I-Frey syndrome yaziwa nangokuthi i-sweat sweating or hyperhidrosis
Emva kokutya ukutya okutshisayo kunye neentyatyambo, abanye abantu bayaphupha ebusweni-emlonyeni, ebunzini, ekhaleni, nangesikhumba. Kwabaninzi, le ngqungquthela ye-trigeminovascular iyinto eqhelekileyo.
Nangona kunjalo, ukujuluka ebusweni emva kokutya naluphi na uhlobo lokutya lubonakalisa imeko ebizwa ngokuba yi-sweat sweating, okanye hyperhidrosis. Ngaphezu koko, ukuqala kokukhupha kungabikho kuphela ekutshekeni kokutya kodwa kubangelwa ukucinga okanye ukuthetha ngokutya.
Izibonakaliso eziqhelekileyo zokukhupha ngokukhawuleza zibandakanya ukujuluka, ukuxubha, ubomvu, kunye nokuphazamiseka okuqhelekileyo kuvezwe kwinqanaba lehlathi. Ngokuqhelekanga, abantu abaneli meko baziva befudumele okanye intlungu ngokutshiza.
Ukukhukhuma okukhenkcezayo kunokuba kungonwabi kakhulu kwaye kuthintela kakhulu umgangatho wobomi bomntu. Ngokutsho kweSood kunye nabalobi-mbambano, ukukhukhumaza "kunokubangela ukukhubazeka okukhulu kwezenhlalakahle ezivela kwisidingo sokuhlaziya rhoqo ukuya ku-house-bound." Ngamanye amazwi, ukufuneka rhoqo ukuba "ukuphosa" ukukhupha kungenza kube nzima kwabanye ukushiya indlu.
I-iteration eqhelekileyo yohlobo lwe-hyperhidrosis yi-Frey syndrome. I-Frey syndrome ibhekisela kwisifungo sokugubha kunye nokutshatyalaliswa ngokusasazwa kwe-nerriculotemporal nerve. I-nerriculotemporal nerve inikezela ngoluvo kwicala lentloko. I-Frey syndrome ikwabizwa ngokuba yi-hyperhidrosis enomdla wesihlathi.
Yintoni iFrey Syndrome?
I-Frey syndrome ayinqabile, kunye nabangaphantsi kwe-20,000 baseMelika abaxilongwa ngonyaka.
Okubalulekileyo, i-Frey syndrome iphumela ekutheni i-revering ephosakeleyo yentsholongwane ejongene ne-salivation, i-sweating, ne-flushing. Kubizwa ngegama lesiFulentshi ye-neurologist, uLucia Frey, owachaza le meko ngokuthi "i-auriculotemporal nerve syndrome" ngo-1923.
UFrey washicilela ingxelo echaza ngokugula kwakhe emva kokuphathwa kwintsimi yasePoland eyayifumana isithukuthezi esinomdla emva kokulondoloza isilonda esinegciwane elichaphazelekayo elichaphazela i- parotid gland .
I-parotid gland iyona mkhulu kunazo zonke izigulane ze-salivary kwaye zisezingeni lesigama. Ifihla umlenze, owanceda ukugaya kunye nokutya. Nangona uFrey wayengesiye ugqirha wokuqala ukuba aqaphele le meko, wayengowokuqala ukuphazamisa imbilini ye-auriculotemporal ekuphuhlisweni kwesi sifo.
Ukukhululwa kwemali nge-parotid gland idibaniswa ngumbutho we-reflex arc obandakanya i-auriculotemporal nerve. Kubantu abane-Frey syndrome, emva kokulimala kwi-nerriculotemporal nerve, le ntsho ivuselela ngokungaqhelekanga. Esikhundleni sokubonelela nje nge-parasy gland, okuza kubangela ukugujwa okuqhelekileyo emva kokusungulwa kokutya, iimbombo ze-parasympathetic ze-auriculotemporal nerve ziphinde zihlaziywe ukuze zinikezele ukugcinwa kwemilenze kunye nemigudu yegazi engaphantsi, okubangelwa ukujuluka nokutshiza, ngokulandelanayo . Ngokuqhelekileyo, lo kuthunga nokuxhamla kungaphantsi kolawulo lovelwano.
