Funda ngakumbi malunga neeNqobo, iingxaki zePhysical Prune Belly Syndrome
I-Prune Belly syndrome, eyaziwa nangokuthi i-Eagle-Barrett okanye i-triad syndrome, isifo sobuthathaka kunye nesethi esahlukileyo seengxaki zomzimba ezizalelwe umntwana. Ezi ngxaki zi:
- Izisu zomzimba phambi komzimba zibuthathaka okanye zilahlekile
- Icandelo le-urinary tract lenze ngokungaqhelekanga. Ezi zibandakanya ukwandisa okungavumelekanga (ukuhluthwa) kwamathambo okuvuthwa, ukuqokelela umchamo kwiidonki ezidlula umchamo ukusuka kwiintso ukuya kwi-vestile, kunye / okanye umva we-urine ukusuka kwisibhanti ukuya kwiibhubhu kunye nemidumba (ebizwa ngokuba yi-reflux vesicoureteral).
- Kwamadoda (ama-95% amatyala), ii-testes zihlala ngaphakathi ngaphakathi kwesisu kwaye azihla kwi-scrotum.
Kukho ezinye iingxaki zomzimba kwintsana, njengengqungquthela yomthumbu, ukuchithwa kwe-hip, clubfoot, iingxaki zokuphefumula okanye intliziyo, kunye neengxaki zesisu.
Izizathu zePrune Belly Syndrome
Isizathu se-syndrome asiyazi, kodwa abaphandi bakholelwa ukuba ukuphazamiseka kokukhula komntwana kubangela ukuba iingxaki ziphuhlise. Kucatshangelwa ukuba into ethile ibimbela inxalenye yecala lomgubo, kwaye oku kubangela ukuba ezinye iicatshulwa ziphuhlise ngokungavamile. I-Prune Belly syndrome ivela kwi-1 kwi-40,000 yokuzalwa e-US
Ukuxilongwa kweMeko
I-Ultrasound ngexesha lokukhulelwa ngamanye amaxesha liyakubona ukuphuhliswa okungavumelekanga kwiphepha le-bladder kunye ne-urinary. Nangona umntwana ekhula, i-fluid ikhula kwisisu sayo, eselula kwaye sikhulu. Umkhuhlane uphinde uhlaziywe ngaphambi kokuzalwa, ngoko ngexesha lokuzalwa, usana luba nesisu esiswini okanye isisu somzimba (ngoko ke igama elithi "prune belly").
Emva kokuzalwa, i-ultrasound kunye ne-x-ray inganquma ukuba yiyiphi indlela yokungaqhelekanga kwamanxiwa. I-Prune Belly syndrome ibonakala ngoku:
- Ezinye okanye ubuninzi beentlungu zesisu zisuke zingekho. Oku kunika ubonakala obomvu okanye obunjenge-prune-like.
- Nangona i-attachments ye-muscle emathanjeni ingaba khona, izihlunu zincinci kwaye zincinci ngaphezu kwesikhumba.
- Udonga lwesisu lincinci, isisu esisodwa sibonisa ukuba sikhulu kwaye sikhululekile, kwaye amathumbu angabonwa ngodongxongo lwesisu esiswini.
- Izikhumba zesikhumba zibonakala ziphuma kwiqhosha lomlenze okanye zihamba ngesisu.
- Kwangathi ngamanye amaxesha ukuhamba okuvela kwintonga ye-pubic kungabikho kwaye ngamanye amaxesha isalathisi sesisu sinokuxhumeka kwi-vestile kwi-canal (urachus) okanye nge-cyst.
- Ukutshitshiswa kwezimbambo okanye ukunqumla kwesifuba kunokubangela ukuba isifuba siphumelele kubantwana abane-syndrome.
- I-bladder ekhulisiweyo ikhoyo phantse kuzo zonke iimeko.
Ngelishwa, i-Prune Belly syndrome ingaba nemiphumo emibi kakhulu kwintsana. Iingxelo zibonisa ukuba i-20% yabantwana bafa ngaphambi kokuzalwa, kwaye i-30% ifa ngenxa yengxaki zeengtso kwiminyaka emibini yokuqala yobomi. Kwi-50% eseleyo yeintsana, kukho iindidi ezihlukeneyo zeengxaki ze-urinary.
I-Prune Belly Syndrome isoloko ifunyaniswa phantsi kweendlela ezahlukeneyo zamagama, ezifana nesifo sesisu esiswini esiswini, ukungabikho komzimba kwesisu esiswini, ukungabikho kwesisu esiswini, i-Eagle-Barrett syndrome, i-Obrinsky syndrome okanye i-triad syndrome.
Unyango lwe-Eagle-Barrett
Akukho nonyango ye-Eagle-Barrett (i-prune belly syndrome), kodwa ukulungiswa kwiphepha le-urinary lenziwa.
Abanye oogqirha bazama ukulungisa iingxaki kwi-fetus ngaphambi kokuzalwa, kodwa oku kuye kwaba nemiphumo edibeneyo. Abantwana abaxhomekeke kwizifo ezithintela umchamo banikezwa ngamagciwane okukhusela kunye nokuhlinzwa kunokuzisa iifestile zenkwenkwe kwi-scrotum yakhe.
Ngamanye amaxesha nangona kukho unyango olungcono, izintso zomntwana ziyayeka ukusebenza (ukungaphumeleli kwenkunzi). Unyango lwalo luba yi- dialysis okanye i-kidney transplantation.
Amacandelo ophulo olungcono, ngokukhethekileyo ukusebenzisa i-laparoscopy, aya kwenza imisebenzi yokulungisa imfuneko yomntwana ene-Prune Belly syndrome nzima. Njengoko kuninzi okufundwayo nge-syndrome, unyango lunokuphuculwa kwaye abantwana bancedwa ukuba baphile ixesha elide.
Imithombo:
I-Prune Belly Syndrome Network. Malunga nePrune Belly.
UFranco, I. (2001). I-Prune Belly syndrome. iMedicine ifumaneka kwi http://www.emedicine.com/med/topic3055.htm
Leeners, B., Sauer, I., Schefels, J., Cotarelo, CL, Funk, A. (2000). I-Prune-belly syndrome: Izinketho zokwelapha kuquka ukufakwa kwe-vesica amniotic shunt. J Clin Ultrasound, Vol. 28, No. 9, iphe 500-507.