I-Mycosis fungoides (MF) yinto eqhelekileyo ye- T-cell lymphomas , iqela leentsholongwane ezingabonakaliyo ezikhula esikhumbeni. I-Sezary syndrome, ifomu engavumelekanga, ivela malunga nama-5% kuwo onke amacala e-mycosis fungoides. EUnited States, malunga nama-1000 amatyala amatsha e-mycosis fungoides ayenzeka ngonyaka.
I-MF ichaphazela amadoda kabini ngokuphindaphindiweyo njengabasetyhini, kwaye iqheleke kubantu abamnyama kunabantu abamhlophe.
I-Mycosis fungoides inokuqala nanini nayiphi na iminyaka, kodwa i-age eliqhelekileyo ineminyaka engama-50 ubudala. Isizathu sesifo asiyazi.
Iimpawu ze-Mycosis Fungoides
I-Mycosis fungoides iyaqhubeka kwizigaba, ezichazwa yimpawu zesikhumba, eziquka:
- Isigaba sePatch - Ikhumba livelisa iiplanga ezibomvu, ezibomvu; Abantu abanobumnyama abanokuthi bangabonakala njengobunzima obukhulu okanye obumnyama kakhulu. Ezi zikhumba zesikhumba zininzi kakhulu. Ezinye iindawo zingaphakanyiswa kwaye zikhuni, kwaye ziyaziwa njengeiplati. Iipatches kunye neeplathi zivame ukubonakala kwiindawo, ukucwenga, iinqumlo, phantsi kweengalo, kunye nasebeleni / esifubeni.
- Isigaba se-tumors se-Skin - i-Red-violet ephakanyisiweyo (iigununu) zivela kwaye ingaba yimihlathi (njengama-mushroom) okanye isilonda.
- Isilu esibomvu (erythroderma) isigaba - Ukongezelela kwiipatches kunye nezicubu, isikhumba somntu singakha iindawo ezinkulu ezibomvu ezinomtsalane kunye ne-scaly. Ubunzima besikhumba ebusweni bunokukhupha, kunye nesikhumba seentende kunye neengqungquthela zingase zenzeke kwaye zenzeke.
- I-lymph node stage - Kule nqanaba, i-mycosis fungoides iqala ukufudukela kwezinye iindawo zomzimba. Iinkalo zokuqala ezichaphazelekayo zi-lymph nodes, ezinokutsha, kwaye kaninzi ziba ngumhlaza. Umdlavuza weMF ungasasazeka kwisibindi, emaphaphu, okanye ematyeni.
Ukuxilongwa kweMeko
Le meko yaziwa nangokuthi i-Alibert-Bazin syndrome okanye i-granuloma fungoides.
Ngokuqhelekileyo, kukho iminyaka engama-6 ukususela kwixesha iimpawu ziqala de ukuxilongwa kwe-mycosis fungoides. Ngesi sifo, ukudideka nezinye iimeko ziqhelekile njengoko izigaba zokuqala zesi sifo zifana ne-eczema okanye i-psoriasis.
Ukuze kuhlolwe kakuhle i-mycosis fungoides, isampuli yesikhumba inokuthathwa (i- biopsy yolusu ) kwaye ihlolwe ngesi sifo. Iimvavanyo zeLebhu zenzelwa ukuchonga ukuqhubela phambili komhlaza.
Ukuqonda izigaba ezahlukeneyo zesifo, iimvavanyo ezahlukeneyo zenziwa ukuhlola i-lymph nodes, igazi kunye nezitho zangaphakathi. Uninzi lwezigulane lubonisa iimpawu ezigcinwe kuphela esikhumbeni, njengama-patches (amabala ahlukeneyo) kunye namacwecwe (aphakanyiswe okanye aphethwe 'amabala').
Unyango lweMF
Ukuba i-mycosis fungoides isesigaba sokuqala, unyango olunjengama-steroid creams, unyango olusisigxina, i-chemotherapy esetyenziselwa ulusu, okanye i-ray ye-electron radiation ingasetyenziswa. Injongo kukubeka umdlavuza weMF kwi-remission, edla ukuhlala ixesha elide.
Ukuba isifo somntu asiphendulanga unyango lwesikhumba, okanye eso sifo siphumelele kwisigaba somzimba, izifo zonyango ezifana ne-recombinant alfa interferon okanye i- chemotherapy zingasetyenziswa. Ngelishwa, akukho nonyango ye-mycosis fungoides, ngoko inani lexesha umntu aphila ngalo nesi sifo kuxhomekeke ekubeni lide liye lasasazeka kangakanani ngexesha lifumaneke kwaye unyango luqala.
Umthombo:
I-Pinter-Brown, iLC (2002). Mycosis fungoides. eMedicine.