Ngamanye amazwi, emva kokulimala i-auriculotemporal nerve, iimfayili zayo ezihlaziyekileyo zibuyela kwi-salivation kuphela kodwa zilawula ukujuluka nokutshiza emva kokuba umntu evuselelwe ukutya. Ngaphezu koko, kwabanye abantu, lo mzekelo we-sweat of sweating ungadlulela phambili ubuso kunye nokuchaphazela i-trunk, iingalo kunye nemilenze.
Ummandla ophezulu wendawo uchaphazelekayo, ngakumbi iimpawu.
Izizathu
Nantoni na eyonakalisa i-auriculotemporal nerve ingabangela i-Frey syndrome, kuquka oku kulandelayo:
- I-Parotid gland ukuhlinzwa (imbangela enkulu)
- Ukuxhwaleka okubi kumhlathi
- Ukuhlinzwa kwekhanda
- Ukusuleleka kwintsholongwane yommandla we-parotid
- I-Mandibular fracture
- Ukwaphuka kwe- temporomandibular
- Ugqirha ukuya kwi-joint temporomandibular
- Ukususwa kweengqungquthela ze-submandibular
- Ukususwa kwegciwane le-thyroid
- I-Thoracic sympathectomy (utyando lwenziwe ukulawula ukujuluka)
- Ukuxhatshazwa okanye ukulimala emva kokunikezelwa kwe-forceps (kwiintsana)
Kwiminyaka ye-1940, ukuhlinzwa ngokugqithisileyo kwe-parotid kwakusasazwa kwiUnited Kingdom ukujongana neemeko ezahlukahlukeneyo, zomibini ezingumdlavuza kunye ezingenanto.
Ukukhupha kunye nezinye iziphumo ezinobungozi, kuquka ukulimala komzimba, ukunciphisa ubuso, isifo se-fistula, i-hematoma kunye ne-keloids zaziqhelekileyo phakathi kwezigulane ezitholwe ngophengululo lwe-parotid gland. Ingqalelo, abantu abane-parotid gland yabo basuswe banako ukufumana ama-Frey syndrome kunokuba abo banesabelo se-parotid gland kuphela.
I-Frey syndrome ingabonakala nakwezinye iimeko ezilandelayo ze-neurological:
- Ubuso be-herpes zoster
- Ukulimala kweChorda
- Intloko yentloko
- I-diabetes neuropathy
- Encephalitis
- Syringomyelia
- I-Tumor kwi-trunk yesibeleko somlomo
Uninzi lwabantu abafumana ukujuluka okunomdla aluxhatshazwa yiyo kuphela-phakathi kwe-10 ne-15 ekhulwini labantu abayifumanayo bafuna unyango. Ukongezelela, emva kokuhlinzwa okwenziwe nge-parotid, iipesenti ezili-10 kuphela zezigulane zibika iimpawu ezibonakalisa le meko. Nangona kunjalo, ngokuqhubeka nokubuza imibuzo, iipesenti ezingama-30 ukuya kuma-50 zezigulane ziya kuvuma kwiimpawu zokukhupha. I-Frey syndrome ibonakala iphakathi kweenyanga ezili-1 ukuya kwezi-12 emva kokuhlinzwa.
I-Frey syndrome inokwenzeka kubantu kubani na ubudala. Nangona kunjalo, akunqabile kwiintsana nabantwana abaye bakhathazeka ngokwenene kwindawo yendawo yokuhamba emva kokunikezelwa kwe-forceps, kwaye ukulimala kwindlela yokunikezelwa kwezinto ezinqabileyo kunqabile.
Kubantwana, ukutya kokutya okungahambi kakuhle kunokuphambuka ngeFrey syndrome. Nangona kunjalo, iimpawu zokutya ezibangelwa ngumzimba emva kokungena kokutya kungekhona ngexesha lokufuna.
