I-Lymphangiomatosis iyisifo apho izicubu ezininzi (i-lymphangiomas) okanye i-cysts zikhula kwinkqubo ye- lymph yomzimba. Nangona ezi zicubu zingekho umdlavuza, zihlasela izicubu zomzimba kwaye zibangele ubuhlungu, ukuphefumula, kunye nezinye iimpawu ezixhomekeke kuye apho zivela khona. I-Lymphangiomas inokukhula emathanjeni, izicubu eziphathekayo, kunye nezitho zomzimba, kwaye ziyakwazi ukuphazamisa, ukunciphisa okanye ukutshabalalisa izicubu.
Yintoni eyenza i-lymphangiomatosis ayisaziwa.
I-Lymphangiomatosis isoloko ifunyaniswa kwiintsana kunye nabantwana abancinci kodwa ingenzeka nanini na. Ichaphazela bonke abesilisa nabesifazane bazo zonke iintlanga. Ngenxa yokuba i-lymphangiomatosis inqabile kwaye kunzima ukuyixilonga ngokuchanekileyo, ayaziwa ukuba bangaphi abantu abachaphazelekayo kulo lonke ihlabathi.
Iimpawu
Iimpawu ze-lymphangiomatosis zixhomekeka apho izilonda zikhula khona emzimbeni.
- Imipu - ingabangela ukukhwehlela okungapheliyo, ukuqhuma , ukuphefumula , ukuqokelela umkhuhlane ojikelezayo kwimipuphu
- Intliziyo-ngokukhawuleza kwentliziyo, intlungu yesifuba
- Isisu, amathumbu - iintlungu zesisu, isisongela, ukuhlanza, isifo sohudo
- Izintso - iintlungu, ukwanda kwengcinezelo yegazi
- Amathambo - intlungu, ukutyhafa kwethambo ekhokelela ekuqhekekeni, ukunyanzelwa kwamagxa emgodini
Ngexesha elide, omnye okanye ngaphezulu amathambo angathatyathwa yi-lymphangioma tissue, eyaziwa ngokuba yisifo seGrham. I-Lymphangiomas ayikhuli ebuchosheni ngenxa yokuba i-lymph system ayifuni kulo.
Ukuxilongwa
Ukuxilongwa kwe-lymphangiomatosis kusekelwe kwiimpawu kunye nobukho be-lymphangiomas emzimbeni. I-CT (computed tomography) iskena kunye ne-imagination magnetic resonance (MRI) isetyenziselwa ukuhlola isifo. Isampula (i-biopsy) yesistim isathathwa ukunceda ukuqinisekisa ukuba i-tumor i-lymphangiomas.
Unyango
I-Lymphangiomatosis ihamba ngokugqithisa ngokuhamba kwesikhathi. Njengoko iimvumi zikhula, zinokubangela iimpawu ezinzulu, ezinye zazo zingasongela ubomi, ezifana nokubangela ukuba i-fluid iqokelele kwimipuphu evimbela ukuphefumla. Ukutshatyalaliswa kokutshatyalaliswa kwezicubu kunokwenzeka, kodwa ezinye izicubu zinokuba nzima ukuba zisuswe ngokupheleleyo xa zisasazeka. Iyeza elithi Intron A (interferon alfa), i-chemotherapy, okanye unyango lwe-radiation lunokuba luncedo ekuphatheni lesi sifo. Ezinye iindlela zonyango okanye ukuhlinzwa kuthi luncedo ekunciphiseni ezinye iimpawu okanye iingxaki ezibangelwa yi-lymphangiomatosis. Ngokomzekelo, ityhubhu ingeniswa kwisifuba (thoracentesis) ukucima i-fluid egciniweyo, okanye utyando lwenziwa kwintsipho ukuze kunqunywe amazinyo.
Imithombo:
> "NgeLymphangiomatosis." I-Lymphangiomatosis & I-Gorham's Disease Alliance. 06 Septemba 2007. Lymphangiomatosis & Gorham's Disease Alliance.
> Marom, Edith, Cesar Moran, & Reginald Munden. "Lymphangiomatosis jikelele." I-American Journal ye-Roentgenology 182 (2004): 1068.
> Rostom, A Y. "unyango lwe-lymphangiomatosis ye-thoracic." IiNgxelo zeZifo ebuntwaneni 83 (2000): 138-139.