Izifo zePick kunye neCorticobasal Degeneration zithinta i-Circadian Rhythms
I- dementias ye-frontotemporal efana ne-Pick's disease kunye ne- corticobasal diseneration ichaphazela njani ukulala? Funda malunga nale miqathango, kubandakanye iimpawu zabo eziqhelekileyo, kunye nendlela i-dementia echaphazela ngayo i-lobes yangaphambili kunye neyesigxina yengqondo ichaphazela ubuthongo kunye neengqungquthela ze-circadian.
Yintoni i-Frontotemporal Dementia?
I-Dementia ibandakanya izifo ezahlukahlukeneyo ezithintela ingqondo kwaye zichaphazele imemori, ingqwalasela, ubuntu, ulwimi, ukulungisa ingxaki kunye nomsebenzi wemihla ngemihla.
Kule nkalo ebanzi, kukho iimeko ezichaphazela indawo ezithile zeengqondo kwaye zikhokelela ekusebenzeni okuthe ngqo. Enye yale mimandla ekhethekileyo i-dementia ye-frontotemporal (FTD), isifo esichaphazela i-lobes yangaphambili kunye neyesimo seengqondo (esekelwe kumacala angaphantsi nangaphantsi kwengqondo). Ichaphazela ama-5 ukuya kwe-15 ekhulwini labantu abaneengqondo.
Ukugula komzimba kwangaphambili kubandakanya izimo ezimbini ezihlukeneyo: isifo sikaPickk kunye ne-corticobasal deerasal. I-yangaphambili ibonakala ngeziphumo ezingaqhelekanga ezibizwa ngokuba zizidumbu ze-Pick, ezifumaneka kwi-neurons yengqondo equlethe isixa esingaqhelekanga okanye uhlobo lweprotheni ebizwa ngokuba yi-tau. Kukho izityalo ezibonakala ngathi zinegalelo ekufikeni kwesi sifo, kodwa isizathu esingaziwayo sisaziwa. Isifo sikaPick sisimo esinqabileyo esivame ukuvela kubantu abaneminyaka engama-40 ukuya kwengu-60 ubudala.
Ngokwahlukileyo, ukuchithwa kwe-corticobasal (CBD) kubonakala ngokulahlekelwa ngokuthe ngcembe kwe-neurons kwi-cortex ye-cerebral kunye ne-basal ganglia, kwiindawo ezimbini zobuchopho ezibalulekileyo ekucingeni nasekuhambeni.
Le ntlupheko ingathintela kwelinye icala lomzimba ekuqaleni, kodwa njengoko isifo siqhubeka, zombini amalungu omzimba angabandakanyeka. I-CBD ingaqala malunga no-60 ubudala.
Ziziphi iimpawu ze-Frontotemporal Dementia?
Ummandla wengqondo echaphazelekayo kwi-frontentiyomenti ye-dementia ibangela isethi ethile sempawu.
Ngesifo sikaPickk, ubuntu bokuqala kunye nokuguquka kokuziphatha kwenzeka. Oku kungabonakala njengobunzima kwizithuba zentlalo ngeendlela ezingaqhelekanga, ezinyanzelisayo okanye ezingalunganga. Ngokwahlukileyo, isifo sika-Alzheimer sisoloko sibonakala ngokulahleka kweememori njengesifo esibalulekileyo. Abantu abanesifo sikaPikk banokutshintshwa kwimiba engathandabuzekiyo okanye babonakale bengakhathazeki (ukungakhathaleli), kwaye kunokukho iingxaki ezinxulumene nentetho (ebizwa ngokuba ngu-aphasia) kunye nokucinga okungaphumeleli. Ekuhambeni kwexesha, ubuthathaka okanye ukufumanisa kungakhula. Njengomthetho, ezi zimpawu ziya kuqhubeka ziba nzima.
Ukuchithwa kwe-corticobasal kuneempawu ezongezelelweyo ngenxa yeziphumo kwi-basal ganglia. Oku kunokubangela iimpawu ezifana nesifo sika-Parkinson, kubandakanywa ukuqina, ukunyakaza okufutshane kunye nokungalingani. Abantu abane-CBD baya kuhlakulela i-apraxia, oko kungenako ukuqhuba intshukumo enenjongo nangona amandla okusebenza kunye nokuququzelela. Ngokomzekelo, umntu onomdla we-CBD akanako ukulinganisa intshukumo yokuxubha amazinyo, ukutshaya i-cigarette, ukudibanisa iinwele, okanye ukutya isobho kwi-spoon. Ezi ngxaki ekugqibeleni zenza kube nzima ukuhamba. Intetho ingayeka, kwaye ubunzima bokugwinya kungenzeka.
