I-Nephrotic syndrome inokuhamba kunye nesifo sesifo ngenxa yesifo sikashukela, iziyobisi, njl
I-Nephrotic syndrome idibanisa iziphumo ezithile zonyango ezingabonwa kwizigulane ezinezifo zengqondo. Ngoko ke, ukuxilongwa kweklinikhi kwaye akusiyo isifo ngokwalo. Ingabonwa kwiimeko ezahlukeneyo ezikhokelela kuyo. Ukuhlanganiswa kwezinto ezingaqhelekanga ezidibene ndawonye phantsi kwe-ambulula i-term nephrotic syndrome ziquka:
- Iproteinuria ephezulu, okanye ukulahleka kwinqanaba eliphezulu leprotheni kumchamo
- Iprotheni ephantsi yegazi
- I-Edema / ukuvuvukala emzimbeni
- Inqanaba eliphezulu le-cholesterol egazini
- Ukuthambekela okunokwenzeka ukwakha i-blood clots
Indlela Ephuhliswa ngayo
Ukutshintshwa kweentso '(ebizwa ngokuba yi- glomerulus ) kunokukhokelela kwi-nephrotic syndrome. Ezi zinguqu zinokuthi zenzeke ngokwazo ngaphandle kwengcaciso ecacileyo kodwa ziyabonakala ngokuqhelekileyo ngenxa yomonakalo ezintsheni 'ukuhlunga kwezinye izifo ezikhankanywe ngezantsi. Kungakhathaliseki ukuba yintoni isizathu, ukuguqulwa kweso sakhiwo sefayili kubangela ukungabikho komsebenzi walo.
Ngokuqhelekileyo iifayile zezintso zifakwe ngendlela enokuvumela kuphela izinto ezithile / iibhoksi eziphuma egazini ukuya emcinini. Ikhumbule kwiimolyuli ezinkulu njengeeproyiyini zeeprotheyini ezitholakala egazini (enye yazo i-albumin). Kwi-nephrotic syndrome, irayiliti ilahlekelwa amandla ayo okubandlulula phakathi kwezinto ezidlulayo kuyo, kwaye nakwii-molecule ezinkulu njengeprotheni ziqala ukuphuma kumchamo.
Oku kubeka i-cascade yeziganeko ezikhokelela kwi-nephrotic syndrome epheleleyo. Ngendlela, izinto ezilungileyo ziwela emcimbini kunye nombi, kwaye umzimba uqala "ukuphosa umntwana ngaphandle kwamanzi okuhlamba".
Ziziphi izifo ezichaphazela iinjongo ezenza i-Nephrotic Syndrome
I-Nephrotic syndrome inokuvela kwiimeko ezahlukeneyo.
Nangona kunjalo, ngamanye amaxesha akukho nto ingabonwa. Eminye yezifo eziqhelekileyo eziyaziwayo ezenza utshintsho olukhokelela kwi-nephrotic syndrome ziquka:
- Iswekile yemellitus
- Amanye amachiza afana ne-bisphosphonates (asetyenziswa ukunyanga i-osteoporosis), i-NSAID i-painkillers, kunye
- Izifo ezenza ngokuzenzekelayo njenge-lupus
- Inokuthi ifumaneke ngokuhambelanayo namanye amachiza
- Izifo ezingapheliyo ngeendlela ezingaqhelekanga zokuzikhusela ngamanye amaxesha zingakhokelela kwi-nephrotic syndrome. I-HIV ngumzekelo oqhelekileyo.
- Ezinye iibhoksi zendalo
Ukuxilongwa
Njengoko kukhankanywe ngasentla, ukuxilongwa kwe-nephrotic syndrome kubandakanya ukuxabisa iinqununu zeziphumo ezenza i-nephrotic syndrome. Ngokuqhelekileyo, isikrokro sisuswa kwisigulane ngokungekho esinye isizathu sokuvuvukala ngaphakathi kwamehlo okanye kwiintloko. Uphando lwale nto luya kubandakanya ukuhlolwa komchamo. Oku kuya kubonakalisa ukulahlekelwa kakubi kweprotheni kumchamo. Ngamanye amaxesha izigulane ezineeprotheyini eziphakanyisiwe kakhulu emanzini ziya kubhala isikhalazo okanye i-sud in urine. Ezinye izinto ezingaqhelekanga njengezinga eliphantsi leprotheni egazini okanye amanqanaba aphezulu e-cholesterol nazo ziyaqatshelwa kwiimvavanyo zebhu.
Zonke ezi mvavanyo zingentla ziza kubakho ukuba zichaze isizathu sokuba nesifo se-nephrotic. Ukuba isizathu asibonakali kwimbali yekliniki, kufuneka ukuba i-kidney biopsy iyenze ukuba yenze isifo esithile esibangela i-nephrotic syndrome.
Iingxaki
I-Nephrotic syndrome ngenxa yezifo ezithile ziyakwazi ukuzilungisa ngokwazo. Nangona kunjalo, i-nephrotic syndrome engakhange ifakwe ingenakho imiphumo emibi.
- Eyona nto ibonakalayo yenyusa ukuqhuma kweentso , kunye nokukwazi ukucoca iimveliso zentengiso kunye nokugqithiseleka komzimbeni.
- Amazinga aphezulu e-cholesterol abonwa kwi-nephrotic syndrome iya kwandisa umngcipheko wesifo senhliziyo.
- Izigulana nazo zinomngcipheko ophezulu wokwenza amacandelo egazi kwaye ziyakwazi ukubona izinto ezinjenge-vein thrombosis kunye ne-pulmonary embolism.
- Ingozi eyongeziweyo yezosuleleko ibonakala ngenxa yokulahlekelwa kwamagciwane okukhusela (ayenayo iiprotheni) kumchamo.
Unyango
Ukuze uphathe isifo se-nephrotic, kufuneka uqale uqonde isizathu sokuba une-nephrotic syndrome. Ukuba isizathu asibonakali kwimbali yeklinikhi yedwa, i-kidney biopsy iya kufuneka ukuba uphendule lo mbuzo. Emva kokuba kuboniswe isizathu esithile, unyango lunokuquka ukudibanisa kwamachiza ahlukeneyo avela kwi-renin-angiotensin ukuvimbela imishanguzo yengcinezelo yegazi (ebizwa ngokuba yi-ACE inhibitors okanye i-angiotensin receptor blockers), kwi-steroids, kwenye imithi yokuxilonga (njenge cyclosporine), njl. imeko ephathwa kakuhle ngokufuna ingcebiso yesazi se-nephrologist .
Khumbula, umphumo wonyango ophumelelayo kwakhona uya kuxhomekeka kwisizathu. Amanye amaziko akwazi ukuphendula unyango, ngelixa abanye bengasayi kubuya umpu omkhulu apho.
Ulwaphulo oluthile luya kufuneka ludibaniswe nokugxilwa ekuphatheni iingxaki eziza kuphuhliswa. Ngenxa yoko iipilisi zamanzi ezinjenge-furosemide ziyimfuneko yokuphatha ukukhukhuma okukhulu okubonakalayo. Igalelo legazi lingafuneka ukuba ezinye izigulane zithintele ukukhusela igazi. Ukutya okuphantsi kwe-sodium ku soloko kuyimfuneko.