Yintoni iHemosiderosis?

Iimpawu zingaphumelela ngokuxhomekeke kwiNkcazo eSebenzayo

I-hemoneary hemosiderosis yintlupheko yemiphunga eyenza ukuphuma kwamanzi, okanye ukubola, ngaphakathi kwimiphunga, ekhokelela kwisakhiwo esingaqhelekanga sensimbi. Esi sidibansi sinokubangela i-anemia kunye ne-lung scarring eyaziwa njenge-pulmonary fibrosis. I-Hemosiderosis ingaba isifo esiphambili semiphunga, okanye isibini ukuya kwi-cardiovascular or systemic disease njenge-systemic lupus erythematosus.

Izifo zaseprayimari zivame ukufunyanwa ngethuba lobuncinci.

Izizathu ze-Primary Hemosiderosis

I-hemosiderosis yeprayimari ibangelwa ngu:

I-syndrome ye-Goodpasture ivame ukubonwa kwindoda ebesemdala xa i-Heiner syndrome ihlolwe ngokusesikweni. Idiopathic pulmonary hemosiderosis ingenzeka kubantu beliphi na ubudala kodwa ixhaphake kakhulu kwizingane eziphakathi kweminyaka eyi-1 no-7.

Iimpawu zeHemosiderosis

Iimpawu eziphambili ze-hemosiderosis ziquka ukukhwehlela igazi (i-hemoptysis), ukusilela kwesinyithi (i-anemia), kunye neenguqu zamaphaphu. Iimpawu zingaqala ngokukhawuleza okanye zivele ngokukhawuleza. Ukuba imeko ikhula ngokukhawuleza, iimpawu ezinjengokukhathala okungapheliyo, ukukhwehlela okuqhubekayo, impumlo, ukuqhuma, kunye nokukhula okulibala.

Ukuba umntwana wakho une-Heiner syndrome, unokwazi ukubona izifo zentloko ephakathi, ukukhwehlela okuqhubekayo, impumlo engapheliyo, kunye nokufumana ubunzima obubi.

Ukufumana iSifo

Ukuba ugqirha wakho uxolisa i-hemosiderosis, banokuyilungisa iimvavanyo zegazi, izithethe zezitshixo , ukuhlaziywa kwegazi kunye nokuhlalutya kwe-sputum yegazi. Ezi mvavanyo zinokunceda ukuhlula phakathi kwe-primary hemosiderosis - I-goodpasture syndrome, i-Heiner syndrome, kunye nezifo ze-idiopathic-kunye ne-hemosiderosis yesibini.

Iimvavanyo zegazi ziya kuhlola i-anemia kunye nezibonakaliso zezinye iimeko. Amanqanaba aphezulu e-immunoglobulin angabonisa i-Heiner syndrome ngelixa ijikeleza i-antibodies anti-GBM ekhomba kwi-Wellpasture syndrome. Iimvavanyo zeStool ziza kukhangela igazi kwi-stool, ezinokuthi zenzeke nge-hemosiderosis. I-urinalysis iya kubheka igazi. Ukuba igazi okanye iprotheni likhoyo, linokubonisa ukuba isifo esiphambili okanye sesibini. I-x-ray yesifuba sinokuthi isixhobo sokuxilonga esibalulekileyo.

Izinyango Zonyango

Ulwaphulo lwe-Hemosiderosis lugxininisa unyango lokuphefumula, i-oksijini, ukuguquka kwamagciwane kunye nokunyuswa kwegazi ukujongana ne-anemia ephezulu. Ukuba umntwana wakho une-Heiner syndrome, bonke ubisi kunye neemveliso zobisi kufuneka zisuswe ekudleni kwazo. Oku kuphela kunokwanela ukucima nayiphi na ukuphuma kwamaphaphu. Ukuba i-hemosiderosis ingenxa yesinye isifo, ukunyangwa kwesimo sengqondo kunokunciphisa ukuphuma kwegazi. I-Corticosteroids inokunceda abantu abanompawu kuphela ophuma kumaphaphu abo, kungekho mnye umbane okanye izifo zesibini. Iziyobisi ezinokungena emzimbeni zinokukhetha ukonyango. Nangona kunjalo, uphando luyaqhubeka luhlola ukuba lusebenza kangakanani ixesha elide.

Ngaba wena, okanye umntwana wakho, unokufumanisa i-hemosiderosis, kuya kufuneka ukuba ulandelelwano oluqhubekayo ngononophelo.

Kungenzeka ukuba ugqirha wakho uya kufuna ukugcina iliso kwi-oxygen saturation. kunye nomsebenzi wakho wemiphunga kunye neentso. Ugqirha wakho unokucela kwakhona iimvavanyo zegazi kunye nesifuba x-rays.

Umthombo:

Napchan, GD (2015). Hemosiderosis. Medscape. http://emedicine.medscape.com/article/1002002- ukubukela kwakhona