I-Frontotemporal Dementia kunye neMiphumo yokulala
Ukulala kwabantu abane-dementia ye-frontotemporal kungashintsha, kwaye ngokwenene, umzekelo wokulala nokuvuka uguqulwa.
Isiqhelo sesiqhelo se-circadian siyahlukana kakhulu, kunye nomxube wee sibini ezenzeka emini nasemini. Oku kubonakala ngathi iyakwandisa ngaphaya kweenguqu ezinokuthi zenzeke xa zihlala kwisibonelelo sokuhlala esixhasayo njengendlu yokuhlala. Abantu abachaphazelekayo banesithuba esiphambili sokulala , balele belele baze bavuke ngaphaya kwexesha eliqhelekileyo.
Xa kugqitywa nge- electroencephalogram (i-EEG) , isingqimba seengqondo zengqondo asiqhelekanga: kuphuculwa ngexesha lokuvuka. Nangona kunjalo, kunokuba kuyinto eqhelekileyo kwisinye kwisithathu sabantu, ngoko ke akusivivinyeni epheleleyo ukuxilonga imeko.
Ezinye iingxaki zokulala zingenzeka kwi-dementia ye-frontotemporal ngezizathu ezifanayo ezenzekayo kubemi jikelele, kubandakanya i- apnea yokulala .
Ezi zingadinga ukuphonononga okongezelelweyo kunye nezinga elifanelekileyo lonyango, ngokuxhomekeka kwintlupheko ephantsi kwengqondo.
Unyango kunye neNgcaciso kwi-Frontotemporal Dementia
Akukho zonyango ezizodwa ezinganciphisa okanye ukuguqula inkambo ye-dementias. Unyango, oluquka ukusetyenziswa kwamachiza, lunokujoliswa ekunciphiseni iimpawu ezithile, kodwa ngelishwa, ezi zinokumelana nokungenelela. Unonophelo oluxhasayo lunyanzelekile, kubandakanywa nokubonelela indawo ekhuselekileyo kunye nenqanaba elifunekayo loncedo.
Ukugxekwa kwe-dementia ye-frontotemporal ngokuqhelekileyo kuyimpofu, kunye nenkambo eqhubekayo kwaye ibonakalayo-kwaye ukukhubazeka kuyindawo eqhelekileyo yezifo. Isifo sikaPick siya kubangela ukufa phakathi kweminyaka emi-2 ukuya kwe-10, ngokuqhelekileyo ukususela kusuleleka (njengemiphunga ye-pneumonia okanye i-urinary infection tract), okanye enye inkathazo yokukhubazeka okukhulu. I-Corticobasal diseneration ilandela ixesha elifanayo, liqhuba phambili kwiminyaka engama-6 ukuya kwe-8 kwaye iholele ekufeni ngendlela efanayo.
Kubalulekile ukuba abanonophelo kunye nabathandekayo babantu abane-dementia ye-frontotemporal bagcine inethiwekhi yenkxaso kwaye bafumane uncedo njengoko kuyimfuneko. Ukuphazamiseka ubuthongo kungaba yincinci encinci kumxholo wezinye iingxaki, kodwa ukuphazanyiswa kwamaphethini okulala kuqhubeka kuthatha umrhumo kumntu ochaphazelekayo kunye nabanakekeli bakhe. Ngoko ukuphatha ukuphazamiseka kokulala kunokufumana inxaxheba kunye nokunciphisa umthwalo wokunyamekela.
Ukuba ufumanisa ukuba ufuna uncedo olongezelelweyo ekulawuleni le meko, unokuzuza ngokubonisana ne-neurologist, onokukunceda ukulungelelanisa ukunakekelwa kwaye unikezele ukuhanjiswa kwizibonelelo kwindawo yakho.
Imithombo
Kryger, MH et al . "Imigaqo kunye nokuSebenza kweMithi yokulala." Elsevier , i-5th edition, iphe. 1042.
"Isifo sikaPickk." Health PubMed . Kufumaneka: NgoJanuwari 30, 2013.
"I-NINDS Corticobasal Ulwazi loKwenziwa kweNgcaciso." Isiko seSizwe seNational Psychology and Stroke . Kufumaneka: NgoJanuwari 30, 2013.