I-pulmonary artertension isifo esibi kakhulu apho kukho unyango kodwa akukho unyango, ngokweNational Heart, Lung, ne-Blood Institute. I-pulmonary blood pressure yonyango ingabangelwa okanye iyenzeka ngenxa yesinye imeko yesibini.
Iziphumo zengcinezelo yexinzelelo
I-pulmonary artertension arterial (okanye i-high blood pressure kwimaphapha) yinto engavamile kodwa yonyango kakhulu.
Le ngxaki, engahambelani nokunyuka kwengcinezelo yegazi (system pressure), ibangelwa ukulahlekelwa kwemitha yemiphunga kunye nokulahlekelwa kwezinto eziguquguqukayo (umthambo) we-pulmonary umzobo onomsebenzi wokubuyisela igazi kwimiphunga ye-oxygenation.
Izifo ZamaRheumatic Associated With Pulmonary Hypertension
I-hypertension ye-pulmonary idibene nenani leemeko. Kwizigulane ezinobunzima obukhulu bemiphunga (i-fibrosis njengoko ibonwe kwi- scleroderma kwaye ngamanye amaxesha i- rheumatoid arthritis ), kukho umthamo wamaphaphu owehlayo ukuze intliziyo ikhulise uxinzelelo oluyimfuneko ukuphalaza igazi nge-pulmonary umthambo kwimiphunga. Ezinye izigulana ziphuhlisa umthamo we-pulmonary umxinzelelo ngenxa yokunciphisa umthamo. Oku kuya kubonakala kwiimeko ezifana ne-scleroderma (ngokuphindaphindiweyo kwifom encinane ebizwa ngokuba yi-CREST) okanye ngaphantsi kwe-lupus (systemic lupus erythematosus). Kungekudala olu hlobo lwengqondo yomshukela lufunyaniswe ukuba ludibana nokusetyenziswa kweziyobisi ezingasemarike.
Iimpawu
Iimpawu zeli meko ziquka ukuphefumula kwentlungu kunye nentlungu yesifuba. Ukuxilonga kunokucetyiswa yindlela engavumelekiyo ye-intliziyo (i-echocardiogram). I-catheterization ye-cardiac (i-catheterization yenhliziyo) eneengxaki ezithile zonyango ngokuqhelekileyo zenziwa ukuze kuqinisekiswe ukuxilongwa.
Unyango
Kwixesha elidlulileyo, kwakungekho unyango oluncinane olukhoyo kule ngxaki eqhubekileyo.
Ngethamsanqa, kukho iindlela zokwelapha ezitsha ezikhoyo ukunceda izigulane ngeemeko zazo kubandakanya:
- i-epoprostenol (i-short-acting drug that requires infusion continuously with IV)
- treprostinil (elawulwa yi-infusion ephantsi)
- umphathi (ngomlomo)
- sildenafil (ngomlomo)
- iloprost (inhaled)
Iinkqubo zokongeza ezongezelelweyo ziquka i-oksijeni, i-blood thinners, i-diuretics ne-cardiopulmonary rehabilitation. Ukuba ufumene le ngxaki, kukulungele ukubona udokotela wemiphunga onobuchule kule ngxaki.
Impendulo eyanikwe nguScott J. Zashin, MD, uprofesa oncedisayo wezonyango kwiYunivesithi yaseTexas Southwestern Medical School, iCandelo leRheumatology, eDallas, eTexas. UDkt. Zashin naye uhamba noogqirha kwii-Hospital zasePresbyterian zaseDallas nasePlano. Ungumntu we-American College of Physicians kunye ne-American College of Rheumatology kunye nelungu le-American Medical Association. UDkt. Zashin ngumlobi weArthritis ngaphandle kobuhlungu - Ummangaliso we-Anti-TNF Blockers kunye nombhali-mbhali we- Natural Arthritis Treatment .