Ubuninzi Emva kokuxilongwa
Ukuba wena okanye othandekayo uye wafumanisa ukuba une- amyotrophic lateral sclerosis (ALS), ebizwa nangokuthi isifo sikaLou Gehrig, enye yemibuzo yakho yinto yokugxekwa kwesi sifo. I-ALS inempembelelo ebalulekileyo kwixesha lokuphila kodwa kukho unyango olunganciphisa ukulahleka komsebenzi kwaye luyakwandisa ubomi.
Yintoni i-ALS?
I-ALS isifo esinesifo esiphezulu segazi esichaphazela iiseli zesisongela engqondweni nasemgodleni.
Yisifo esiqhubekayo esichaphazela i-neurons yeemoto ezifikelela kwintliziyo ukuya emkhosini. Ezi zixhobo ze-neurons zilawula umzimba wonke. Ngokuhamba kwexesha, ingqondo ilahlekelwa amandla ayo okulawula ukunyakaza kwemizimba ngenxa yokufa kwezi zixhobo zomoya.
ALS Life Life
Umlinganiselo wokuphila komntu onesi-ALS uneminyaka emibili ukuya kwemihlanu ukususela ngexesha lokuxilongwa. Nangona kunjalo, ihluka kakhulu:
- Amaphesenti angama-50 abantu abane-ALS baphila ngaphezu kweminyaka emithathu.
- Ipesenti ezingama-20 zihlala iminyaka emihlanu okanye ngaphezulu.
- Ipesenti ezilishumi zihlala iminyaka eli-10 okanye ngaphezulu.
- Iipesenti ezintlanu ziza kuphila ngaphezu kweminyaka engama-20.
Iindlela zokwandisa ubomi obulindelweyo
Nangona kungekho nonyango ye-ALS okanye iindlela zokumisa ukuqhubela phambili kwesi sifo ngokupheleleyo, kukho ezinye izinto ongayenza ukuphucula ixesha lokuphila. Ezi ziquka:
- Amachiza: I- Riluzole isetyenziswe ukususela ngo-1995 yaye iboniswe kwiimvavanyo zeclini ezinokuphinda zikhunjulwe ngokungapheliyo ukuze zenze ixesha elingaphantsi kweenyanga ezimbini ukuya kwethathu lilinde ixesha lokuphila, nangona ezinye izifundo ezinzima kakhulu zibonise ukuba izidakamizwa zibe nefuthe elincinci. Ukongezelela, ezinye iziyobisi zisetyenziselwa ulawulo lweempawu ezinokukunceda ukuphucula umgangatho wobomi kunye nokwandisa ukusebenza. I-Radicava (edaravone) yavunywa ngo-2017. Kwizilingo zeklinikhi, yanciphisa ukuhla komsebenzi.
- Ukungena kwemvelo: Ukusetyenziswa kwe- non-vasive ventilation (NEV) kuboniswe ukulondoloza ukusinda phakathi kweenyanga ezi-7 ne-11, kuxhomekeke kwithuba elide elisetyenziswe ngayo imihla ngemihla kunye neempawu ezahlukeneyo zesigulane. Imoya ephambili ye-NEV i-positive vent-pressure ventilation, ephefumula ngokugqithiselayo kwimaski ehambelana nomlomo neempumlo.
- I-Percutaneous Endoscopic Gastronomy (PEG): Ityhubhu yokutya ifakwa kwisisu ize iphume ngaphandle komzimba ngokusebenzisa udonga lwesisu. Nangona uphando luye lwahluleka ukubonisa impembelelo eqhubekayo ngexesha lokuphila, i-American Academy ye-Neurology incoma ukuba i-PEG isetyenziselwa abantu abane-ALS ukugcina ubunzima bomzimba. Oogqirha abahlukeneyo baneengcamango ezahlukileyo malunga nexesha elifanelekileyo lokuyenza inkqubo ye-PEG kwaye baqale ukutya ngale ndlela.
ILizwi
Ukuqhubela phambili kuye kwenzelwa kwiminyaka yamuva kwenkxaso kunye nonyango lwe-ALS. Ukuzifundisa ngokonyango kunye neendlela zokunyamekela i-ALS kunokukunceda uqonde oku kulukhuni nokuxilongwa. Thetha ugqirha malunga nento ongayenza ukuze uncede umntu onesi-ALS aphile ngokukhululeka ngokukhawuleza kangangoko kunokwenzeka.
Imithombo:
> Izinto Okufanele Uzazi Nge-ALS. ALS Association. http://www.alsa.org/about-als/facts-you-should-know.html.
> Imibuzo ebuzwa rhoqo malunga neRadicava (i-Edaravone). ALS Association. http://www.alsa.org/research/radicava/radicava-xesha elide-asked-questions.html.
> Miller RG, kunye. al. Qalisa ukuhlaziywa kweParameter: Ukunyamekelwa kwesigulane nge-amyotrophic lateral sclerosis: Ukusetyenziswa kweziyobisi, ukondla kunye nokuphefumula (ubungqina obusekelwe kubungqina): Ingxelo yeCandelo leMigangatho yeMigangatho ye-American Academy ye-Neurology. Neurology 2009; 73; 1218-1226.
> Pinto S, uCarvalho MD. Ubomi obutsha obuphuculayo ekuphuculeni unyango lokuphulukana nokuphefumula kwizigulane ze-amyotrophic lateral sclerosis. Ulawulo lweeNdedeenerational Disease Management . 2014; 4 (1): 83-102. i-doi: 10.2217 / nmt.13.74.