Izibonakaliso zokuqala kunye neziPhambili zeCF, i-Progressive and Genetic Disease
Ngokuqhelekileyo, iimpawu ze-cystic fibrosis ziyanda njengoko eso sifo siqhubeka. Umqathango, obangelwa yintsholongwane engaphelelekiyo, kubangela ugcino oluxubileyo lokwakha emiphakeni (ukuvalela i-airways nokukhokelela kwizifo, umonakalo wamaphaphu kunye nokuhluleka kokuphefumula), i-pancreas (ukukhusela umzimba ukuba ungaphuli kakuhle ukutya ukufumana izondlo) kunye nezinye izitho.
Umzimba ongenasiphelo awuvumeli umzimba ukuba udlulise amanzi kunye netyuwa ukuya kunye nakwiiseli, kubangele iminyango (ngokuqhelekileyo yincinci kunye neyomanzi kubantu abanempilo ngokubhekisele kumaninzi kwaye banamathele kubantu abaneCF). Iimpawu ezinqamlekileyo ziphi izitho zecala kunye nokuthintela ukusebenza kakuhle komzimba.
Iimpawu zokuqala zeCystic Fibrosis
Ininzi yexesha, iintsana ezisandulweyo nge-cystic fibrosis (CF) zibukeka njengezinsana eziphilileyo ngenxa yokuba isifo asibanga nantoni na engabonakaliyo kwimigangatho yokuqala. Phantse i-20% yexesha, iintsana kunye ne-CF ziza kuba nomqobo omkhulu emathunjini ekuzalweni okubizwa ngokuba yi-ileus ye-meconium. Olu hlobo lwesithintelo alufanekiyo ngaphandle kokuba umntwana unayo i-CF, ngoko ke ukuba kwenzeka njalo kubonwa njengesilingo sokuqala sesi sifo.
Iimpawu eziqhelekileyo zeCystic Fibrosis
Ukuba i-cystic fibrosis ayitholakali ekuzalweni, ezinye iimpawu ziza kuqala ukuvela ngonyaka wokuqala okanye ezimbini zobomi, njenge:
- Ukungalungi kobutyebi. Iiblockages kwi-pancreas kunye neengqungqumbo zamathumbu zithintela ukuba inkqubo yokugaya isebenze ngokufanelekileyo. Ukutya okudliwayo kudlula emzimbeni ngaphandle kokuba ezininzi izondlo zixutywe, ezibangele ukukhula okubi. Ukuba umntwana akasabuyisanga ubunzima bakhe bokuzalwa ngo-4-6 kweeveki ubudala okanye ubonisa umzekelo oqhubekayo wokukhula okubi, ugqirha unokuqala ukukhankanya iCF.
- Ukutya okunzulu. Ngenxa yokuba izondlo azixhamli ekudleni, ingqondo izama ukuhlangabezana neemfuno zamandla omzimba ngokuthumela iimpawu zendlala. Abantu abane-cystic fibrosis baya kuba neenqweno ezinqwenelekayo kwaye banokudla ukutya okuninzi ngaphandle kokufumana ubunzima bobunzima.
- I-Bulky, i-Oily, i-Foul Smelling Bowel Movements. Inkqubo yokutya yokungafaki kakuhle inenkathazo ethile yokugaya amafutha kunye nama-protein. Ininzi yezinto eziqhelekileyo ezixhaswa yinkqubo yokugaya ukutya ixiliswe ngamathumbu, okubangelwa ukunyuka kwezilwanyana ezingavamile eziqhelekileyo kwizigulane ezineCF.
- Izifo eziHlaphayo kunye nezifo zokuphefumula. Ukukhupha, ukuphefumula ubunzima, kunye nezifo zokuphefumula rhoqo zihlala zizibonakaliso zokuqala ezibonakaliswa ngabazali babantwana abaneCF.
- Skin Skin. Impembelelo yemfuza eyenza i- cystic fibrosis iphazamise amandla omzimba wokuhambisa ityuwa ngaphakathi nangaphandle kweeseli. Iityuwa ezingenakunyulwa zikhutshwe ngesikhumba ngeemfosane ezikhukhulayo, zibangele uphawu lwe-salta elimnandi lokutya. Ngamanye amaxesha, kusenokuba netyuwa ebonakalayo ekhutshwe kliniki. I-Salt excretion nge-glands ye-sweat isiseko sovavanyo oluqhelekileyo olusetyenziswa ukuxilonga i-cystic fibrosis.
Iimpawu eziPhambili kunye neengxaki zeCF
Iimpawu eziphambili ze-cystic fibrosis aziqhelekanga iimpawu zesifo ngokwayo, kodwa iimpawu zomonakalo ezibangelwa yiCF ngaphezu kwexesha. Ngethuba le miqathango ibonakala, abaninzi abantu sele besazi ukuba banesifo se-cystic fibrosis kwaye baye bahlala nesi sifo ixesha elide. Ezi nkxalabo zilandelayo ziyimpawu eziphambili zeCF:
- Ukunyanzelisa Ubusuku. Ngamanye amaxesha ukutshatyalaliswa okutshatyalaliswa kubonakala kumantombazana ane-cystic fibrosis ngenxa yesondlo esingondlekiyo.
- Ukungenzi lutho. Uninzi lwabesilisa abane-cystic fibrosis alukho nto ngenxa yemfihlo yokuvimba ukuhamba kwesidoda. Abasetyhini banokufumana ukungabikho komntwana ngenxa yentsholongwane yomlomo wesibeleko esivimba ukungena kwesidoda kwizitho zokuzala.
- Sikashukela. Ngokuhamba kwexesha, umonakalo owenziwe kwi-pancreas yi-cystic fibrosis ubangela ukuba uyeke ukuvelisa i-insulin eyaneleyo. Phantse i-15% yabantu abane-cystic fibrosis abafikelela kwiminyaka yabantu abadala baya kuhlakulela isifo sikashukela esasisifo se- diabetes .
- Izifo zesifo. Ukukhutshwa kwamathambo e-bile kwisibindi kubangela ukulimala kunye nomonakalo wesibindi malunga ne-5% yezigulane ze-cystic fibrosis. Ukuba umonakalo wesibindi uvela, ngokuqhelekileyo kubonakala kubantu abadala.
- Izifo zeGallbladder. I-gallbladder igcina into ebizwa ngokuba yi-bile eyenziwa yi-isibindi kunye ne-aids kwisigxina seoli. Kwabantu abaninzi abane-cystic fibrosis, i-bile ibinzima kwaye ayikwazi ukudlula kwi-bile duct ukushiya i- gallbladder . Uninzi lwalo xesha aluvelisi iimpawu, kodwa malunga ne-10% ye-cystic fibrosis iya kwakha i-gallstones efuna ukuhlinzwa.
- Pancreatitis. Xa i-bile ishiya i-gallbladder, ihamba emathunjini amancinci ngokusebenzisa i-buct ye-bony efanayo ekwabelwana ngayo ne-pancreas. Ukuba i-gallstone ishiya i-gallbladder kwaye iyanamathela kwi-buct ye-bison ejwayelekile, iimfihlo ze-pancreatic ayikwazi ukufikelela. Oku kubangela ukuvuvukala nokukhathazeka kakhulu kwamaphancrewa eyaziwa ngokuba yi-pancreatitis, efuna ukungenelelo ngoncedo.
Umthombo:
Foundation Cystic Fibrosis. Malunga neCystic Fibrosis. 10 uEpreli 2016