nezibonakaliso zezikhumba ezibonakalayo.

Ukongeza kwiimpawu zesikhumba, iimvavanyo zegazi zenziwa ukuba zibone i-enzyme ze-muscle kunye neempawu zokuvuvukala. Abanye abantu abane-dermatomyositis banesifo se-anti-nuclear antibody (ANA). I- IMRI ), i-electromyography (EMG), kunye ne-biopsy ye-muscle ingahlola isifo somzimba kunye nomonakalo.

Ukunyangwa kweDermatomyositis

Unyango lwe-dermatomyositis ujolise ekulawuleni izifo zesisu kunye neempawu zesikhumba. Ngokuqhelekileyo, i-corticosteroid efana ne-prednisone ilawulwa ukunciphisa ukuvuvukala kwemisipha. Ukuba iimpembelelo ze-steroid ziba nzima, imithi ye-immunosuppressant okanye i-cytotoxic, njenge-methotrexate (iRheumatrex) okanye i-azathioprin (Imuran), isenokusetyenziswa. I-Methotrexate inokunceda ekunciphiseni iimpawu zesikhumba. Abantu abane-dermatomyositis banemifanekiso kwaye bayakukhusela ulusu lwabo kwi-sun exposure.

Ukuba ububuthakathaka besisu bukhona, unyango lomzimba kunye nokusebenza luyakunceda ukuphucula umsila kunye nokukhusela iingxaki ezifana nezivumelwano. Abanye abantu bangadinga unyango lweempawu zenkqubo okanye iingxaki.

Outlook

Uninzi lwabantu abane-dermatomyositis luya kufuna unyango lwangexesha elide.

I-calcinosis inokuba nzima ukunyanga kwesi sifo kubantwana nakwishumi elivisayo. Abanye abantu banokuvelisa umhlaza okanye ukungaphumeleli komzimba, okukhokelela ekulindeni ubomi obufutshane. Nangona kunjalo, abaninzi abantu baphendula kakuhle unyango kwaye banokuphucula abanye okanye zonke iimpawu zabo.

Imithombo:

Callen, JP (2002). Dermatomyositis. eMedicine. http://www.emedicine.com/med/topic2608.htm.

UMyositis Association. Yintoni i-Myositis?