Ukuphazamiseka Kweengxaki zeMpahla yegazi
I-Klippel-Trenaunay-Weber syndrome (KTW), eyaziwa ngokuba yi-Parkes-Weber syndrome, yintlungu yesitya segazi esikhoyo ekuzalweni. Abaphandi abaqinisekanga ukuba kutheni kwenzeka okokuba kungabonakali kudlulayo kwizityalo. Isifo se-Klippel-Trenaunay-Weber sichaphazela amadoda namabhinqa. Ayaziwa ukuba kwenzeka kaninzi kangakanani.
Iimpawu
Iimpawu ze-KTW syndrome zingaquka:
- Isikhulu esikhulu se-port mark-wine markmark (ngokuqhelekileyo uphawu lokuqala olubonwayo) lubangelwa imilambo encinci yegazi phantsi kwesikhumba. Kungenzeka kube bumnyama obomvu, obomvu, uveliswe, okanye unokuba ne-bumps on it bleed easily. Ixesha eliqhelekileyo i-port idayini enkulu kwaye ivela kwi-KTW syndrome ihlala ichaphazela umlenze (kathathu ngokuphindaphindiweyo kunamanye amanxalenye), i-markmark yokuzalwa ihlanganisa, umzekelo, ukususela kwisithambiso kunye nokunyuka kwizwane kwinqanaba elichaphazelekayo lomzimba.
- i-hemangiomas - imibala engaqhelekanga yemithambo yegazi
- imilenze ye-varicose
- iingxube zemithambo yegazi ezibizwa ngokuba yi-arteriovenous malformations (AVMs)
- Ukukhula ngokugqithisileyo kweethambo eziluhlaza kunye namathambo emlenzeni ochaphazelekayo
Iingxaki zeetyhulwa zegazi kunye nokugqithisa ukukhokelela ekuphumeni kwegazi, intlungu, izifo zesikhumba (i-cellulitis), ukuhamba nzima, kunye negazi (ezinokunqumla ukujikeleza kwegazi emlenzeni, okanye ukuhamba kwezinye iindawo zomzimba kwaye kubangele umonakalo). Umntu ngamnye onesifo se-Klippel-Trenaunay-Weber uyathinteka ngendlela yakhe, kwaye iingxaki ezinokuhlangenwe nakho zingenakunqweneleka ngokukhawuleza ukuba zikhubaza kakhulu.
Izimbilini zegazi ezimbini ezinempawu ezifanayo ziyi-Klippel-Trenaunay syndrome kunye ne- Sturge-Weber syndrome . Zibini zenza i-port port ne-blood malformations malformations. Nangona kunjalo, ngokungafani ne-Klippel-Trenaunay syndrome, i-Parkes-Weber syndrome kunye ne-Sturge-Weber syndrome ziquka ii-AVM kwaye ziyakwazi ukuba zinzima kakhulu iimpawu ezinzima.
Ukuxilongwa
Iimpawu ze-Klippel-Trenaunay-Weber syndrome zikhona xa zizalwa. Ukuxilongwa kusekelwe kwiimpawu, ngokukodwa ubukho be-port stain stain kunye nokukhula ngokugqithisileyo kwezicubu ezincinci okanye amathambo. I- CT scan kunye ne- MRI zinceda ekuqaliseni ubungakanani be-syndrome.
Unyango
Unyango lwe-KTW syndrome ligxile kwiimpawu. Abantu abaninzi bancedwa ngonyango olulula ezifana ne-elastic compression stockings, eyanciphisa intlungu kunye nokuvuvukala. Ulwaphulo lwe-Laser lunokunciphisa okanye luphelise i-port stain stain. Ngamanye amaxesha utyando kufuneka ukuba ususe i-hemangioma enkulu okanye ukususa izicubu ezingaphezulu komlenze ongezantsi. Kwiimeko ezinqabileyo, umlenze ochaphazelekayo ungadinga ukuba unqunywe ngenxa yamacangci egazi okanye ukugqithisa okukhulu.
Nangona unobungozi kunye nobuhlungu, abantu abaninzi abane-Klippel-Trenaunay-Weber syndrome bahamba kakuhle nonyango. Ugqirha lufuneka kuphela kwiimeko ezinzima.
Umthombo:
> "Inkcazo ye-Klippel-Trenaunay Syndrome." Ukuqonda i-Klippel-Trenaunay Syndrome. Iqela leNkxaso ye-Klippel-Trenaunay ye-Syndrome. 26 Meyi 2009