Ukuxilongwa
Indlela elula yokufumanisa i-Frey syndrome iquka ukusetyenziswa kwefowuni (isalathisi) ipowder ebusweni. Le nqubo ibizwa ngokuba nguvavanyo oluncinci. Isigulane sinikwa iilekese zemon okanye ezinye ukutya okumnandi ukukhuthaza ukujuluka. Iindawo ezichaphazelekayo apho iifomthi ezithukuthelayo zifake i-blue-black. Amaconsi angacinywa kalula ebusweni ukuze uvavanyo luphindwe kwakhona. Olu vavanyo lunokusetyenziswa ukuvavanya i-Frey syndrome kubantu abangenazo iimpawu (oko kukuthi, izigulane ezingabonakaliyo).
Nangona olu vavanyo luchanekile, aluyi kubonisa ubunzima beemeko. Ukongezelela, lo vavanyo lunoo mngcipheko we-inhalation we-starch powder. Olu vavanyo lufanele lugcinwe elukhumbeni olomileyo, kwaye akufanele lusetyenziswe kubantu abaphefumula kakhulu.
Olunye uvavanyo olubizayo kunye nolubandakanyekayo lokuhlola ukujonga ukuba umntu unayo i-Frey syndrome iquka indlela yokusebenzisa i-biosensoring esebenzisa i-enzymatic electrodes ezibona amanqanaba eL-lactate elukhumbeni.
Uvavanyo olongezelelweyo oluthile lwe-Frey syndrome luquka ukusetyenziswa kwephepha elilodwa lephepha lesinyama ebusweni ukujonga ukujuluka emva kwesigulane sishukunyiswa ngokutya okumnandi.
Ekugqibeleni, i-infrared thermography ingasetyenziselwa ukujonga i-Frey syndrome. Olu vavanyo lokuxilonga ludinga ukuba ubushushu kunye nomswakama ekamelweni kube njalo. Okokuqala, emva kokuvuselela, indawo ebushushu iboniswayo ehambelana nokuhlanjululwa kwemithambo yegazi. Okwesibini, indawo ebanda kakhulu iboniswe ngumbonakaliso obonisa ukukhukhuma. Ezi zinguqu zinzima ukujonga ngeso luntu kubantu abanelinen emnyama.
Unyango
Kwinkoliso yabantu, i-Frey syndrome iyahamba yodwa ngexesha elingama-5 iminyaka. Abantu abaneempawu ezincinci kufuneka baqinisekiswe ukuba imeko iya kudlula yodwa ngaphandle kwonyango.
Kulabo bachaphazeleke kakhulu ngolu hlobo, ukukhukhuma ngokugqithiseleyo kuyona nto ibangela ukuba umntu afune uncedo.
Botox
Uphando olusisiseko-uphando lubonisa ukuba unyango lweBotox njengendlela eyona ndlela ethembisayo neyimpumelelo yokuphatha ukujuluka nokunyuka kwe-Frey syndrome. Ngokukodwa, i-Botox yonyango iboniswe ukuba i-98 ekhulwini iphumelele ekuphatheni iimpawu zesithukuthezi esinamandla. I-botox unyango sele ibonakalise ngempumelelo kubantu abanobuhlungu obushushu besifo sesifo sikashukela, uhlobo lomonakalo wesifo ngenxa yesifo sikashukela.
Kwinqaku le-2017, uLovato kunye nabalobi babambisene babhale oku kulandelayo:
I-BTX [i-Botox] unyango luphumelele kakhulu kunyango lwe-swerey sweating (Frey syndrome), kwaye unokuqwalaselwa njengonyango lwegolide oluqhelekileyo kule nkcazo ye-post-parotidectomy.
Xa unyanga i-Frey syndrome nge-Botox unyango, ugqirha kufuneka uqaphele kuqala indawo echaphazelekayo ngokusebenzisa iindlela zokuvavanya okufutshane. Le ndawo iyahlukana kwiibhola ezincinci, eziphakathi kwe-1 no-1.5 cm. I-Botox ijojowe kwisithuba ngasinye kulezi zikwere ukufaka i-effect, ifom.
