I-Cystic Fibrosis ithathwa njani?

Ukugcina Izinto Ziqhubekile

I-Cystic fibrosis iyisifo esingazikho unyango owaziwayo. Iinjongo zonyango ukunciphisa iimpawu, ukucotha inkqubela yesifo, ukuthintela iingxaki, kwaye ngokwandisa umgangatho wobomi kwi-CF isigulane.

Indlela yoLuntu

Izifundo zibonise ukuba iziphumo zingcono xa izigulane ze-cystic fibrosis zithola unyango liqela labaqeqeshi abaqeqeshiwe ngokukodwa kwiziko le-CF elivumelekileyo kwi-United States.

Amalungu eqela leCF aquka rhoqo:

Mayeza

Abantu abane-cystic fibrosis baya kufuneka bathathe unyango bonke ubomi babo. Amanye amayeza aqhelekileyo:

I-antibiotics: ithathwa ukukhusela okanye kunyanga intsholongwane. Ngamanye amaxesha i- antibiotics ithathwa ngomlomo, kwaye ngamanye amaxesha iyisilwanyana esiphefumlelweyo kwaye isetyenziswe ngokusetyenziswa komshini obizwa nge-nebulizer.

Ulwaphulo-mthetho: I- anti-inflammatory yiyilisi eyanciphisa ukucasuka nokuvuvukala. Izidakamizwa ezichasayo zingabhalwa kwizigulane zeCF zokunciphisa ukuvuvukala emiphakeni nokuphefumula.

I-Steroids yinto enye yeziyobisi ezichasayo, kodwa azinasetyenziselwa kakhulu unyango lwe-CF ngenxa yokuba zingabangela isifo sikashukela okanye iingxaki ngeentso namathambo. Izidakamizwa ezingekho-stteroidal anti-inflammatory (NSAIDs), ezifana ne-ibuprofen, ziqheleke kakhulu kwi-CF unyango.

Ii-enzymes: Enye yeengxaki ezibangelwa yi-CF kukuba i-secretions ezinqamlekileyo kwiipancreas ziyakuthintela ukukhulula i- enzyme umzimba kufuneka udle ukutya. Ukuba ukutya akugutywanga, umzimba awukwazi ukufumana nayiphi na izondlo. Abantu abane-CF kufuneka bathathe iipilisi eziqulethe ii-enzyme ezifunekayo phambi kwesidlo ngasinye.

I-Mucolytics: I- Mucolytics ngamachiza ancedayo kwi-mucus encinci kwaye yenza kube lula ukukhwehlela. Zivame ukuba zichazwe kwizigulane ze-cystic fibrosis ukuze zibancede zicacise iindlela zabo zokuhamba ngeenqwelo ezinqamlekileyo, ezinamathele ezinokuthi i-CF ibangele. Ngamanye amaxesha i-mucolytics ithathwa ngomlomo kwaye ngamanye amaxesha bayakhutshwa nge-nebulizer.

UkuCima kweAwayway

Inxalenye ebalulekileyo yonyango lwe-cystic fibrosis kukusetyenziswa kweendlela ezahlukeneyo zokunceda ukukhulula nokususa i-mucus. Izigulane zeCystic fibrosis kufuneka zibe nale nyango rhoqo ngamaxesha. Ulwaphulo luya kubandakanya enye okanye ngaphezulu kwezi ndlela:

I-Chest I-Psytic Treatment (CPT): Eli gulisa lisebenzisa ubuchule obubizwa ngokuba yi-percussion equka ukubethelwa kwesigxina kwezandla-kwiindawo ezicwangcisiweyo zesifuba. Ngezigulane ezisandul 'ukufumana i-CF, umgulisi wokuphefumula okanye umongikazi uya kwenza iPCT kodwa abazali baya kufundiswa ukuba benze njani ukuze bakwazi ukuthatha unyango ekhaya. Iseshoni yohlobo lweCPT ihlala malunga nemizuzu engama-30 kwaye kuya kufuneka ukuba yenziwe ngokuphindwe kabini ngosuku.

