Ubudlelwane phakathi kwePortal Hypertension kunye neCape Counts

Ukuba unogonyamelo lwengcinezelo kwaye udluliselwa kwi-hematologist, unokuzibuza ukuba kutheni udokotela wegazi egxininisa ingxaki yesibindi sakho. Abantu abaneengxowankulu zengxowankulu banokunyuka ukunyuka kwegazi kumnye wemifuno ye-portal (imvumba egaxa igazi kwi-tract static tract). Oku kunyuka ukuxhatshazwa kwegazi kudla ngokungenazo iimpawu kude kubekho iingxaki.

Ezi nkxwaleko zibandakanya i-splenomegaly, ukwandiswa kweseyile. I-Splenomegaly ayinayo impawu ezithile. Abantu abane-splenomegaly bangachaza ukuzaliseka kwisisu, ngokukodwa kwicala lasekhohlo apho ipenethi ikhona. Basenokukhalaza nokuziva bezele emva kokutya ukutya okuncinci kuphela. Oku kubangelwa yipeni ekwandisiweyo kwisisu.

I-Splenomegaly ingaqhelekanga xa ihlolwe ngugqirha wakho kodwa ukuba kufuneka ukuba i-ultrasound ingqinisise ukuxilongwa.

I-Spleen neAgazi yeGazi

I-splenomegaly kwi-portal yongcinezelo yonyango ingabangela ukubala kwegazi eliphantsi. Enye yomsebenzi wepen ukucoca zonke iiseli zegazi ukwenzela ukuba ukuguga okanye ukulimaza iiseli zegazi kungasuswa kwi-circulation. Ngoko naliphi na ixesha ngexesha elithile inani legazi elibomvu, iiseli zegazi ezimhlophe kunye neeplatelet zikhona kwipeni.

Njengoko ipenti ikhulisa, ezininzi zala maseli zibanjwe ngepeni.

Ukongezelela, oku kunokukhokelela ekususweni kweeseli zegazi ngokukhawuleza kunokuba ziqhelekile. Oku kungakhokelela ekubeni ne- anemia (inombolo ephantsi yamaseli obomvu), i- thrombocytopenia (inombolo ephantsi yeeplatelets), kunye ne-leukopenia (inani eliphantsi lamaseli egazi ezimhlophe).

Ezi zinguqu zifumaneka rhoqo ngexesha lomsebenzi wegazi oluqhelekileyo oluquka inani elipheleleyo legazi (CBC).

Ngokuqhelekileyo, inani le-anemia, thrombocytopenia, kunye / okanye i-leukopenia ibonayo ludinga ukulinganisa kunye neempawu ezincinci. Akuzona zonke iintlobo zeeseli zegazi ezichaphazelekayo. Ukongezelela, ubunzima bunqunywe bubungakanani besite. Njengoko ubukhulu bepen buyanda, ukubala kwegazi kunokwenyuka ngaphantsi okanye ngokuphambene, ukubala kwegazi kunokunyuka ukuba ipensi yehla ngobukhulu.

Ngaba unyango lufunekayo?

Ubunzima be-anemia / thrombocytopenia / leukopenia yakho inquma ukuba kufuneka uphathwe okanye cha. Ngethamsanqa, abantu abaninzi banamashintsho amancinci kuphela kwigazi kwaye abafunanga unyango.

Unyango lwengqondo yonyango ngokwawo ngamanye amaxesha lunokuphucula ukubala kwegazi. Ukuba utshintsho lunzima, i- splenectomy (ukususwa kokutyunjwa kweseyile) kunokucetyiswa. Ukugqiba ukuba ngaba ufuna i- splenectomy kufuneka ulinganiswe ngokucophelela malunga neengozi zale nonyango , ingozi enkulu yokwanda kwe-sepsis (intsholongwane ephezulu yegazi).

Ukuba ufanele ufumane i-splenectomy, kubalulekile ukuba ugonywe kwiibhaktheriya ezininzi zibangele izifo: iStreptococcus pneumoniae , i- Neisseria meningitidis , kunye neHaemophilus influenzae uhlobo b (ukuba ungadideki nentsholongwane ephezulu ye-influenza).

Ukwandisa impendulo kula ma-immunizations, kufuneka banikwe ubuncinane iintsuku ezili-14 phambi kwe-splenectomy. Ukuba ukuhlinzwa kuyiphuthuma kwaye ukugonywa akunakunikwa kwangaphambili, kunokulawulwa ngomhla we-14 emva kokusebenza.

Emva koko, mhlawumbi uza kufakwa kwi-penicillin ubuncinci bonyaka omnye, ngezinye izikhathi ngonaphakade. Zonke iifom zifuna iimvavanyo zonyango ukulawula ukusuleleka kwebhaktheriya. Ngethamsanqa, ukugonywa kuye kuncitshise amathuba okusuleleka.

ILizwi

Ukuva ukuba i-portal yakho yengozi yentsholongwane kunye ne-splenomegaly ibangele ukuba nexabiso eliphantsi legazi liyakusiza.

Ngethamsanqa, ininzi yexesha eli tshintsho lincinci kwaye ayifuni unyango. Ukuxoxa ngeenkxalabo zakho neqela lakho lezonyango kunokuncedisa ukuxhalabisa kwakho malunga nale nkxalabo.

> Imithombo:

> Schrier SL. Indlela yokufikelela kwisigulane somntu omdala nge-splenomegaly kunye nezinye iingxaki zeplenemic, i-Extrinsic ye-hemolytic anemia ngenxa yokumonakalisa umonakalo: Ukuhlukana kwe-hemolysis kunye ne-hypersplenism. Ku: U-UpToDate, i-Post TW (Ed), UpToDate, i-Waltham, MA.

> McClain KL. Indlela yokufikelela kumntwana onesipali esandisiweyo. Ku: U-UpToDate, i-Post TW (Ed), UpToDate, i-Waltham, MA.