Inkcazo, Iinkcukacha ze-Mantle Cell Lymphoma
Yintoni i-lymphoma yesigcawu seengubo, kwaye yintoni na kufuneka ndiyazi malunga nale hlobo lomhlaza?
Sibanzi
I-Cell Exit Lymphoma yinto engaqhelekanga ye-non-Hodgkin's lymphoma (NHL) . I-5-7% kuphela ye-NHL yeli qela. I-lymphoma ye- B lymphocytes, okanye "i-B-cell". Nangona kubonakala ngathi i-tumor ekhula ngokukhawuleza, ephantsi kwe-microscope, ikhula ngokukhawuleza kwaye iziphatha njenge-lymphoma ephezulu.
Kubizwa ngokuba 'yengubo' yeseli lymphoma ngoba kuqala kuvela kwinxalenye ye-lymph node ebizwa ngokuthi 'ingubo'.
Izinto zobungozi
I-Cell Extension Lymphoma ixhaphake kakhulu kumadoda kunabesifazane kunye nabantu abadala. Ixesha elidlulileyo lokuxilongwa liyiminyaka eyi-60. Akukho ziphumo ezinobungozi bokufumana olu hlobo lwe-lymphoma, nangona iimeko ezininzi ezivela kwizifo ezithintekayo kwiimeko zamakhemikhali ziye zajongwa nje ngeemeko zengozi ye-non-Hodgkin's lymphoma ngokubanzi.
Iimpawu
I-cell ventic lymphoma iqala kwi-lymph nodes. Into yokuqala abantu abaninzi bayayiqaphela ukuba iindidi ezandisiweyo entanyeni, ukuvuthwa okanye izibilini. Esi sifo sikhula ngokukhawuleza kwaye ngexesha libonwa ngugqirha, isifo sele sisasazeka kwezinye izitho zomzimba. Kwabanye abantu esi sifo sikhula ngokukhawuleza, into ethi i-oncologists ibhekisela kuye ngokuthi "indolent" kodwa le yodwa. Umongo wethambo, i-spleen, intamo ye-throat iyathinteka kubantu abaninzi, kwaye ngokuqhelekileyo iiseli ze-lymphoma egazini.
Amathumbu nawo anokuchaphazeleka kwabanye abantu, kwaye ivelise iimpawu ezinjengeentlungu zesisu okanye isifo sohudo.
Ukuxilongwa
Izilingo ze-Santle cell lymphoma zifana nezo zenye iindidi ze-lymphoma. Ziquka ukuhlolwa kwegazi, ukukhangela kunye nokuhlolwa komongo wethambo . Emva kokuba iimvavanyo zityhila ukuba yiziphi iindawo zomzimba ezichaphazelekayo, isigaba sesifo sinokumiselwa .
Uninzi lwabantu lunesifo sesigaba se-III okanye IV esasasazeka kwizitho ezahlukeneyo zomzimba.
Unyango
I-cell ye-Mantle cell lymphoma iphathwa ngokukodwa nge-chemotherapy, kodwa indlela ephathwa ngayo ngenyameko incike kakhulu kwiminyaka yobudala. Abantu abadala, abasempilweni abadala, i-chemotherapy elandelwa yi-stem cell transplant ingaba yinto efanelekileyo, kodwa ibandakanya ukutyhefuza. Ukholo aluqhelekanga ngaphandle kokuba isifo sifumaneka kwangaphambili, kwaye injongo yonyango kukugcina isifo silawulwa ixesha elide kunokwenzeka. Zininzi unyango zidibene neRituxan (rituximab) kwaye le nyeza ingasetyenziselwa ulondolozo olulandelayo kunyango ngokunjalo.
Izidakamizwa ezitsha ezifana neVelcade (bortezomib) kunye neTranda (bendamustine) zihlukile kwezinye iirimimethrapi ze-chemotherapy. Ukuhlanganiswa amaninzi kweziyobisi kunye namachiza amatsha kufundiswa kwizilingo zeklinikhi, kwaye mhlawumbi ukuba unyango olutsha kunye nonyango lwe-vestium lymphomawill luza kufumaneka kwixa elizayo.
Ekubeni isifo sisoloko siphezulu, unyango olunjengokuhlinzwa kunye nokunyanga kwamayeza kaninzi luba negalelo elincinane.
Ukujamelana
Ukujamelana nokuxilongwa ngokutsha kwe-lymphoma kunokuba kubi. Ufanele uqale phi xa uqala ukufumanisa i-diagnostic? Kwabanye abantu, unyango olubi lungaba lukhetho olufanelekileyo.
Kwabanye, unyango olubi lungahle lube lukhethi olukhethekileyo. Nangona kunjalo, kusekho nethemba lomgangatho omhle wobomi kunye nexesha onalo. Hlola ezi ngcebiso malunga nokujongana nomhlaza wesigulo . Fumana kwiintsapho kunye nabahlobo . Kukho uluntu olukhulu lwenkxaso yabantu abane-lymphomas kwi-intanethi kulabo bafuna inkxaso kwabanye abafumana into efanayo. Yaye ukhumbule ukuba uphando luqhubekayo, kwaye kukho intuthuko ethembekileyo eyenzekayo kunyango lomhlaza namhlanje.
Imithombo:
Avivi, I., no A. Goy. Ukucwangcisa i-parantgm ye-Mantle Cell Lymphoma paradigm: Impembelelo ye-Novel Treatments on Current Practice. Uphando lweKlinikhi yeKhansela . 2015. 21 (17): 3853-61.
U-Cheah, uC. C., uSymym, J., noMnu Wang. I-Mantle Cell Lymphoma. Umbhalo we-Clinical Oncology . Ishicilelwe kwi-intanethi ngaphambi kokushicilelwa ngoJanuwari 11, 2016
Dreyling, M., Ferrero, S., kunye ne-European Mantle Cell Lymphoma Network. Inendima yonyango ejoliswe kuyo kwi-stilence cell lymphoma: ukutshintshwa kokufa okanye kuphila? Haematologica . 2016. 101 (2): 104-14.
Ubuqili, uMnu, noJ. Armitage. Indawo yokutshintshwa kwesoli ye-slim cell lymphoma. Oncology . 2013. 27 Isibonelelo 2: 2-6.
Maddocks, K., no K. Blum. Izicwangciso zonyango kwi-lentipho cell cell. Unyango lwe-Cancer noPhando . 2015. 165: 251-70.
UMartin, uP. Ibrutinib - unyango olutsha oluqhelekileyo lwe-vestima ye-vestima ephindaphindiweyo? Lancet . 2015 Dec 4. (Epub ngaphambi kokuprinta).
Tucker, D., kunye noMthetho. I-Ibrutinib yesalathini yeselfu ye-lymphoma. I-Future oncology . 2016. 12 (4): 477-91.
Vose, J. Mantle cell lymphoma: ukuhlaziywa kuka-2015 kwi-diagnostic, umcipheko-mngcipheko kunye nokulawulwa kweklinikhi. I-American Journal yeHematology . 2015. 90 (8): 739-45.