Izifo Zengcinezelo Ezifa
I-Bartter syndrome isifo esinjengobomi esiyicala esibangelwa sisiphako kwiintso zokukwazi ukubuyisela i-potassium. Oku kwenza izintso zisuse i-potassium kakhulu emzimbeni.
I-Bartter syndrome izuze ifa lokuzimela , nangona ngamanye amaxesha kunokwenzeka kumntu ongenalo nentsapho yembali yesifo. Ayaziwa ngokuthe ngqo ukuba i-Bartter syndrome ihlala kangakanani, kodwa uphando oluthile luqikelela ukuba luchaphazela abantu abayi-1.2 ngabantu abayizigidi.
Kubonakala ukuba kwenzeka kaninzi kubantwana abazalwe ngabazali abanobubele, okanye abahlobene ngokuthe ngqo. Isifo seBartter sichaphazela abesilisa kunye nabesifazane bazo zonke iintlanga.
Iimpawu
Iimpawu zeBartter syndrome zingabandakanya:
- ubuthathaka kunye nokukhathala
- ukwanda kwamanzi (polyuria)
- ukomeleza ukwanda (i-polydipsia)
- ukuvuswa ebusuku ukuvuthwa (i-nocturia)
- ukunyuka kwamanzi
- ukunqwenela ityuwa
- ukuxhamla imisipha
- ukuqothulwa
Abantwana abane-Bartter syndrome banenkinga yokukhula nokuphuhlisa ngokuqhelekileyo.
Ukuxilongwa
I-Bartter syndrome isoloko ifunyaniswa ebuntwaneni ngokusekelwe ekuhloleni ngokomzimba, iimpawu ezikhoyo kunye neziphumo zeemvavanyo zegazi kunye neemvavanyo zomchamo. Ezi ziquka:
- izinga eliphantsi le potassium egazini
- Izinga eliphezulu le potassium kumchamo
- Iqondo eliphantsi le-chloride egazini
- izinga eliphezulu le-chloride kumchamo
- Amanqanaba aphakamileyo amahomoni kunye ne-aldosterone egazini
I-Gitelman syndrome ifana ne-Bartter syndrome ukuze kufuneke iimvavanyo ezingaphezulu ukufumana ukuba yeyiphi ingxaki ekhoyo.
Unyango
Ukunyangwa kwe-Bartter syndrome kugxininise ekugcineni i-potassium yegazi kwinqanaba eliqhelekileyo. Oku kwenziwa ngokutya okunotye kwi-potassium nokuthatha izongezelelo ze-potassium ukuba kuyimfuneko. Kukho neziyobisi ezinciphisa ukulahlekelwa kwe-potassium emcini, njenge-spironolactone, i-triamterene, okanye i-amiloride.
Amanye amayeza asetyenziswa ukuphatha i-Bartter syndrome ingaquka i-indomethacin, i-captopril, kunye nabantwana, i-hormone yokukhula.
> Imithombo:
> "Bartter Syndrome." I-Medical Encyclopedia. 15 Oktobha 2008. I-MedlinePlus.
> "Yintoni iBartter's Syndrome?" Amanqaku. 5 u-Oktobha 2008. I-Bartter Site.
> "Bartter Syndrome." Iingxaki zeTybular kunye neCystic Kidney Disorders. Ngomhla ka-2006. I-Merck Manuals Library yonyango.