I-Cystic fibrosis iyisifo esongela ubomi, ekuhambeni kwexesha, ukuphazamisa ukusebenza kwemiphunga. Akukho nonyango ye- cystic fibrosis kwaye akukho mntu unyango olufanelekileyo lwe-cystic fibrosis. Kunoko, izicwangciso zonyango ziyahlukahluka ngokweemfuno zakho. Ngenxa yokuba i-regimen yonyango iguquke njengokuba i-cystic fibrosis iyaqhubeka, kuyimfuneko ukuba uhlolisiswe ngugqirha ogxininise ekwenzeni unyango lwe-cystic fibrosis.
Unyango lwe-cystic fibrosis luwela kwiintlobo zintathu: ukulungiswa kwendlela yokuhamba nomoya ukukhupha imiphunga ye-mucus, ukuxilongwa kweyeza ukuze uvule i-airways ne-pancreatic supplementation ukuncedisa ukugaya.
Ngethamsanqa, ukuqhubela phambili kwezokwelapha kuye kwaba negalelo ekuphuculeni ngokugqithiseleyo abantu abano-CF. Ngamhlanje ngokunyanga okufanelekileyo, umntu ono-CF unokulindela ukuba aphile kwiminyaka ephakathi. Nangona kunjalo, nceda ugcine ukhumbule ukuba isitshixo sokuphila ubomi obunempilo kunye ne-cystic fibrosis kukusebenza ngokusondeleyo kunye nodokotela wakho, ukuzinyamekela kwaye uhambelane nezicwangciso zonyango.
Ukuba une-cystic fibrosis, uya kuthatha unyango imihla ngemihla ebomini bakho bonke. Uninzi mhlawumbi uza kufumana enye okanye ngaphezulu kwezi ziyeza kwiyeza lakho kwikhabhinethi ngexesha elithile kunyango lwakho.
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TobiUTobbi uyisifo sokulwa ne-antibiotic esetyenziselwa ukuphatha iPseudomonas aeruginosa, ibhaktheriya ekhula kwimiphunga yabantu abaninzi abane-cystic fibrosis. Funda oko kufuneka ukwazi ngoTobhi, kubandakanywa nemiphumo emibi, izilumkiso zokhuseleko kunye noxanduva lwemali.
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PulmozymeI-Pulmozyme (dornase alfa) yinxalenye ebalulekileyo yokonyango kubantu abaninzi abane-cystic fibrosis. Funda oko kufuneka ukwazi ngePulmozyme, kubandakanywa nemiphumo emibi, izilumkiso zokhuseleko kunye noncedo lwezemali.
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Enzyme zePancreaticUninzi lwabantu abane-cystic fibrosis luthatha i-enzyme ye-pancreatic substitution xa yidla ukuba ivumeleke ukuba ithathe izondlo kunye nokuphepha ukuphazamiseka kwe-malabsorption. Funda okufuneka ukwazi malunga ne-pancrelipase, kubandakanywa nemiphumo emibi, izilumkiso zokhuseleko kunye noncedo lwemali.
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Imithi echasayoNgamanye amaxesha ukusetyenziswa kwemithi evuthayo kuvulelwe abantu abane-cystic fibrosis ekuncedeni ukunciphisa ukuvuvukala kwamaphepha emoyeni nokuphucula umsebenzi wamaphaphu. Funda into ofuna ukuyazi malunga neentlobo ezahlukeneyo zemithi echasayo, kubandakanywa nini kunye nendlela imishanguzo echasayo ngayo isetyenziselwa unyango lwe-cystic fibrosis, iingeniso ezinokubakho kunye nemingcipheko ekhoyo yokusetyenziswa kakubi.
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BronchodilatorsAbantu abaninzi abane-cystic fibrosis basebenzisa imithi ebizwa ngokuthi i- bronchodilators ukunceda ukuphucula umphunga.
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AzithromycinI-Azithromycin yintsholongwane eyenziwa ukunyanga abantu abane-cystic fibrosis (CF) okanye ngaphandle kwe-cystic fibrosis. Funda malunga nemiphumo emibi, izilumkiso zokhuseleko kunye nezinye izinto ofuna ukuba wazi.
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Inhaled Hypertonic SalineI-hypertonic saline yonyango oluthembisayo elinokukunceda imfihlo yokunciphisa nokunciphisa iintsholongwane zokuphefumula kubantu abane-cystic fibrosis. Funda ukuba i-hypertonic saline yiyiphi indlela, isebenza ngayo, ngubani oyisebenzisayo kunye nezibonelelo ezinokubakho kunye neempembelelo zonyango lwe-hypertonic saline.