I-VATER Syndrome (ngamanye amaxesha ibizwa ngokuba yi-VATER okanye i- VACTERL ) iyisethi yeziphene zokuzalwa ezihlala zihlangene. Ama-initials kwi- VATER syndrome abhekisela kwiindawo ezinhlanu ezahlukeneyo apho umntwana angenakho ukungaqhelekanga:
- Iimpazamo
- Akukho
- T rachea
- E sophagus
- R enal (izintso)
Kukho nokuba neemeko zomzimba kunye nesigxina, ezitshintsha isichazi esiya ku- VACTERL
Umntwana ofunyaniswe ngenye yezi syndromes akayi kuba neengxaki kuyo yonke indawo, kodwa i-constellation yeziphene zokuzalwa ezibandakanya ezininzi kwiindawo.
I-VATER Syndrome Diagnosis
I-VATER ayiyiyo i-disret disorder okanye izifo, ngoko akukho vavanyo lwezonyango ezifana nokuhlolwa kwegazi onokuyifumanisa ingxaki. Ukuze ufumane i-VATER Syndrome, umntwana kufuneka abe neengxaki ezintathu ezichazwe ngasentla.
Nangona i-disorder engavamile (echaphazela enye kwi-10,000 ukuya kuma-40,000 abantwana), iimpawu ziyahluka kakhulu kumntwana omnye ukuya kwelinye. Into ebalulekileyo ye-VATER kukuba akubonakali ithintela uphuhliso lwengqondo. Ngaloo ndlela, ukuba umntwana unempawu zempawu ze-VATER kunye nemingeni ephuhlisayo kunye / okanye ingqiqo, ukuxilongwa kwe-VATER akufanelekanga.
Izizathu zeVATER Syndrome
Ekubeni i-VATER ayisona isifo esiyiyo, ibhekiselwa kuyo ngokuthi "unxulumano olungabonakaliyo lweziphene zokuzalwa." Ngamanye amagama, isethi esithile sendawo yokuzalwa esichaphazelekayo esingaba yinxalenye yeVATER okanye i-VACTERL ayifumene ukuba ixhunyiwe.
Esikhundleni saloo nto, zihlala kunye kunye ngokuqhelekileyo ukuba ziqokelele iimpawu zeempawu.
Ayikho isizathu esaziwayo ngoku, kodwa i-defect yegciwane iyakholelwa ukuba ibandakanyeka. Uphando lubonisa ukuba uhlobo oluthile lomonakalo lunokuvela ngaphambi kokukhulelwa. Kwakhona, abafazi besifo sikashukela babonakala banakho ukufumana abantwana abane-VATER.
Unyango lweVATER Syndrome
Nangona abanye abantwana abaneVATER / VACTERL banokuba neengxaki ezinzima kangangokuthi bahluleka ukukhula njengabantwana, abaninzi bakhula kwaye baphile ubomi obupheleleyo.
Indlela yokonyango incike ngokupheleleyo kwiimfuno ezithile zomntwana ngamnye. Ngokomzekelo, ezinye zezinto ezingaqhelekanga kwizitho kunye neengalo zingaphathwa ngempumelelo ngokuhlinzwa. Abanye bangadinga ukungenelela kwamachiza, unyango lomzimba , unyango lootitshala, njalonjalo.
Njengoko abantwana abaneVATER bekhulile baze baqale ukuya esikolweni, banokuba nemiba ethile yokuphuhliswa okanye yomzimba ekufuneka iqwalaselwe. Ngokomzekelo, banokuba nobunzima bokuhamba, ngokuzivocavoca ngamandla, okanye ukulungelelanisa imoto.
Kubalulekile ukuba uqaphele, nangona kunjalo, ukuba i-VATER ayiyona ingxaki yengqondo. Uninzi lwabantwana abane-VATER kufuneka bakwazi ukulawula iimfuno zesiqhelo nangokwengqiqo esikolweni ngaphandle kobunzima obukhulu.
Abazali bezingane abaneVATER / VACTERL banqwenela ukucela ukwelulekwa ngezofuzo njengoko bacinga ukuba babe nabantwana abaninzi. Ingxaki leyo i-genetic kwaye ngenxa yoko, umngcipheko wokuba nomnye umntwana onentsholongwane efanayo okanye ephathelene nemfuyo iphezulu.
Izibonelelo zeVATER Syndrome
Ukongezelela kokubuza imibuzo yakho ngogqirha, ezi zixhobo zinokuba luncedo ekuqhubeni ukuqonda i-syndrome.
- Isiko seSizwe soLwazi lweBiotechnology
- I-Reference Reference Home
Izibhedlele ezininzi zebonke kulo lonke ilizwe zisebenzela unyango lwe-VATER. Ezinye ziyingcali kwimiba ethile yeli gciwane elinzima kakhulu.
- Isibhedlele Sezingane ZaseCincinnati