I-Leukemias yabantwana: Ngokuthelekisana nomdlavuza kunye ne-Congenital

Xa isihloko se- leukemia siphakanyiswa , abantu abaninzi banokuqonda ngokucacileyo ukuba le nto ingabantwana besifo. Kodwa emva koko, iinkcukacha zibonakala zifihliwe. Kufuneka kuqatshelwe ukuba, ngelixa i-leukemia yinto ehlaseleyo yokusweleka kwabantwana , kuyinyaniso ukuba ukukhulelwa kwe-leukemia kusengumncinane.

Isifo esingapheliyo kunye neLukemia

I-leukemi i-acute iyakhula ukukhula ngokukhawuleza.

Iiseli ezihlambalaza-ezibizwa ngokuba yi-blasts-zikhulile kwaye azizange ziphuhlise ngokwaneleyo ukuphumeza imisebenzi yazo ye-immune system. Ngokwahlukileyo, i-leukemia engapheliyo ikhula kwiiseli ezihlukeneyo okanye ezivuthiweyo, ezingenza ezinye zeemisebenzi zazo, kodwa kungekhona kakuhle. Iiseli ezingaqhelekanga ze-leukemia ezingapheliyo zivame ukunyuka kwizinga elincinci kunama-leukemi. Nangona kunjalo, i-leukemia engapheliyo ayinqabile kubantwana .

Uninzi lwama-leukemia ebuntwaneni lunomdlavuza we-lymphocytic (ALL). Uninzi lwamatyala aseleyo luyi-leukemia enamandla ( AML ). Imimiselo ye-'miyeloid 'kunye ne' lymphocytic 'kula magama ibhekisela kwiintsapho ezimbini ezahlukeneyo zeeseli: ezo ziza kuphakamisa iiseli zegazi ezimhlophe (lymphocytic); kunye nalawo aya kuphakamisa iiseli ezibomvu zegazi, iiplatelets, kunye neeseli zegazi ezimhlophe ezifana ne-monocytes, neutrophils, kunye nokunye.

Ubuntwaneni kunye neLukemia yaseCenital

Nangona i-leukemia yiyona nto ixhaphake kakhulu ebuntwaneni, i-leukemia yokuzalwa yintsholongwane ayinqabile, equkethe ngaphantsi kwe-1 ekhulwini yeeukemias bonke abantwana.

Le meko ichazwa njenge-leukemia eyenzeka ngaphakathi kweeveki ezi-4 ukuya kwezi-6 zokuzalwa. Kucingelwa ukuba le ntsholongwane iqala ukuphuhlisa ngaphambi kokuba umntwana azalwe.

Ngelishwa, i-6-month-long rate is survived is one-third-half, nangona i-chemotherapy enobudlova. Nangona kunjalo ukukhutshwa ngokukhawuleza kuye kwabikwa, kodwa isayensi ayinikelanga iimpendulo ezicacileyo malunga nendlela oku kwenzeka ngayo.

Inyaniso yokuba le miqondiso engabonakaliyo iye yabikwa, inokubangela ukuba kubekho inkqubo yokwenza isigqibo sokwenza isigqibo koogqirha nabazali. Abanye baye bazibuza ukuba ingaba indlela ekhuselekileyo yonyango, ingakumbi ekuqaleni, iyalungelelaniswa.

Kufuneka kuqatshelwe ukuba i-leukemia yokuzalwa engesiyo kuphela i-leukemias ekufuneka ibikwe ngokubonakalayo. Ukukhutshwa ngokukhawuleza kwenzeka kwezinye iindidi ze-leukemia ngokunjalo, kwaye ukuxolelwa kusenokukhawuleza, okanye kukufutshane, okanye kukuhlala ixesha elide, kuxhomekeke kwimeko echaziweyo.

Izibalo zeNtsholongwane yabantwana

Nangona i-leukemia ngumdla wesifo esiqhelekileyo kubantwana kunye nentsha, ngokubanzi, i-leukemia yobuntwana isisifo esingavamile. Phantse iipesenti ezingama-75 zama- leukemi phakathi kwabantwana kunye nentsha BONKE, kwaye amaninzi amatyala asele a-AML.

Ngokutsho kokuhlaziywa kwamanani e-American Cancer Society, BONKE baqhelekileyo ebuntwaneni bentsapho, bekhankanya phakathi kweminyaka emi-2 ne-4 ubudala. Iimeko ze-AML zininzi zisasazeka kwiminyaka yobuntwana, ngaphandle kokuba i-AML idlula ngokuqhelekileyo kwiminyaka emibili yokuqala yobomi kunye neminyaka yobutsha.

Ngokubhekiselele kobuhlanga kunye nobuhlanga, BONKE baqheleke ngakumbi kubafundi baseSpain nabamhlophe kunabantwana base-Afrika nabama-Asia nabaseMerika, kwaye kuyaqheleke kubafana kubafana kumantombazana.

I-AML iyenzeka ngokulinganayo phakathi kwamakhwenkwe namantombazana kuzo zonke iintlanga.

I-leukemia engapheliyo ayinqabile ebantwaneni, kodwa xa iyenzeka, ininzi yale miba inokuhlala isifo esingapheliyo sesifo se-leukemia (CML), esichaphazela kakhulu abantwana abaselula kwiqela elivisayo kunabantwana abaselula. I-juvenile ye-myelomonocytic leukemia (i-JMML) ngokuqhelekileyo ivela kubantwana abancinci, abaneminyaka engama-2 ubudala.

> Imithombo:

> Fozza C, uBellizzi S, uBonfigli S, i-Campus PM, uDore F. Longinotti M. Cytogenetic kunye neHematological Remontaneous Frequency on a Case of Acute Myelogenous Leukemia. I-eur. J. Haematol. 2004; 73: 219-222.

> Jain N, Hubbard J, Vega F, Vidal G, Garcia-Manero G. Borthakur G. Ukuxolelwa ngokukhawuleza kwe-Acute Acute leukemia: Ingxelo yeziGulane ezintathu noVavanyo lweeNcwadi. Lekemia yekliniki. 2008: 2: 64-67.

> IMartelli MP, iGionfriddo I, Mezzasoma F, iMilano F, i-Pierangeli S, i-Mulas F. i-Arsenic i-Trioxide kunye ne-All-Trans i-Retinoic Acid Target NPM1 i-Mutant Oncoprotein Levels kunye ne-Induce Apoptosis kwi-NLM1-i-AML Cells. Igazi . 2015; 125: 3455-3465.

> Verhaak RGW, Goudswaard CS, van Putten W, Bijl MA, et al. Ukuguqulwa kweNucleophosmin (i-NPM1) kwi-Acute Myeloid Leukemia (AML): Umbutho kunye nezinye izinto ezingafaniyo ze-Gene kunye nokuSungulwa kweGenesis Ukubonakalisa iziTyikitya kunye nokuBaluleka kwabo okuBalulekileyo. Igazi . 2005; 106: 3747-3754.

> I-Wiemels J. Impembelelo malunga neengxaki ze-Leukemia yabantwana. Ukusebenzisana kweMicrobiological . 2012; 196 (3): 10.1016 / j.cbi.2012.01.007.