Izinto omele uziqwalasele ukuba une-cystic fibrosis
I-Cystic fibrosis ayisisifo sisodwa kwiminyaka yobuntwana. Abantu abaninzi abane-cystic fibrosis bakhokelela ubomi obuvelisayo, kwaye abanye babo banabantwana babo. Amadoda amaninzi anama-cystic fibrosis aqhelekanga. Phantse amaphesenti angama-95 amabhinqa aneCF alahlekile i-deferens yabo, ityhubhu edibanisa ii-testes kwi-urethra.
Ngokungafani namadoda aneCF, abaninzi abafazi banako ukukhulelwa.
Abasetyhini abaninzi abane-cystic fibrosis abakhulelweyo bayakwazi ukuthwala ukukhulelwa kwabo kwixesha. Kukho izinto ezininzi zokucinga ngazo naliphi na isibini esilungiselela ukuba nabantwana. Nangona kunjalo, xa omnye wabazali abanokuba ne-cystic fibrosis, kukho izinto ezingakumbi zokuqwalasela. Nazi ezinye zezinto oza kuzifuna xa uzicwangcisa intsapho yakho
Ukuqonda Umngcipheko Wengane Yakho Yokufa I-Cystic Fibrosis
Ukuba unayo i-cystic fibrosis, oko kuthetha ukuba uneekopi ezimbini eziphosakeleyo zegciwane le- CFTR . Uya kudlula enye yezo zinto kumntwana wakho. Umntwana wakho uya kuba ngumthwali okanye abe nesifo se-cystic fibrosis, kuxhomekeke kwimfuza ayifumana kumlingane wakho.
- Ukuba iqabane lakho linezifo zomzimba eziqhelekileyo zeCFTR, umntwana wakho uya kuba nomzimba owodwa ongenasiphelo kuwe kunye nomnye wesisu oqhelekileyo kwiqabane lakho. Lo mntwana uya kuba ngumqhubi we-cystic fibrosis.
Ukuba iqabane lakho liqhelekileyo kunye nelinye igciwane le-CFTR eliyimpembelelo, ungumphathiswa. Ingane yakho iya kuba neepesenti ezingama-50 yokuba nesifo se-cystic fibrosis kunye neepesenti ezingama-50 ithuba lokuba ngumthwali, kuxhomekeke kwiyiphi imfuyo umntwana azuze ngayo kwiqabane lakho.
Ukuvavanya i-Genetic ukufumanisa ukuba iqabane lakho lingumthengisi likhoyo kwaye lingakunceda wenze izigqibo ezinolwazi malunga nokuba nabantwana kunye. Kukho ezinye iindlela ezingaphaya kokukhulelwa kwabo bafuna ukwandisa iintsapho zabo. Ukusebenzisa iqanda okanye umniki wesilisa okanye ukwamkela unako ukuzalisa intsapho yakho.
Ukukhulelwa Kwimingeni yeCystic Fibrosis Izigulane
Uxinzelelo lokukhulelwa lunokuba nzima ukuba i-cystic fibrosis. Iingxaki eziqhelekileyo kubasetyhini abakhulelweyo abaneCF ziquka:
Ukwanda kobunzima bokuphefumla. Umsebenzi ophantsi weemiphunga ungabhubhisa abo bane-cystic fibrosis. Le yingozi enkulu yokukhulelwa kwabasetyhini abaneCF.
Ukwandiswa kwezifo zokuphefumula. Umsebenzi ophantsi weemiphunga ungabangela izifo zokuphefumula, ezenza kube nzima ukuphefumula.
Sikashukela . Umzimba utshintsho ngexesha lokukhulelwa kunokubangela ukuba abafazi abanempilo babe nesifo sikashukela. Umngcipheko omkhulu nakwabesifazana abane-cystic fibrosis ngenxa yomonakalo weCF obangela i-pancreas.
Ukungondleki. Ukukhulelwa kwandisa ngakumbi ukunyusa amandla emzimbeni, okwenza ukondla okwaneleyo kunzima nakakhulu ukugcina.
Abasetyhini abaneCF bahlala benza ngcono ngokukhulelwa xa kucetyiswa kuba bafumana iliso elifutshane ukususela ekuqaleni. Iingcali zakho ze-cystic fibrosis ziyingcali kwiimeko zakho kwaye kufuneka uxoxe nabo ukuba ufumane ukuba unempilo ngokwaneleyo ukujamelana nokunyuka kokukhulelwa.
Ukuba ukhulelwe, kufuneka uyeke ukuthatha naziphi na ii-A, D, E, okanye iivithamini zeK. Endaweni yoko, tshintshela kwiivithamini zokubeletha kunye ne-Vitamin E. ezongezelelweyo.
I-antibiotics efana ne-fluoroquinolones kunye ne-tetracyclines kufuneka ivalwe.
Umthombo:
Edenborough, F., et al. (2008). Izikhokelo zolawulo lokukhulelwa kwabasetyhini abane-cystic fibrosis. Umbhalo weCystic Fibrosis. (7) S2-S32.