Izintso zakho zizitho zombini ezinobhontshisi zilapha ngaphantsi kwembambo yakho. Umsebenzi wabo oyinhloko ukucoca igazi ukwenzela ukukrazula umzimba wenkunkuma kunye nolunye utywala.
I-Immunoglobulin I-nephropathy (I-nephapatropathy ye-IgA) yinkinga yeengtso echaphazela i-glomerulus, enxibelelwano olunzulu lweemithwalo yegazi elijongene nalo msebenzi wokucoca igazi.
Sibanzi
Intsho nganye iqulethe iiprephoni eziligidi, kunye nephron nganye iqukethe i-glomerulus.
Ezi ntengiso ze-glomeruli okanye ubuninzi bemithambo yegazi zicofa ngegazi lakho igazi. Bathumela iimveliso ezinkunkuma kunye nomthamo (njengomchamo) kwi-vestile kunye nokukhulula igazi nezinye iamolekyu ezinkulu, njengeeprotheni, zibuyele kwigazi.
Ngokuqhelekileyo, isistim somzimba somntu sikhupha i-antibody, i-immunoglobulin A, ekuphenduleni uhlobo oluthile lwe-trigger njengentsholongwane yentsholongwane. Kodwa kubantu abane-nephropathy ye-IgA, i-immunoglobulin A iyakha kwaye ibeke kwi-glomeruli yeentso zabo.
Le-immunoglobulin I-buildup ibangela ukutshaya kweengso, kwaye ekugqibeleni ukutshabalalisa, okwenza kube nzima ukuba i-glomeruli isebenze umsebenzi wokucoca. Ngenxa yoko, ukungaphumeleli kwezintso kungenzeka.
Izibalo
ENyakatho yeMerika, malunga nabesilisa abaphindwe kabini kunabesifazana bane-IgA nephropathy, kwaye oku kubhekisela kubo bobabini kunye nabantu abadala. Ukongeza kwinto eqhelekileyo kwindoda, i-igA nephropathy iyinto eqhelekileyo kwiCaucasians nakwa-Asiya kwaye inqabile kubantu base-Afrika-baseMelika.
Ekugqibeleni, eUnited States, ngaphezu kwesiqingatha sabantu abadala, abaneminyaka engama-30 okanye ngaphezulu kwixesha lokuxilongwa kwe-IgA nephropathy, babe nesigaba sesithathu ukuya kwisigaba sesi-5 isifo sesifo esingasasigxina. Oku kuphakamisa ukuba ukufumanisa i-igA nephropathy ngaphambili kungenceda, njengoko unyango lunokunciphisa umsebenzi wezintso zehla.
Ukuxilongwa
Izimpawu ezimbini eziqhelekileyo ze-IgA nephropathy zigazi e-urine , okubangela ukuba umchamo ubonakale kumbala we-tea, kunye neprotheni emcinini , okubangela ukuba umchamo ubonakale u-foamy.
Nangona kunjalo, uninzi lwabantu abane-neopropathy ye-IgA abanalo iimpawu. Ukuba umntu ubona igazi elikhulu emvini, kwaye banesifo sofuba se-IgA, ngokuqhelekileyo emva kokusuleleka kwintsholongwane yentsholongwane njengomkhuhlane okanye isisu somkhuhlane.
Ngaloo nto, ugqirha unokugxekisa wena okanye umntu onomthandayo unesiphithiphithi se-IgA esisekelwe kwimbali echanekileyo, kunye nobungqina bemigodi negazi. Ukuqinisekisa ukuxilongwa, i-nephrologist (ugqirha ogxininisa kwizifo zengqondo) uya kususa iincinci ezincinci zesifo. Le nqubo ibizwa ngokuba yi-biopsy kwaye yenziwa ngokubeka inaliti emhlane wakho, apho iinjongo zingakwazi ukufikelela lula.
