Xa Ukuphuma Kwegazi Kulo Bumbo Kuvinjiwe
I-Budd-Chiari syndrome yimeko ebangelwa ukuphazamiseka kwegazi ephuma kwisibindi, ngokuqhelekileyo ngegazi le-clot. I-Budd-Chiari syndrome isoloko ivela kubantu abaneengxaki eziphambili ezibangelwa i-blood clotting, kuquka i- antiphospholipid syndrome kunye neengxaki ze-proyeloproliferative ezifana ne-polycythemia vera kunye ne-paroxysmal nocturnal hemoglobinuria.
Izifo ezivuthayo ezingapheliyo ezifana nesifo se-Behcet, isifo sesisu se-inflammatory, sarcoidosis, i-Sjogren syndrome, okanye i-lupus ingabangela nesifo seBudd-Chiari.
Isifo seBudd-Chiari sichaphazela abantu bazo zonke iintlanga kwaye zichaphazela amadoda nabasetyhini ngokulinganayo. Kuyaziwa ukuba isifo seBudd-Chiari sisifo esiyintlekele, kodwa ngokuthe ngqo ukuba kwenzeka kangakanani.
Iimpawu
Uninzi lwabantu abahlakulela i-Budd-Chiari syndrome baneempawu ezintathu eziphambili:
- Ama-Ascites, apho i-fluid iqokelela kwisisu esiswini, ngokuqhelekileyo yenza isisu sifakwe
- Intlungu zesisu
- Isibindi esandisiweyo, esaziwa ngokuba yi-hepatomegaly, kuba igazi lingadlulela esibindi kodwa kungekho kulo.
Ukwakhiwa kwegazi kwisibindi kunokudala umonakalo kwiiseli zesibindi. Ukuba isibindi asisebenzi kakuhle, umntu unokuhlakulela i-jaundice (ukuphuka kwamehlo kunye nolusu) kunye neengxaki zeengtso.
Ukuxilongwa
Iimpawu eziqhelekileyo ze-Budd-Chiari syndrome azikho izikhokelo zokuxilongwa ngenxa yokuba ezo zimpawu zibangelwa ziintlungu.
Ukuba umntu unesifo esenza i-Budd-Chiari syndrome, nokuba kunjalo, kunokukunceda ukuxilongwa. Umkhuhlane oqokelela esiswini ungahlolwa ukuba uncede uqinisekise ukuxilongwa. I-Ultrasound kunye ne-imagination magnontic resonance (MRI) inokunceda ukuhlola umsebenzi wesibindi kunye nokuhamba kwegazi. Isampuli (i-biopsy) yesibindi ingathathwa ukuze ihlolwe iiseli phantsi kwe-microscope.
Unyango
Ukuba ishiywe ingaphendulwanga, i-Budd-Chiari syndrome ingaphazamisa isibindi. Amayeza anikelwa ukutshabalalisa nayiphi na i-clots yegazi ekhoyo kwisibindi aze anciphise ukubunjwa kwamacwecwe amatsha. Ukutya okunesityuwa esezantsi kunokunceda ukulawula i-ascites. Iinkqubo ezikhethekileyo zokupasa ziyakunciphisa ukudibanisa kwegazi kwisibindi. Ukuba isibindi sonakaliswe kakubi, ukufakelwa kwesibindi kunokufuneka.
> Umthombo:
URoy, P., uNwakakwa, Shojmanesh, H., & Khurana, V. (2003). Isifo seBudd-Chiari. eMedicine.