I-Hematohidrosis-imeko engabonakaliyo, engekho yobomi kunye nexinzelelo
Nangona i-swem-sweat-okanye i-hematohidrosis-ingabonakala iyantyaza, kwindlela ebonakala ngayo, iimeko ezibuhlungu. Imiphumo emibi yale meko engabonakaliyo yimiqondo yengqondo, kwaye abantu abane-hematohidrosis banenkathazo yokusebenzisana nabanye ngenxa yokoyika ukuba baqale ukuphuma, ikakhulukazi phantsi kweemeko ezixinzelelekileyo.
Kule ncwadi, kukho iincwadana ezimbalwa zeengxelo, okanye i-akhawunti, okanye ukukhukhulwa kwegazi.
Kukho ezinye iingcamango malunga nokuba zeziphi izinto ezibangelwa okanye ezibangelwa i-hematohidrosis, kodwa inkxaso yokuxhasa ayikho. Ukongezelela, akukho nonyango olusekelwe ku-hematohidrosis. Makhe sibone ngento encinci esazi ngayo ngokukhipha igazi.
Iimpawu
I-Hematohidrosis yenzeke ngaphezu kwesikhumba esingahambelaniyo, esingenasiphako ngaphandle kwezilonda. Ngokuqhelekileyo kwenzeka ngexesha loxinzelelo lwengqondo. Kwakhona kwenzeka ngexesha lokuzilolonga okanye ukulala. Umfutho wegazi uphefumlelwe ebusweni nasezandleni. Kuyathakazelisa ukuba i-hematohidrosis iye yabhalwa kwintombazana eneminyaka eyi-10 kunye ne-hemolacria, enye imeko engaqhelekanga eyenza iinyembezi zamanzi. (Le ntombazana yabhekana negazi kunye neinyembezi.)
Iziganeko zesifungo segazi ziye zabonwa ngokugqibela phakathi kwemizuzu emihlanu ukuya kwemihlanu. Kubonakala ngathi, ukujuluka kugalelwe igazi kunye nokuzikhupha ngokukhawuleza.
Ukuxilongwa
Ukongeza kwimbali yonyango, i-hematohidrosis ifunyaniswa xa iiselom zegazi ezibomvu (oko kukuthi, i-erythrocytes) zigcinwa kwi-sweat sweety under the microscope.
Amanye amanyathelo e-laboratory yegazi aphakathi kwemida eqhelekileyo kubandakanya inani elipheleleyo leeseli zegazi, iphaneli yamathambo kunye nezifundo ze-coagulation. Ukongezelela, iziphumo ezivela emzimbeni nangokwenyuka kwezilwanyana zingabonakali.
I-skin biopsies yenziwe ngabantu abambalwa abanokufumana i-hematohidrosis.
Iziphumo zezi biopsies azihambelani kwaye azihambelani, ezinye zibonisa i-histology eqhelekileyo ngelixa abanye babonisa ukudibanisa kwemithambo yegazi ye-periglandular, ukuvuza kwegazi malunga ne-capillaries ye-dermal, okanye iiseli ezibomvu zegazi kwiingcingo zezinwele zezinwele.
Ukwahlula omnye-okanye enye indlela-ukuxilongwa kwezigulane ezinikezela ngegazi eliyigazi liyi-disorder disorder. Ingxaki eyiyo ingxaki enkulu yengqondo eyenza isigulane esithatha indima egulayo, kunye nokubonisa ngobuxoki ngokugula, ukulimala okanye iimpawu zomzimba. Ngokufanayo, ukuxhatshazwa kwakhona kuthathwa njengoluhlu lohlulo lwe-hematohidrosis. Okubaluleke kakhulu, ukuxhatshazwa ngokungafaniyo nokungafani kwintlupheko enenjongo: Ukugxeka kubangelwa yimfuyo. Ukulawula izifo ezibuhlungu kunye nokukhathazeka, izigulane ezinikezela ngegazi elikhukhulayo zingaqwalaselwa ngeklinikhi ngenxa yegazi.
