Sibanzi
Nangona amagama angase abonakale eshaqisayo, i-Erythroblastopenia yexesha elifutshane ye-Childhood (TEC) yintswelo yokunciphisa i- anemia yobuncinane. Yona nto ibangelekileyo yokunciphisa imveliso yeselom ebomvu ebuntwaneni. I-Erythroblast yileli iiseli eziza kuba ngamaseli obomvu kwaye -penia livela kwigama lesiGrike elisweleka. Okubalulekileyo, iziphumo ze-anemia ezibangelwa ukungakwazi kwethambo lomongo ukuba zivelise amaseli obomvu ngexesha elithile.
Iimpawu
I-anemia kwi-TEC yinkqubo encinci ukuze abanye abantwana bangenayo impawu. Aba bantwana banokufunyanwa ngesiganeko ngomsebenzi wegazi rhoqo okanye bafumane kwakhona ngaphandle kokuya kunyango. Kwezinye izigulane, iimpawu zihlobene ne-anemia. Ziquka:
- Ukukhathala okanye ukhathala
- Isikhumba esinamabala
- Utywala
- Intliziyo yentliziyo esheshayo, ebizwa ngokuba yi-tachycardia
- Ukuqhawukelwa ngumphefumlo
Rick Factors
Njengoko igama libonisa, i-TEC ivela ebuntwaneni. Uninzi lwabantwana lufunyaniswa phakathi kweminyaka emine kunye nemine. Abafana babonakala benomngcipheko othe wenyuka xa kuthelekiswa namantombazana.
Ukuxilongwa
Akukho vavanyo lovavanyo olulodwa lwe-TEC. Ezinye izigulane zichongiwe ngumsebenzi wegazi oqhelekileyo wokuhlola abantwana kakuhle. Kwezinye izigulane, ukuba i-anemia iyakrokrelwa, i-TEC ichongiwe kwibala elipheleleyo legazi (CBC). Ngokubanzi, i-CBC iya kubonisa ukuba yi-anemia ehlukeneyo. Ngamanye amaxesha kukho i- neutropenia (inani elinciphile le-neutrophils, uhlobo lweseli legazi elimhlophe).
Iibomvu zegazi ezibomvu ziqhelekileyo kodwa ziyakwandiswa xa isiguli siqala ukubuyela.
Inxalenye esilandelayo ye-worp is count reticulocyte count. Ama-Reticulocyte ayenamaqebunga egazi obomvu asanda kukhishwa emlonyeni wethambo. Ekuqaleni kweso sifundo, i-reticulocyte count is down, ebizwa ngokuthi i-reticulocytopenia.
Emva kokuba isisombululo somnxeba usisombululo, i-reticulocyte count ikhuphuka (ephezulu kuneyona eqhelekileyo) ukuzalisa i-cell red and supply returns to normal when anemia is resolved.
Ngexesha lomsebenzi, kubaluleke kakhulu ukuhlukanisa iTEC kwiDamond Blackfan Anemia (DBA), uhlobo olulwelwe yi-anemia. Izigulane ezine-DBA zineempembelelo ezinzima kwixesha elizeleyo. Izigulane ezine-DBA zincinci (ngaphantsi kweminyaka eyi-1) ekuxilongweni kunye neeseli ezibomvu zegazi zikhulu kunezona ziqhelekileyo (macrocytosis). Ngokuqhelekileyo, ukuba ukuxilongwa akucaci ukuba umtsalane we-bone aspirate kunye ne-biopsy kufuneka uyenze. Ngamanye amaxesha uvavanyo oluvakalayo lokuqinisekisa i-TEC kukuba isiguli siyifumana ngaphandle kokungenelela.
Izizathu
Impendulo emfutshane asiyazi. Phantse isiqingatha sezigulane ziza kugula i-viral illness 2-3 months before diagnostic. Kukhankanywa ukuba intsholongwane ibangela ukuxothwa kwesikhashana kwe-red cell cell production in the bone. Iintsholongwane ezininzi zidibaniswe ne-TEC kodwa akukho nanye kwisiseko esifanayo.
Ubude
Kwiimeko ezininzi, i-TEC isisombululo kwiinyanga ezili-1 ukuya kwezi-2 kodwa kukho iingxelo zabantwana ezithatha ixesha elide ukuba bafumane.
Unyango
- Ukuqwalaselwa: Ukuba i-anemia ilungile kwaye umntwana wakho akanakunzima, akukho nonyango olufunekayo. Ugqirha wakho unokunyusa ukubala kwegazi lomntwana wakho ngexesha elide lugqitywe.
- I-Corticosteroids: Ngamanye amaxesha i-steroids efana ne-prednisone isetyenzisiwe kodwa akukho bungqina obuqinileyo bokuthi le nyango iyanciphisa ixesha lokubuyisela.
- Ukutshatyalaliswa kwegazi : Ukuba i-anemia iyingozi okanye umntwana wakho unempawu ezivela kwi-anemia (ukuxakeka, ukukhathala, ukuphefumula okufutshane, izinga lentliziyo eliphakamileyo, njl.) Ukunikezelwa kwegazi kunokunikezelwa.