Emva kwe-biopsy, i-pathologist iza kuhlola iingcuphe zeengso phantsi kwe-microscope kwaye ziyiqhekeza ukuze zibone ukuba zikhona i-deposit IgA. Ukuba kukho ubungqina be-IgA buildup, oku kuya kuqinisa ukuxilongwa kwe-IgA nephropathy.
Kubalulekile ukuba uqaphele ukuba oogqirha abenziyo i-kidney biopsy kuwo wonke umntu ophethe igazi okanye iprotheni emcinini.
Endaweni yoko, ukuba unayo igazi okanye iprotheni kumchamo wakho, ugqirha wakho unokugada umchamo wakho kunye nomsebenzi wezintso emva kweenyanga ezintandathu ukuya kwezilishumi elinesibini okanye njalo.
Unako ukwenza i-biopsy ukuba umsebenzi wakho wezintso uqala ukuhla (njengoko kubonakaliswe ngumgangatho ophezulu we-creinine kwi-blood test) okanye uqala ukuba nexabiso elongezelelweyo lokulahleka kweprotheyini kumchamo wakho.
Ukuba nomfutho wegazi ophezulu unokuba nesizathu sokuba kutheni ugqirha wakho enze i-kidney biopsy (ukuba kukho igazi kunye / okanye iprotheni emcinini).
Unyango
Kubantu abaxilongwa nge-IgA nephropathy, ukuya kwisiqingatha kuya kuhamba ngokucothayo (kwiminyaka emashumi ukuya kwiminyaka) ukuphulukana nokuphela kweengxaki zezintso (ezibizwa ngokuba yi-end-stage stal disease, okanye i-ESRD).
Ngokuxhomekeke kwizinto ezinxulumene nephopropathy yakho ye-IgA, ugqirha wakho unokukuphatha ngamachiza okunciphisa ukuqhubela kwesifo sakho sezintso.
La mayeza aquka i-angiotensin-guqula i-enzyme (ACE) inhibitors okanye i-angiotensin II receptor blockers (ARBs) ukulawula uxinzelelo lwegazi. Iingxube zeoyile zokutya zentlanzi nazo zivame ukucetyiswa.
Ugqirha wakho unokuphatha ukuvuvukala okwenzeka nge-IgA nephropathy ngokukunika i-steroids njenge-prednisone.
Ukuba uqhubela phambili kwisifo sokuphela kwesigulo, unokuphathwa nge-dialysis okanye ukutshintshwa kweengtso .
Nangona ukutshintshwa kwentliziyo kukukhethwa kukho, akuqwalaselwe njengonyango, njengoko i-nephropathy ye-IgA ingakwazi ukuhlala kwiimpso esanda kutsalwa.
ILizwi
Ingaba wena okanye umntu obathandayo uye wafumanisa ukuba unesifo sofuzo se-IgA, esinye isifo sesifo, okanye ufunyenwe ukuba negazi kunye / okanye iprotheni kumchamo wakho, qi niseka ukuba ulandele ugqirha wakho njengoko ucebisi.
Oku kuhlala kunjalo ngokwenene ne-IgA nephropathy, njengoko kunzima kakhulu oogqirha ukuba baxelele ukuba ngubani oya kulungile kwaye ngubani oza kuphuhlisa isifo sesifo sesifo.
> Imithombo:
> Cheung CK, uJarratt J. (2017). Inkcazo yeklinikhi kunye nokuxilongwa kwe-IgA nephropathy. UGlassock RJ, uFervenza FC, ed. UpToDate, Waltham, MA: UpToDate Inc.
> Isizwe seSizwe seSifo sikashukela kunye neeNtsholongwane zeNtsholongwane kunye neNtsholongwane. (2014). Iizintso Zakho kunye nendlela Abasebenza ngayo.
> IgA Nephropathy Foundation yaseMelika. (nd). Imibuzo ye-FAQ - Yintoni i-IgA Nephropathy?
> Wyatt RJ, uJulian BA. IgA nephropathy. N Engl J Med. 2013 Juni 20; 368 (25): 2402-14.