I-Vibration: Enye inqubo eyenziwa ngamanye amaxesha kunye ne-percussion ngexesha le-CPT liguqula. Oku kwenziwa kwakhona ngezandla, kodwa njengokuba igama libonisa, isishukumisi esishukumisayo sisetyenziselwa ukuba sisetyenziswe.

I-Postural Drainage: Ngexesha le-CPT, isigulane sifakwe kwizikhundla eziya kuvumela amandla adonsela amandla ukukhupha izikhuni ezikhululiwe ziphuma emiphakeni. Oku kwaziwa ngokuba ngumsele wamanzi.

I-Inflatable Therapy Vest: Ngamanye amaxesha, endaweni ye-CPT ye-manual, ifowuni ebizwa ngokuba yi-device kunye ne-airway imvume. I-vesti igqithise kwaye ichithe ngokukhawuleza ukukhupha i-mucus ngokunyakaza okuncincileyo. Iintlobo zokusebenzisa i-vesti yinto yokuba isigulane sinokwenza unyango ngaphandle koluncedo, kwaye iiseshoni ziphela malunga nemizuzu engama-20.

I-Flutter Idivayisi: Eyaziwa nangokuthi i-valve ye-flutter, esi sixhobo esincinane esiphethwe ngesandla sibonakala sifana ne-inhaler.

Isigulane sibeka umlomo emlonyeni wakhe kwaye siphephe ngamandla. Ifowuni isebenzisa umoya okhuphekileyo ukudala izibilini zesifuba.

Ukutya

Abantu abane-cystic fibrosis abazifumani kakuhle izondlo ngokutya abazidlayo, kwaye umsebenzi wokuphefumula ubangele batshale iikhalori ezingaphezulu. Le ntsebenzo kabini ibangela ukungondleki nokukhula okubi. Ukulwa neengxaki zesondlo, izigulane ze-CF zifuna ukuya kuma-calories angama-50% ngaphezulu kwabanye abantu abaneminyaka yabo. Izidlo zondlo zidala izicwangciso zokutya ezizimeleyo ezihambelana neemfuno zesigulane ngasinye, kodwa ngokuqhelekileyo, abantu abane-cystic fibrosis banokulindela ukuba:

Ukuzivocavoca

Umsebenzi wezobugcisa unomvuzo omfutshane kunye nexesha elide kubantu abane-cystic fibrosis. Inzuzo ngokukhawuleza kukuba usebenze ngamandla emoyeni emiphakeni kwaye unceda ukukhulula i-mucus. Inzuzo yexesha elide lokuzivocavoca kukuba inceda ukuphucula impilo kunye nokunyamezela komzimba, okwenza umzimba ube namandla ngakumbi ukulwa nemiphumo yeCF.

Ukufakelwa kwezityalo

Xa i-cystic fibrosis iqhubela phambili kwaye ibangela umonakalo omkhulu wemiphunga, ukufakelwa kwemiphunga kunokuba yindlela yokonyango kubantu abahlangabezana nemigqaliselo. Nangona ukufakelwa kwemiphunga akuyona inketho kubo bonke abantu, kuboniswe ukuba yimpumelelo kakhulu kwizigulana ezithile zeCF. Abantu abangaphezu kwe-1600 abane-cystic fibrosis baye bafumana ukufakelwa kwemiphunga, kwaye malunga nesiqingatha sabo baye basinda okungenani kwiminyaka emihlanu emva kokufumana umphunga omtsha.

Imithombo:
Bilton, D. (2008). Icystic fibrosis. Mayeza. 36, 273 - 278.
Pitts, J., Flack, J., & Goodfellow, J. (2008). Ukuphucula ukondla kwisigulane se-cystic fibrosis. Umbhalo weNkcazo yeMpilo yezeMpilo. 22, 137-140.