Ingqalelo, ezinye iindlela zonyango lwe-Frey syndrome ziye zazama. Ngokona nxalenye, ezi zonyango zibonelela ngokukhawuleza okanye akukho ncedo.
Abachasayo
Okokuqala, abafaki-nxamnye nabo baye bafakwa kwiindawo ezichaphazelekayo. Ezinye izigulane ziye zaxela uxolo olunqamlekileyo kwixesha leeveki ezimbalwa zibulela abantu abachasayo. Ngezona ziphumo ezilungileyo, ifom ye-gel ye-antiperspirant isetyenziswe ebusuku ukuze umise isikhumba kwaye uhlanjwe kusasa. Isixhobo sonywele singasetyenziselwa ukomisa i-antiperspirant emva kwesicelo.
Kwithuba leeyure eziyi-12 emva kokufaka isicelo, isiguli kufuneka siphephe ukukhawula indawo ephathwayo. Ngokuhamba kwexesha, njengoko ukugubungela ngokugqithiseleyo kuqhuba ikhosi yayo kwaye iyanqumla ngokwabo, iingazi ezincinci zabalandeli abachasayo zingasetyenziselwa, kwaye izigulane aziyi kufuneka ukufaka izicelo zokuchasa iintsuku zonke. Ingqalelo, abachasayo banokusebenza njengesikhumba esichukumisayo kwaye baholele ekuvukeleni. Kufuneka isilumkiso kufuneka sithathwe ukuze sigweme ukuqaliswa kwe-antiperspirant kwiso.
Anticholinergics
Okwesibini, i-anticholinergics yama-topical asetyenziswe ukuphatha i-Frey syndrome. Ezi anticholinergics ziquka i-scopolamine, i-glycopyrrolate, kunye ne-diphemnanilmethylsulfate kwaye ingasetyenziswa njengezicombululo okanye izicucu. I-Anticholinergics inokuphucula iimpawu malunga neentsuku ezi-3.
Okubaluleke kakhulu, i-anticholinergics ifakwe ngesikhumba kwaye ingabangela imiphumo emibi yenkqubo equka umlomo owomileyo, umbono ophazamisayo, amehlo anamehlo, ukugcinwa kwemigodi, ukunyuka kwentliziyo, kunye nokunyamezela. Ukongezelela, i-anticholinergics ayifanele isetyenziswe kubantu abane glaucoma, isifo sikashukela, isifo se-thyroid, ukunyanzeliswa kwegazi, kunye ne-hepatic, intshontsho, i-cardiovascular or central disease.
Izinketho zokuphanda
Okwesithathu, ukuhlinzwa akuzange kuphumelele ukunyanzelisa iimpawu ze-Frey syndrome. Ezi zonyango ziquka i-sympathectomy yomlomo wesibeleko, i-tympanic neurectomy, ukutshintshwa kwe-sternocleidomastoidtransfer kunye ne-graerm-fat grafts. Ukongezelela, izixhobo ezahlukeneyo kunye nezithintelo zokungena ngaphakathi ziye zazisetyenziselwa ukuphatha imfucuza.
Ngokuqondakalayo, abaninzi abantu abahlakulela ukuzithukumeza okwesibini ukuya kutyando banqwenela ukufumana utyando olungakumbi ukunyanga le meko.
> Imithombo:
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> Fealey RD, uHebert AA. Isahluko 84. Ukuphazamiseka kwe-Eccrine Sweat Glands kunye ne-Sweating. Ku: Goldsmith LA, Katz SI, Gilchrest BA, Paller AS, Leffell DJ, Wolff K. eds. I-Ditzatrick's Dermatology kwi-Medicine General, 8e eNew York, NY: McGraw-Hill; 2012.
> Lovato, A, et al. I-botulinum yonyango ye-toxin: i-functional silence of salivary disorders. Acta Otorhinolaryngologica Italica. 2017; 37: 168-171
> Sood S, Quraishi MS, uBradley PJ. I-Frey syndrome kunye nokuhlinzwa ngonyango. I-Otolaryngology. 1998; 23: 291-301.