Cinga ngeNgqungquthela yexesha elide kunye neNyango
Ukuphulukana nokunciphisa ingxaki kunokuba nzima ukulawula, ngokuphelisa ubuthongo obushushu obusuku kunye nobuthathaka obuthathaka obubizwa ngokuba yi- cataplexy . Ngoko, kuyinto engokwemvelo ukuzibuza malunga nexesha elide lokuxela.
Nangona ngokuthe ngcembe sifumana ukuqonda okungcono kwintlupheko kunye neendlela zokuyiphatha, umbuzo uhleli: Ngaba iinqununu zisuka?
Funda ngeengcamango zamanje zokuba kutheni i-narcolepsy eyenzekayo kwaye ingaba isizathu esingaphambili singasuswa.
I-Autoimmune Element
Ukholo lwezinto ezinqunyulwayo lukholelwa ukuba lubangelwa inkqubo yokuzimela. I-immune system ijongene nokulwa nezifo, kodwa ngamanye amaxesha le arsenal enamandla iphendukele emzimbeni ngokwawo.
Xa oku kwenzeka, i-syndromes ethile ingabangela, kubandakanya i-hepatitis, i-rheumatoid arthritis, kunye ne-narcolepsy. Kukho ubungqina obukhulayo bokuthi intsholongwane inokubangela ukuba umzimba uphendule ngokwawo kubantu abathile abachaphazelekayo ngenxa yesigidi sokuzalwa.
Kwixesha lokuhlaselwa, i-immune system iqala ukujolisa nokutshabalalisa inani elincinci le-neurons ngaphakathi kwe- hypothalamus yengqondo. Ezi i-neurons, okanye iiseli zesigulane, ziqukethe i-neurotransmitter ebizwa ngokuba yi- hypocretin okanye i-orexin.
Njengoko lesi sifo sitshintsha, yonke iqoqo lama-60,000 ukuya kuma-70,000 amaseli esisigxina kwi-hypothalamus iyatshatyalaliswa ngonaphakade. Ngenxa yoko, inqanaba le-hypocretin efunyenwe kwi-cerebrospinal fluid (CSF) ehlamba ingqondo ihla i-zero.
Oku kunokulinganiswa nge- puncture lumbar . Xa izigulane zinezintlu, uhlobo lobuthathaka olubangelwa yimvakalelo, amanqanaba e-hypocretin aqhelekanga kwaye oku kubonisa uhlobo lwe-1 lwe-narcolepsy.
Ukongezelela, le nkqubo yonakaliso yenzakazo iyakucasulwa emva kokusuleleka (ngokuqhelekileyo kubanda okanye umkhuhlane).
Ngoku kutshanje, ingozi eyongezelelekileyo yokuxilwa kwinqwaba yafunyanwa emva kokugonywa nge-Pandemrix, i-H1N1 igciwane lokukhusela i-H1N1 ekhutshwe kwixesha lomkhuhlane we-2009-2010 kwaye isetyenziswe kuphela eYurophu. Ukusetyenziswa kusukile ukusukela.
Isimo esinyameko
Ngelishwa, ukutshatyalaliswa kwezi sele zengqondo ngokugqibeleleyo kwaye ilahleko elibangelwa yiyo sigxina. Umonakalo owenziweyo awukwazi ukuhlaziywa ngoku. Ngoko ke, i-narcolepsy yimeko engapheliyo efuna unyango oluqhubekayo.
Kukho unyango oluninzi olunokuba luncedo ekuphatheni iimpawu ezinxulumene neengqungquthela. Ezi ziquka imishanguzo enomdla , njenge- Provigil okanye i- Nuvigil , kwakunye neyeza ezikhusela i-cataplexy, njenge- Xyrem .
Ukuba unobungozi obunzima, kubalulekile ukuthetha ngongcali yokulala ongakwazi ukulungiselela unyango kwiimfuno zakho ezithile. Nangona ukukhubazeka kudla ngokuqhubekayo, abanye abantu banako ukwenza uhlengahlengiso kunye nokusetyenziswa kwamachiza ukugcina imisebenzi eminingi yemihla ngemihla.
Ithemba lihlala kwiminyaka ezayo. Iinkqubo ezitsha zonyango ziyakwazi ukunqanda, ukucotha, okanye ukuguqula ukutshatyalaliswa kwala maseli e-hypocretin equlethwe ngabantu. Ukuhlaziywa kwakhona kwale nxalenye yeeseli zengqondo kunye neziqu ze-stem cell transplants zingaphumelela kwakhona.
Nangona oku kungenelela kusekude ekugqibeleni, kusekho ithuba lokuba olunye usuku lokuhlaselwa kwezilwanyana lunokuthi luhambe ngokukodwa kulabo bahluphekileyo.
Imithombo:
Isitatimende se-CDC malunga neengxowa-mkhuhlane ezilandela ukugonywa kwe-Pandemrix influenza eYurophu.
Kryger, MH et al . "Imigaqo kunye nokuSebenza kweMithi yokulala." Elsevier , edition 5. 2011.