Abaninzi bethu baqhelana neengxaki zamehlo eziqhelekileyo - i- glaucoma , i-cataracts, i-eye eye syndrome kunye ne-macular degeneration. Ulwazi malunga nale miqathango lubonakala lula. Nangona kunjalo, i-Dych's Dystrophy yintlungu engabonakaliyo kwaye abo bachaphazelekayo bashiya iofisi yegqirha kunye nemibuzo engaphenduliyo. Ukuzifundisa malunga nemeko kunokuba ngumngeni.
Ukuba wena okanye umntu omaziyo uye wafumanisa ukuba une-Fuch's Dystrophy, oku kulandelayo kuya kukunceda ufumane ulwazi oluninzi.
Yintoni i-Dych's Dystrophy?
I-Dych's Dystrophy yimeko yelifa elizuze ilifa elibangela ukuphazamiseka kwi-cornea, isakhiwo esicacileyo se-dome esifundweni saso kweso. I-cornea yenziwe ngamathandathu amathandathu eeseli ezinokuphela kweeseli zithuba lokugqibela kwicala elingasemva kwe-cornea. Enye yemisebenzi yamaseli endothelial ukuqhubeka upompa umkhuhlane ngaphandle kwe-cornea, ugcine uyihlanganise kwaye icace. Xa ezi iiseli ziqala ukuhluleka, umbane ukhula kwi-cornea ebangela uxinzelelo kwiiseli. I-cornea iyavuthwa kwaye umbono ubonakala. Kwiifom ezinzima zeDych's Dystrophy, i-cornea inokuhlaziya.
Ngaba ukuxilongwa kwe-Fuch's Dystrophy kuyichaphazela kakhulu ubomi bam?
Ubunzima beCych's Dystrophy buyahluka. Izigulane ezininzi aziyazi ukuba zinemeko kanti abanye banokukhungatheka ngemiboniselo enciphise.
Nangona kunjalo, ezininzi izigulane zigcina umgangatho omhle wombono wokusebenza kakuhle kwimisebenzi yemihla ngemihla.
Ngaba i-Dych Dystrophy iya kundibangela ukuba ndingaboni?
Ngobugcisa bwanamhlanje, ubuphofu buphantse bungekhoyo kubantu abanezigulane ezixhamla kwi-Dych's Dystrophy. Kubalulekile ukuqonda ukuba i-Dych's Dystrophy ayichaphazeli i- retina , isalathisi se-receptor esilumkileyo se-cornea okanye i-nertic optic, intambo yesibindi edibanisa iliso kwingqondo.
I-cornea inikeza iliso kuninzi lamandla alo okubheka. Kwiindlela ezinzima zesifo, ukutshintshwa kwe-corneal okanye inkqubo entsha ebizwa ngokuba yi-DSEK inokubuyisela kumsebenzi oqhelekileyo kwi-cornea.
Luhlobo luni lweempawu endingazifumana ngayo ngeCych's Dystrophy?
Ezinye izigulane zikhalaza ngombono ophazamisekile kusasa obonakala ubhetele kangcono njengoko usuku luqhubeka. Oku kungenxa yokuba umbane ukwakha kwi-cornea ngobusuku. Njengoko uvuka kwaye uhamba malunga nosuku lwakho, iliso livulekele kwimeko yendalo kwaye umkhuhlane ophuphuma ngokwenene kwi-cornea kunye nombono uya kuphucula. Unako ukuva nokubona imvula okanye i-halos ngokujikeleza izibane, ukukhanya kunye nombono wakho ubonakala ngathi i-foggy. Ezinye izigulane zikhalaza ngeentlungu okanye kwintlungu yomzimba wangaphandle.
Ingaba unyango luya kuthinta indlela yam yokuphila imihla ngemihla?
Ukwelashwa kweDych's Dystrophy kumaxesha okuqala kulula. Ngokuqhelekileyo, kubandakanya ukufaka isisombululo se-sodium ye-chloride okanye i-otyment kwi-eyes ukuze ukhonze amanzi. I-5% ye-chloride ye-sodium yinkomati esekelwe kwetyuwa edla ngokuphindwe kabini kwimizuzu emine ngosuku. Ezinye izigulane zifumana iziphumo ezingcono ngokusebenzisa i-ointment formulation yokuba zibeka iso labo ebusuku.
Yintoni eyenzekayo xa i-Dych's Dystrophy ikhula ngakumbi?
Ezinye izigulane azizange zenze uhlobo olubi lweDych's Dystrophy.
Nangona kunjalo, ukuba iqhubekela phambili kwisigaba esibi kakhulu, unokuhlakulela i-coweropathy yobunzima . Yilapho i-fluid egcwele i-bullae okanye i-blisters ifomu kwaye yenza imbonakalo ibonakale kwaye ikwazi ukuqhuma kwaye ibangele intlungu ebonakalayo kunye nolwaphulo lomzimba lwangaphandle. Kule meko, oogqirha abathile baya kufaka i- lens yokubambisa i-lens kwiso lakho kwaye banikezele i-drops eye. Ukuba imeko ibuhlungu, ugqirha wakho unokuncoma ukutshintshwa kwe-corneal okanye inkqubo ye-DSAEK. I-DSAEK (i-Descemet's Stripping Automothe Endothelial Keratoplasty) yinkqubo apho kuphela inxalenye ye-cornea elandelwayo yatshintshwa ngamaseli endothelial enempilo.
Inkqubo ye-DSAEK inenkcitho engaphantsi kune-total corneal transplant kunye nombono obangela ukuba ungcono.
Ngaba abantwana bam bayaba nefa le-Fuch's Dystrophy?
Ezinye iziganeko ze-Dych's Dystrophy zibonakala zingenalo i-genetic pattern. Nangona kunjalo, amaninzi amatyala anokwaziwa njenge-autosomal pattern of inheritance. Oku kuthetha ukuba ukuba unemeko, kwaye omnye wabazali bakho unalo mqathango, umntwana ngamnye unelithuba lama-50% lokuba ne-Dych's Dystrophy.
> Umthombo:
> Afshari, Natalie A. MD; UAron B. Pittard, MD; Adnan Siddiqui, BS; UGordon K. Klintworth, MD, PhD. Ukufundwa kwe-Fuchs Corneal Endothelial Dystrophy eLawula phambili kwi-Keratoplasty engenawo, i-Arch Ophthalmol. 2006.