I-Sarcoidosis Ngokuqhelekileyo ixabana phakathi kwama-20 no-40
I-cardiac sarcoidosis ligama eliyinkimbinkimbi yesifo esaziwayo esincinci esingasichaphazela kakhulu umsebenzi wentliziyo, nangona inokuthi ifake kuyo nayiphi na inxalenye yomzimba.
Isifo esivuthayo esibangela i-clumps ye-cell efana neesisundu ezinqabileyo ukuba zandiswe, i-sarcoidosis ithinta ama-135,000 aseMerika, ayenzeka phantse amaxesha angama-10 njengamaxesha amnyama kunabamhlophe.
Yintoni Edala I-Cardiac Sarcoidosis?
Kuze kube ngoku, izazinzulu azi ukuba kutheni isifo, kodwa bakholelwa ukuba i-genetic predisposition, exutywe kunye neengongoma zendalo, ibeka isifo eso.
I-Sarcoidosis ibetha ngokukhawuleza phakathi kweminyaka engama-20 no-40, kunye nabasetyhini badla ngokuphindaphindiweyo kunamadoda.
Iindawo eziqhelekileyo ezichaphazelekayo ziyimiphunga kunye ne-lymph nodes, nangona i-sarcoidosis ingahlaselwa nesibindi, isikhumba, amehlo, iintso, iimfosholo ezinqabileyo kunye nezinye iindawo.
ICardiac Sarcoidosis Ifunyanwe Njani?
I-Sarcoidosis ithintela intliziyo kwi-5 ukuya ku-25% yazo zonke iimeko ze-sarcoidosis, ezenza impawu ezininzi zingabikho nantliziyo yonke, ukuphefumula, ukuvuvukala komlenze okanye, kwiimeko ezinqabileyo, intlungu yesifuba. Ngenxa yokuba zonke ezi zimpawu zibonakalisa iimeko ezininzi ezahlukahlukeneyo, oogqirha besifo se-cardiac sarcoidosis baqhuba ibhetri yeemvavanyo okokuqala ngaphandle kwezifo.
I-biopsy ye-cardiac enye yeendlela ezimbalwa zokuqinisekisa ukuxilongwa, nangona i-MRI yomzimba ingayibona ngamanye amaxesha iiseli ezinqabileyo, ezifana neziqu zehlabathi okanye izityalo zeryuwa kwaye ekugqibeleni zichaphazela ukusebenza komzimba.
Phantse enye yesithathu yezigulane nge-cardiac sarcoidosis ziye zabonakala zingabonakali zibonakala kwi- echocardiogram . Ezinye iimvavanyo zokuxilonga zibandakanya ukucinga ngesikhokliya kunye nesifo sengqondo se-positron ukuchithwa kwemifanekiso, eyaziwa ngokuba yi-PET.
Ukuvela Kwizinto ezingaphezulu komzimba omnye
Nangona i-sarcoidosis inokukrazula kwaye ihamba, ukuhamba ngebhayisikili ngamaqela asebenzayo kwaye angasebenziyo, ngokuqhelekileyo ivela kwiqela elingaphantsi kwelinye ixesha.
Iimpembelelo entliziyweni zinokuvela kwizinto ezingabonakaliyo. Iingxaki ezinokwenzeka ziquka isigqi senhliziyo esingavamile, ukuphuma kwegazi, ukungaphumeleli kwintliziyo kunye neengxaki ze-valve.
I-Sarcoidosis ithathwa njani?
Olona unyango oluqhelekileyo lwe-sarcoidosis, kubandakanywa nesimo senhliziyo, i-corticosteroid prednisone, iyeza-anti-inflammatory. Ezinye i-steroids ngamanye amaxesha zichazwe, njengokuba zikhuselekile izigulane zomzimba, ezifana nezidakamizwa ezichasene ne-malarial, methotrexate, kunye ne-mycophenolate. Ukulwa nesantya senhliziyo, izigulana zingathatha imithi ethile okanye zibe ne- caremac pacemaker okanye i-defibrillator. Ngokuqhelekileyo, izigulane ze-cardiac sarcoidosis zithoba intliziyo.
Njengaye nezinye iintlobo zesifo senhliziyo, ezichaphazela abantu abangaphezu kwezigidi ezingama-80 baseMelika, oogqirha baqonda ukuba izigulane ze-cararac sarcoidosis zijongene nemithintelo engqondweni engabangela uxinzelelo kwimimandla yabo kwaye ibe negalelo ekunciphiseni intliziyo. Ezinye izibhedlele zinika iingcebiso okanye iiklasi zokunceda izigulane kunye neentsapho zabo zijongene nokuxilongwa kwaye zifunde ukuziphucula nokuzitshintsha.
Isiseko soPhando lweSarcoidosis sithumela uluhlu lweqela lokuxhasa i-intanethi ukunika izigulane kunye neentsapho zabo iindlela zokwabelana nabanye ngamava abo.
Imithombo:
"Unyango lwe-Cardiac". nmh.org . 2008. Isibhedlele saseNyakatho-ntshonalanga.
"IiNkcukacha zeeNkxaso ze-US." sarcoidlife.org . Septemba 2008. Isiseko soPhando lweSarcoidosis.
Greif, M., P. Patrakopoulou, M. Weiss, C. Reithmann, B. Reichart, M. Nabauer, noG. Steinbeck. "I-Cardiac Sarcoidosis igqitywe ngu-Arrhythmogenic I-Dyplasia ye-Right Ventricular / Cardiomyopathy." Uhlobo lwezonyango lwezonyango lweMicrosoft cardiovascular Medicine 5 (2008): 231-6. 1
"Sarcoidosis." nhlbi.nih.gov . NgoJuni 2007. I-National Heart Lung ne-Blood Institute.
"Sarcoidosis kunye nentliziyo." stopsarcoidosis.org . 2007. Isiseko soPhando lweSarcoidosis.