UkuDansa kweEyes UkuDansa kweenyawo
I-Opsoclonus-myoclonus syndrome (i-OMS) isifo sengqondo esivuthayo. Kubangele imiba ebalulekileyo ngezakhono zezithuthi, ukuhamba kwamehlo, ukuziphatha, ukuphazamiseka kolwimi kunye neengxaki zokulala. Ngokuqhelekileyo kuza ngokukhawuleza kwaye ngokuqhelekileyo kungapheliyo; ukuba ufumene unyango lwe-opsoclonus-myoclonus syndrome, kuya kwenzeka ukuba uphelele ubomi bakho bonke.
Igama layo lichaza iimpawu zalo: i- opsoclonus iguqula ukunyuka kwamehlo kwaye i- myoclonus ithetha ukuxhaphazwa komzimba. Kwakhona kwaziwa nangokuthi "i-Kinsbourne syndrome" okanye "amehlo okudansa-inyawo."
Ngubani osemngciphekweni
Kwi- dismute disorder , umzimba uhlasela amaseli akhe aphilileyo. I-Opsoclonus-myoclonus syndrome ibangelwa yintlupheko yomsindo apho izifo zomzimba ziphendulela kwiintsholongwane zentsholongwane okanye i-tumor ebizwa nge-neuroblastoma. Kukho nawuphi na, ama-antibodies aphelisa ukuhlaselwa kweeseli zengqondo, kwaye oku kubangela umonakalo ovelisa iimpawu.
I-Opsoclonus-myoclonus syndrome ivela rhoqo kubantwana. Iintsana ziyinqanaba leminyaka apho i-neuroblastoma idla ngokuqhubekayo; malunga neepesenti ezine zala bantwana baya kuphuhlisa i-OMS. Naliphi na umntwana onesifo se-OMS uza kuvavanywa ukuze abone ukuba unayo isisu, nokuba uyagula ngenxa yentsholongwane yentsholongwane ukusuka kubini behlala behamba kunye.
Unyango
Ixhalabisayo eliphambili nge-opsoclonus-myoclonus syndrome ukuxilongwa kwangoko kwaye unyango ukuze kuphunyezwe ukuxolelwa kwegazi kunye nokubuyiselwa. Ukuba umntwana une-opsoclonus-myoclonus syndrome kwaye une-tumor, i-tumor isuswe ngokugqithiseleyo. Ngokuqhelekileyo, izicubu zisemagaleni okuqala kunye ne- chemotherapy okanye unyango lwe-radiation alufunwa.
Ngamanye amaxesha oku kuphucula okanye kususa iimpawu. Kubantu abadala, ukususwa kwamathumba kaninzi akuncedi kwaye iimpawu zingaphaya ngakumbi.
Ezinye iindlela ziquka:
- Injini ye-Adrenocorticotrophic hormone (ACTH)
- Iimpawu ze-immunoglobulins ezingenakuthandana - ukulungiselela amashishini e-antibodies ukusuka kubanikeli begazi abanempilo
- I-Azathioprin (Imuran) - igxotha i-immune system, eyanciphisa umkhiqizo we-antibodies
- I-Oral and intravenous steroids, njenge-prednisone, dexamethasone, ne-hydrocortisone
- I-Chemotherapy efana ne-cyclophosphamide kunye ne-methotrexate, kubantwana abane-neuroblastoma
- I-apheresis yonyango-yokutshintsha i-plasma yegazi
- I-immunoadsorption - ukucoca ii-antibodies egazini kuye kwazama abantu abadala abane-OMS.
Ukunyanga okuqhubekayo kunye neengxaki zifuneka rhoqo ukulawula iimpawu kunye nokunciphisa umngcipheko we-tumor ebuyelayo.
Prognosis
Abantu abanethuba elihle lokubuyela kwisiqhelo emva kokuba unyango lwabo banabo iimpawu ezintle. Abo baneempawu ezinzima kunokuba banokuphucula imisipha yabo (i-myoclonus) kodwa banenkinga yokusebenzisana. Ezinye iingxaki ezivela ebuchotsheni bobuchopho, njengengxaki yokufunda nokuziphatha, ukungabikho kwengqalelo yokungahambi kakuhle kwempilo (ADHD) kunye nokukhathazeka okunyanzelekileyo, kuya kwenzeka, kwaye ezi zifuna unyango lwabo.
Abantwana abaneempawu ezinzima kakhulu ze-OMS banokulimala kwengqondo engapheliyo engabangela ukukhubazeka ngokomzimba nangokwengqondo.
Ukukhula
I-Opsoclonus-Myoclonus Syndrome ayinqabile; Abantu abayizigidi ezi-1 kuphela bakholelwa ukuba banomdla kwihlabathi. Kubonakala kubantwana nakubantu abadala, kodwa kunokuchaphazela abantu abadala. Kwenzeka kancinci kumaxesha amantombazana kunamakhwenkwe kwaye ngokuqhelekileyo kufunyaniswa kuphela emva kweenyanga ezili-6.
Imithombo:
Pranzatelli, M. "Izimpawu Zobunzima: Umlilo Womngane." Discove r, 2000.
Pranzatelli, M. "Opsoclonus-Myoclonus Syndrome". I-National Organisation for Disorder Disorders, 2016.