I-Antiphospholipid syndrome (APS), eyaziwa nangokuthi 'igazi elinamathele,' liyi-disorder disorder-isiphumo sesistim somzimba sisiguqulele umzimba kwaye sihlasele. Kwimeko ye-APS, umzimba wenza ama-antibodies kwiiprotheni zawo zegazi.
I-Antiphospholipid syndrome iyakwenzeka kubantu abangenawo naziphi na izifo ezihambelana nazo. Oku kuthiwa yi-APS ephambili.
Ingxaki ingenzeka kwakhona nge- systemic lupus erythematosus (SLE) okanye enye i-dismune disorder. Oku kuthiwa yi-APS yesibini.
Ixesha eliphilileyo i-antiphospholipid syndrome ayifakwanga. I-APS antibodies inokufumaneka kwi-50% yabantu abane-lupus kunye ne-1% ukuya kwi-5% yabemi bonke abantu. I-Antiphospholipid syndrome ngokuqhelekileyo ivela kubancinci kubantu abadala, kodwa ingaqala nanini na.
Iimpawu
Ngokumalunga nama-antibodies, umzimba uqala ukuvelisa ama-blood clots. Amacwecwe egazi angavimbela iirriyiti kunye nemithanjeni, ukunqumla ukunikezelwa kwegazi kwinxalenye yomzimba. Iimpawu zamanye amava avela kwindawo (s) kunye nemiphumo yegazi lamacenge :
- Imifuno okanye imirhoxo yeengalo okanye imilenze - Izambatho zingabangela ubuhlungu, ukuvuvukala, ukugada, ukubetha kwezandla okanye iinyawo, okanye umlenze wesilonda. Ukuba ukunikezelwa kwegazi kwakunqunyulwe ngokupheleleyo kwinxalenye, njengokwintwane, umntu angahle alahlekelwe yizwane.
- Iimitha zeentliziyo - Izambatho zingabangela intlungu yesifuba okanye ukuhlaselwa kwentliziyo . Umntu angaba neentliziyo ezibubulayo okanye iingxaki zentliziyo.
- Imikhumbi yegazi yekhumba - Iingubo zingabangela izivunguzo ( purpura ) okanye i-blotchy, i-rash ehlambulukileyo ebizwa ngokuba yi-liveo reticularis.
- Imithambo yegazi yengqondo - I-clot eyanqumla ukunikezelwa kwegazi kwingxenye yengqondo ibangela ukubetha . Umntu onama-APS unokufumana ukuphathwa kwamakhanda okanye ukutshatyalaliswa .
- I-Placenta ngexesha lokukhulelwa - Abasetyhini abane-APS banokuba neentlungu ezingaphantsi okanye ukuzalwa kwangaphambili.
Ifom ephezulu kakhulu ye-antiphospholipid syndrome, ebizwa ngokuba yi-APS enobungozi, ivela xa amalungu amaninzi angaphakathi ahlakulela ama-blood clots kwixesha leentsuku ukuya kwiiveki.
Ukuxilongwa
Ukuxilongwa kwe-antiphospholipid syndrome incike kwiimpawu kunye nezibonakaliso zezibonakalisi, kunye neemvavanyo zelabhoratri. Ukuba umntu uye waba negazi kwiimilenze ngaphandle kwesizathu esithile, umzekelo, i-APS inokuthi ityala. Uvavanyo lwegazi lwe-antiticardiolipin antibodies lunokunceda ukuqinisekisa ukuxilongwa. Ezinye iziphumo zovavanyo ezingavamile, ezifana neeplatelets ezinciphile okanye i- anemia , ingaba khona. Ukucwaninga kwe-tomography (CT) okanye i-imagery magnetic resonance (MRI) inokuqinisekisa ubungqina begazi.
Unyango
Unyango lwe-antiphospholipid syndrome isekelwe kwimpawu zomntu. I-APS enobungozi idinga ukulaliswa esibhedlele. Abanye abantu abanezixhobo zokulwa nezifo kodwa akukho zibonakaliso ze-APS zingaqaliswa kwi-aspirin ye-dose ephantsi imihla ngemihla ukunceda ukunciphisa umngcipheko we-clots blood forming. Ukuba i-clot yegazi ifunyenwe, umntu uqalwe kumachiza e-anticoagulant njengeCoumadin (warfarin) okanye uLovenox (enoxaparin).
Ngamayeza kunye nokuguqulwa kwendlela yokuphila (njengokugweba ixesha elide lokungasebenzi, apho iifom ezinokuthi zenze khona emilenzeni), abaninzi abantu abane-primary antibospholipid syndrome bangakhokelela kwimpilo, ephilileyo.
Abo bafumana ii-APS zesekondari banokuba neengxaki ezingaphezulu ngenxa yeemeko zabo eziphantsi kweempawu ze-rheumatic okanye ezizimeleyo.
Umthombo:
"Antifospholipid Antibody Syndrome." Amanqaku olwazi. 15 Oktobha 2006. I-APS Foundation yaseMelika.