I-Steroid-Incomplesive Encephalopathy Associated w / Autoimmune Thyroiditis
Isifo esaziwa ngokuba ngu " Hashimoto's Encephalopathy " saqala ukuchazwa kuphela ngo-1966. Emva koko, oogqirha baqala ukuhlanganisa iingxelo zecala, kwaye "uHashimoto's Encephalopathy" yaba ligama elamkelweyo ngenxa yesimo sengqondo sokuxhalabisa ehambisana neHashimoto's thyroiditis.
Ngenxa yokuba ezininzi izigulane ngeHacmoto's Encephalopathy ziphucula nge-steroids okanye unyango lwe-immunosuppressant, ezinye iingcali zibhekisela kwimeko "njenge-steroid-respondence-sensitive response that combines thyroiditis" (SREAT).
Kwezinye iimeko, le meko ingabizwa nangokuthi "i-nonimulitic autoimmune meningoencephalitis" (NAIM), engabandakanyekanga kuphela iingxaki ze-thyroid ngaphandle kweempawu ezifana ne-Sjögren syndrome kunye ne-systemic lupus erythematosus-ehlobene ne-meningoencephalitis. Ubume kuzo zonke le miqathango kukuba basabela kwiyeza le-steroid.
Igama elithi "encephalopathy" libhekisela kwisifo sengqondo eguqula umsebenzi wengqondo okanye isakhiwo. Into ebalulekileyo yiphina i-encephalopathy iguqulwa isimo sengqondo. Nangona iimpawu zixhomekeke kuhlobo lokuxhalabisa kunye nokuba lunzulu kangakanani, ezinye iimpawu eziqhelekileyo ziquka:
- ukulahleka kwememori
- kunzima ukugxila
- ukulahlekelwa kwikhono lokuqonda kunye nomsebenzi
- utshintsho lwabantu
- ukunyaniseka nokukhathala
- ukulahleka kwengqondo
- i-myoclonus (i-muscular involuntary muscle)
- i-nystagmus (ukukhawuleza kwamehlo okuzenzekelayo)
- ukuthuthumela
- ukubuthathaka kwezihlunu
- ngqondweni
- ukuxinwa, ukuxinwa
- ubunzima bokugwinya
- kunzima ukuthetha
Ezinye iimpawu ezingabonwa ziquka:
- ukudideka, ukuphazamiseka
- kwengqondo
- intloko
- i-hemiparesis yesigxina esisekunene-ilungelo lokukhubazeka
- iingxaki zokuhamba kweemoto ezintle - iingxaki ngokulungelelaniswa kwezandla, izandla, iminwe
Ngenxa yokuba i-Hashimoto ye-Encephalopathy / SREAT ingacaciswanga, kwiphononongo echazwe kwi- Archives ka- 2006 yakwa -Neurology , iingcali ezichazwe ukuze zichaze iikliniki ezahlukeneyo, i-laboratory kunye ne-radiological findings of the condition.
Injongo yabo kukunceda ukuphucula amandla oogqirha ukuba baqonde kwaye baxilonge le meko.
Uhlolisiso lujonge izigulane ezingama-20 (abafazi aba-14, amadoda angama-6) afunyanwe phakathi kuka-1995 no-2003. Ubudala babo obudala kwizifo zaqala iminyaka engama-56, kunye neminyaka engama-27 ukuya kuma-84 (ububanzi, iminyaka engama-27-84).
Iimpawu zeeklinikhi ezibonakalayo eziqhelekileyo zikhona:
- Ukugubha - 80%
- I-aphasia yexesha elifutshane - 80% (iAphasia inzima ngolwimi, ichaphazela ukukwazi ukuthetha, ukufunda okanye ukubhala)
- I-Myoclonus - i-65% (ngokukhawuleza, ukuxubha ngokungazibandakanyiyo kwe-muscle okanye iqela leentsundu)
- Ukufumana i-ataxia - i-65% (ukungahambi kakuhle okanye ukuhamba ngokukhawuleza, ukuhamba nzima)
- Ukuxhamla - 60%
- Ukulala okungavumelekanga - 55%
I-Misdiagnosis i-Standard
Yiyiphi inkxalabo ekhethekileyo kukuba iingcali zifumene ukuba BONKE ABANTU ABANTU ABAKHUMBI bebenokuqala ukuxilongwa. Umzekelo:
- Incephalitis e-Viral - 25%
- Ukunyuka kwengqondo kwegazi - 20%
- Isifo seCreutzfeldt-Jakob - 15% (Isifo seCreutzfeldt-Jakob sisisifo esingaqhathaniswayo, esinobuhlungu, esihlala sisifo esibuhlungu besifo esibuhlungu, ngezinye izihlandlo esibizwa ngokuba yi "Mad Cow Disease" kubantu)
ILebhu kunye noVavanyo olungavumelekanga kwi-Hashimoto's Encephalopathy / SREAT
Uninzi lweemvavanyo ezingaqhelekanga zabonwa, kubandakanya:
- Amanqanaba enzyme enyukayo - 55%
- Ukunyuka kwamazinga e-thyroid-stimulation hormone (TSH) - 55%
- Ukwanda kwe-sedimentation ye-erythrocyte ("rate rate") - 25%
- I-Cerebrospinal yamanzi engafanelekiyo ibonisa ukuvuvukala - 25%
- Ukuboniswa kwemifanekiso ye-Magnetic engafanelekanga ehambelanayo ne-encephalopathy - 26%
Izigqibo
Abaphandi baphetha ukuba kukho iintlobo ezahlukeneyo zokufunyanwa ezinokudityaniswa ne-Hashimoto's Encephalopathy / SREAT, kwaye loo nto isazi kakuhle.
Abaphandi bancoma ukuba i-Hashimoto's Encephalopathy / SREAT ifanele iqwalaselwe nokuba i-TSH kunye ne "sed rate" iqhelekileyo, i-cerebrospinal fluid ayibonisi ubungqina bokuvuvukala kwaye i-MRI iyinto evamile.
Ngolunye ulwazi
Ulwazi lwe-Encephalopathy yeHashimoto Page
> Imithombo
> Castillo, Pablo MD; et. al. "I-Steroid-Responsive Encephalopathy ehambisana ne-Autoimmune Thyroiditis." Arch Neurol . 2006: 63: 197-202. (Izahluko 63 No. 2, Februwari 2006)
> ISikole kaZwelonke seNational and Disorders and Stroke