Ngokusekelwe kwimiba yecala kwincwadi, kubonakala sengathi i-hematohidrosis inokunyusa ukugula kwengqondo, njengokudandatheka, ukukhathazeka ngokubanzi, kunye nokuphazamiseka kwesifo. Ngokudabukisayo, abantu abanalo mqathango bazihlukanisa nabanye ngenxa yokuhlazeka nokuxhalaba.
Izizathu
Ngokuqhelekileyo, kucetywayo ukuba imilambo yegazi ejikeleze i-eccrine sweat glands igxilise igazi kwiindawo ezinobuncwane ngenxa yeengxaki ezingavamile kunye nokunyuka kwexesha (oko kukuthi, ukuhluthwa).
Ezinye iinkcazo ziphakamisa uxinzelelo lwegazi oluphezulu kunye nokuvuvukala kwemithambo yegazi (oko kukuthi, i-vasculitis) njengezimbangela zokuphuma kumziza.
Ezi ngcamango, nangona kunjalo, zihlala zingavunyelwe, kwaye ukuphuma kwegazi okufanayo kufumaneka kwiintlobo zezinwele kunye nakwiindawo ezingenasifo. Enyanisweni, kwincwadi, izigulana ezimbalwa ziye zanikela nge-otorrhea enegazi, okanye i-earge drainage.
Kwinqaku le-2015 elibizwa ngokuthi "Hematohidrosis: ingcaciso kwi-pathology," u-Uber kunye noogxa babhala oku kulandelayo malunga ne-hematohidrosis:
Ezinye iingcamango zicetywayo, kubandakanywa: ukwandiswa kwengcinezelo yeengcambu ezikhokelela ekuhambeni kweeseli zegazi ngokusebenzisa iidonsi zeengqungqa zomzimba; i-vasculitis yeenqanawa ezidaka; kunye nokwandisa ukusebenzisana novelwano olukhokelela ekunqandeni kweenqanawa zomhlaba kunye nokunyuka okulandelelanayo, okuvumela ukuhamba kwequlatho yegazi kwimida.
Kule nqaku, u-Uber kunye noogxa bebonke baqala ukubhalwa kwekhonkco phakathi kweengqungquthela ze-hypertensive kunye ne-hematohidrosis. Ukusebenzisa iliso lokunyamezela kwengcinezelo yegazi eli-24 ngeeyure ezingama-24, abaphandi baqaphele ukuba ukunyanzelelwa kwegazi kumfazi oneminyaka engama-18 ubudala onama-18/90 ngexesha lokuphuma kwegazi.
Unyango
Akukho ndlela eqinisekisiweyo yokuphatha i-hematohidrosis. Ipropanolol, ebizwa ngokuba yi-beta-blocker esetyenziselwa ukuphatha uxinzelelo lwegazi oluphezulu, incede abanye abantu ngale mqathango. Isizathu sokuba kutheni i-beta-blockers isebenzayo kunyango lwe-hematohidrosis inokubakho nento yokuba ukungenwa kwembeko, okujoliswe yi-beta-blockers, mhlawumbi idlala indima kule mqathango.
> Imithombo:
> Biswas S, Surana T, De A, Nag F. Icala elifuna ukukhupha igazi. Int J Dermatology . 2013; 58 (6): 478-480. https://doi.org/10.4103/0019-5154.119964
> Maglie R, uCaproni M. Iimeko zegazi ezithukuzayo: i-hematohidrosis syndrome. CMAJ . 2017; 189: E1314. https://doi.org/10.1503/cmaj.161298
> Praveen, BK, Vincent, J. Hematidrosis kunye neHemolacria: Ingxelo yeNgxelo. Indian J Pediatr . 2012; 79: 109. https://doi.org/10.1007/s12098-011-0449-2
> Uber M et al. I-Hematohidrosis: ingcaciso kwi-pathology. Int J Dermatology . 2015; 54: e542-e543. http://dx.doi.org/10.1111/ijd.12932