I-POEMS syndrome yinkinga yegazi echaphazela amaninzi amaninzi omzimba kwaye ibangela iimpawu ezininzi. Ichaphazela amadoda namabhinqa kwaye ngokuqhelekileyo iqala emva kweminyaka yobudala engama-50, nangona inokwenzeka nakweyiphi na iminyaka. Ayaziwa ngokuthe ngqo ukuba i-POEMS isifo esingakanani ngenxa yokuba kunzima ukuxilonga ngokuchanekileyo. Isizathu asiyazi.
Iimpawu
Isichazamazwi se-POEMS simele:
- I-P- polyneuropathy, ithetha impawu zesibindi ezinjenge-numbness, ukubetha, kunye / okanye ubuthathaka kwezandla kunye neenyawo
- O- organomegaly, ezithetha izitho ezandisiweyo, ngokuqhelekileyo isibindi, i-spleen, okanye i-lymph nodes. Amaphesenti angama-15 abantu abane-POEMS syndrome bane-Castleman isifo (i-lymph node disorder).
- E - endocrinopathy, ithetha utshintsho kwimveliso yehomoni. Iimpawu ezifana nesifo sikashukela , ukungabi namandla , ukuyeka ukuhamba esikhathini ( amenorrhea ), amanqanaba aphantsi we-thyroid (hypothyroidism), kunye / okanye ukuphuculwa kwebele kumadoda (gynecomastia) unokuba khona.
- I-M- monoclonal gammopathy okanye i-plasma ye-plasma eyandisekayo yinkinga, ezo zombini zithetha iiprotheni zegazi ezingaqhelekanga
- I-S - isikhumba sitshintsha njengokwanda kwe-skin pigment (hyperpigmentation); ukwanda kweenwele zomzimba (hypertrichosis) ebusweni, ezinyeni, nasesifuba; ukunqanda kwesikhumba nokuqinisa, ukuvuvukala (i-edema) yemilenze kunye neenyawo, ukugcotshwa kwezipikili.
Abantu ngabanye banokuva, ukukhathala, iintlungu kunye neentlungu, okanye utshintsho kwimboniso, phakathi kwezinye iimpawu.
Ukuxilongwa
Ukuxilongwa kwe-POEMS syndrome ingenziwa ngokusekelwe ekuhlolweni komzimba kunye nesiganeko sakhe sempilo. Iimvavanyo zegazi ezifana nokubala okupheleleyo kweseli yegazi (CBC) kunye neprotheni ye-prounoelectrophoresis ye-serum yenzelwa ukukhangela ukungaqhelekanga, njengokuba kuhlolwa umchamo. Amanqanaba e-thyroid, i-blood glucose level, kunye namazinga e-estrogen egazini ahlolwe ukuchonga okungaqhelekanga.
I-bone-brown bone and / okanye ithambo x-ray ingenziwa ukuze kuncedwe ukuxilongwa.
Umntu uthathwa njenge-POEMS syndrome ukuba i-"P" (i-polyneuropathy) kunye ne "M" (iiprotheni ezingavamile zegazi) zikhoyo kunye ne-sclerotic (scarring) izilonda zethambo okanye isifo se-Castleman. Abantu abaninzi baya kuba nezinye iimpawu zesifo. Ngenxa yokuba abaninzi oogqirha abaqhelanga ne-POEMS syndrome, iziphumo ezivakalayo zokuvavanya igazi zivame ukuphumela kwi-myeloma ezininzi, okanye iimpawu ze-polyneuropathy zikhokelela ekugqibeleni ukungaphili kakuhle kwe-polyneuropathy (DID).
Unyango
Ukunyanga kwe-POEMS syndrome kuxhomekeke kwonyango lweengxaki zesifo segazi. Uninzi lwabantu lufumana inxalenye yezokwelapha ezifana:
- Ukunyanga kwamayeza
- Imithi yeCorticosteroid njenge-prednisone
- Chemotherapy
- IHormone ukutshintshwa kwama-hormone aphantsi kakhulu
- Ulungiso lwenyama
- Ukutsalwa komnxeba wethambo
Iingcali ezinjenge-neurologist (ugqirha we-nervous system), i-hematologist (ugulane lwegazi), i-dermatologist (ugqirha wesikhumba), kunye ne-endocrinologist (ugqirha we-hormone gland) ngokuqhelekileyo kubandakanyeka ekunyamekelweni komntu one-POEMS syndrome.
Imithombo:
Dispenzieri, Angela. "I-POEMS Syndrome." I-Hematology 2005 (2005): 360-367.
I-Dispenzieri, u-Angela, uRobert A. Kyle, uMartin Q. uLacy, uS. S. Vincent Rajkumar, uTerry M. Therneau, uDirk R. Larson, uFilip R. Greipp, uThomas E. Witzig, uRita Basu, uGuillermo A. Suarez, uRafael Fonseca, John A. Lust, & Morie A. Gertz. "I-POEMS syndrome: iingcaciso kunye nomphumo wesikhathi eside." IGazi 101 (2003): 2496-2506.
"Iimpawu ze-POEMS Syndrome." Unyango lwe-POEMS Syndrome kwi-Clinical Mayo. I-Clinical Mayo. 22 Meyi 2007
Chan, Joanna, & Wingfield Rehmus. "I-POEMS Syndrome." eMedicine. 15 Disemba 2006. WebMD. 22 Meyi 2007